Rosai Dorfman syndrome with extranodal manifestation.
Rosai Dorfman Syndrome (RDS) is a benign condition and a rare cause of cervical lymphadenopathy. It usually occurs in the first decade of life and manifest as massive enlargement of cervical lymph nodes. The disease has a benign course and involvement of the nasal cavity as an extranodal site is exceptional. A 22-year-old male presented as progressive massive bilateral cervical lymphadenopathy accompanied with nasal obstruction and occasional episodes of epistaxis. A FNAC from cervical lymph node and biopsy from nasal mass was compatible with RDS.
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Department of E.N.T, Himalayan Institute of Medical Sciences, Jolly-grant, Dehradun (UA) - 248140, India.
Bisht
Manisha
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Varshney
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Pathak
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D000328:Adult; D003937:Diagnosis, Differential; D015618:Histiocytosis, Sinus / Q000503:physiopathology* / Q000601:surgery / Q000628:therapy; D006801:Humans; D008198:Lymph Nodes / Q000473:pathology*; D008297:Male; D009296:Nasal Cavity / Q000473:pathology* / Q000601:surgery; D009333:Neck / Q000473:pathology*