Duplication and exstrophy of the bladder with clitoris and vagina duplex as well as uterus bicornis.
The variants of bladder exstrophy with duplication of the bladder are extremely rare and associated with further malformations of the genitourinary system. Initially, the clinical appearance is that of a classic exstrophy. In this case a second, regularly configured bladder with a normal supravesical urinary tract was found covered by an omphalocele like a cutaneous bag. At the same time, there was a duplication of the vagina and a bicornuate uterus. The surgical treatment, aiming at anatomic reconstruction of the genitourinary system and closure of the symphysis, was successfully performed without any complication.
Kluwe
Wolfram
W
Department of Surgical Pediatrics, Children's Hospital, Inselspital, University of Bern, Bern, Switzerland. wolfram.kluwe@insel.ch
Mau
Harald
H
D000015:Abnormalities, Multiple / Q000601:surgery*; D001746:Bladder Exstrophy / Q000601:surgery*; D002987:Clitoris / Q000002:abnormalities* / Q000601:surgery; D005260:Female; D006554:Hernia, Umbilical / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D019651:Plastic Surgery Procedures / Q000379:methods*; D001743:Urinary Bladder / Q000002:abnormalities*; D014599:Uterus / Q000002:abnormalities* / Q000601:surgery; D014621:Vagina / Q000002:abnormalities* / Q000601:surgery