Contrasting behavior of endolymphatic sac tumors: a report of 2 cases and literature review.
BACKGROUND
Endolymphatic sac is an established source of low-grade neoplasms, posing a difficult problem in local tumor control.


METHODS
Two cases of endolymphatic sac tumors are described in detail with regard to their clinical presentation and radiological findings. Both cases had diametrically opposite clinical outcomes in spite of repeated surgical interventions. A case with severe paraneoplastic syndrome and death after "cancer cachexia" is described.


CONCLUSIONS
Although endolymphatic tumors are known for their low-grade aggressiveness, in occasional cases, they may behave in a highly malignant behavior. The present communication highlights the contrast in clinical outcome and makes the clinician cautious of this special subgroup of tumors with a highly aggressive nature.
Mohindra
Sandeep
S
Department of Neurosurgery, Postgraduate Institute of Medical Education and Research, Chandigarh, India. satya_sandee@yahoo.com
Chhabra
Rajesh
R
Mukherjee
Kanchan Kumar
KK
Gupta
Sunil Kumar
SK
Mohindra
Satyawati
S
Vashista
Rakesh K
RK
D000293:Adolescent; D004428:Ear Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000628:therapy; D004712:Endolymphatic Sac; D017809:Fatal Outcome; D006801:Humans; D008297:Male; D008875:Middle Aged; D009361:Neoplasm Invasiveness; D010257:Paraneoplastic Syndromes / Q000209:etiology* / Q000628:therapy; D011859:Radiography; D019291:Skull Base; D016896:Treatment Outcome