Combined Scimitar syndrome and interruption of the inferior vena cava causing mega-azygous and hemiazygous veins.
Computed tomography angiography detected scimitar syndrome with venous drainage to the inferior vena cava caudal to an interruption of the inferior vena cava in a 48-year-old woman. The hepatic veins drained to the supra-hepatic portion of the inferior vena cava cephalic to the interruption, which was a short area of atresia. Azygous and hemiazygous veins were massively enlarged since they drained the right lung, abdomen viscera exclusive of the liver and lower extremities. Inferior vena cava interruption by a short, focal atresia has not previously been described. The inferior vena cava immediately caudal to the interruption is presumed to remain patent because of the scimitar vein flow.
Greenberg
S Bruce
SB
Radiology University of Arkansas for Medical Sciences, 800 Marshall Street, Little Rock, AR 72202, USA. greenbergsbruce@uams.edu
D001401:Azygos Vein / Q000473:pathology*; D004108:Dilatation, Pathologic; D005260:Female; D006503:Hepatic Veins / Q000503:physiopathology; D006801:Humans; D008875:Middle Aged; D012039:Regional Blood Flow; D012587:Scimitar Syndrome / Q000473:pathology* / Q000503:physiopathology; D014682:Vena Cava, Inferior / Q000002:abnormalities*