Rosai Dorfman syndrome with sinonasal mucosa and intraocular involvement.
A 15 year-old-male presented with concurrent sinonasal polyposis and anterior uveitis with cervical lymph node enlargement. Cervical lymph node biopsy confirmed Rosai-Dorfman disease. Though patient's eye symptoms did not respond well to topical corticosteroid treatment but he showed a remarkable regression in the size of nasal polyps and cervical lymph nodes after systemic corticosteroids. Intraocular involvement in such a case is rare.
Kare
M
M
Department of Medicine, Goa Medical College, Bambolim, Goa.
Dang
S
S
Dang
A
A
D000293:Adolescent; D001707:Biopsy, Needle; D003937:Diagnosis, Differential; D015618:Histiocytosis, Sinus / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D008198:Lymph Nodes / Q000473:pathology*; D008297:Male; D009297:Nasal Mucosa / Q000382:microbiology / Q000473:pathology*; D009298:Nasal Polyps / Q000601:surgery; D009333:Neck / Q000473:pathology; D010256:Paranasal Sinuses / Q000473:pathology*