title: Pentalogy of Cantrell : successful early correction.
abstract: The pentalogy of Cantrell is a rare midline developmental field complex often with a dismal outcome. We present a newborn qualifying for Cantrell's pentalogy with an abdominal wall defect, a diaphragmatic defect and a heart defect, a ventricular septal defect (VSD) and a left ventricular diverticulum. Early operative correction following accurate diagnostic work-up was prompted at the age of 11 weeks because of progressive heart failure. Beside correction of the VSD and the abdominal and diaphragmatic defects, resection of the distal part of the diverticulum was possible without damage to the LAD and preserving good contractility. Two years postoperative follow-up is uneventful.
authors: Department of Pediatric Cardiology, Wilhelmina Children's Hospital, University Medical Centre Utrecht, 3508 AB, Utrecht, The Netherlands. amhkorver@hotmail.com
authors: A M H
authors: AM
authors: Korver
authors: F
authors: F
authors: Haas
authors: M W
authors: MW
authors: Freund
authors: J L M
authors: JL
authors: Strengers
mesh_terms: D034861:Abdominal Wall / Q000002:abnormalities*; D000015:Abnormalities, Multiple / Q000601:surgery*; D017023:Coronary Angiography; D004240:Diverticulum / Q000601:surgery*; D006325:Heart Atria / Q000002:abnormalities; D006331:Heart Diseases / Q000601:surgery*; D006345:Heart Septal Defects, Ventricular / Q000601:surgery*; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D013577:Syndrome; D013909:Thorax / Q000002:abnormalities; D014057:Tomography, X-Ray Computed