Non-transplant surgical approach to liver-based hereditary haemorrhagic telangiectasia: a first report.
A 55-year-old woman with hereditary haemorrhagic telangiectasia (HHT) underwent a left lateral liver bisegmentectomy (removal of segments 2 and 3) for hepatic-based arteriovenous malformations. This lesion determined a progressive fatigue and invalidating effort dyspnoea. The postoperative course was uneventful and the patient is currently doing well at 4 years after surgery. To our knowledge, this is the first case of hepatic-based HHT treated with liver resection. This anecdotal report should promote the evaluation of this approach in order to define its role in the treatment of liver involvement in this rare disease.
Orlando
Giuseppe
G
Department of Transplant Surgery, University of L'Aquila, San Salvatore Hospital, L'Aquila, Italy. giuseppe_orlando@hotmail.com
Sabbà
Carlo
C
De Liguori Carino
Nicola
N
Scelzo
Chiara
C
Tariciotti
Laura
L
Bonanni
Luigi
L
D'Angelo
Maurizio
M
Baiocchi
Leonardo
L
Lerut
Jan
J
Tisone
Giuseppe
G
D005260:Female; D005500:Follow-Up Studies; D006498:Hepatectomy / Q000379:methods*; D006801:Humans; D008875:Middle Aged; D018570:Risk Assessment; D012720:Severity of Illness Index; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000175:diagnosis* / Q000601:surgery*; D013997:Time Factors; D016896:Treatment Outcome