title: Non-transplant surgical approach to liver-based hereditary haemorrhagic telangiectasia: a first report.
abstract: A 55-year-old woman with hereditary haemorrhagic telangiectasia (HHT) underwent a left lateral liver bisegmentectomy (removal of segments 2 and 3) for hepatic-based arteriovenous malformations. This lesion determined a progressive fatigue and invalidating effort dyspnoea. The postoperative course was uneventful and the patient is currently doing well at 4 years after surgery. To our knowledge, this is the first case of hepatic-based HHT treated with liver resection. This anecdotal report should promote the evaluation of this approach in order to define its role in the treatment of liver involvement in this rare disease.
authors: Department of Transplant Surgery, University of L'Aquila, San Salvatore Hospital, L'Aquila, Italy. giuseppe_orlando@hotmail.com
authors: Giuseppe
authors: G
authors: Orlando
authors: Carlo
authors: C
authors: Sabbà
authors: Nicola
authors: N
authors: De Liguori Carino
authors: Chiara
authors: C
authors: Scelzo
authors: Laura
authors: L
authors: Tariciotti
authors: Luigi
authors: L
authors: Bonanni
authors: Maurizio
authors: M
authors: D'Angelo
authors: Leonardo
authors: L
authors: Baiocchi
authors: Jan
authors: J
authors: Lerut
authors: Giuseppe
authors: G
authors: Tisone
mesh_terms: D005260:Female; D005500:Follow-Up Studies; D006498:Hepatectomy / Q000379:methods*; D006801:Humans; D008875:Middle Aged; D018570:Risk Assessment; D012720:Severity of Illness Index; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000175:diagnosis* / Q000601:surgery*; D013997:Time Factors; D016896:Treatment Outcome