Chronic inflammatory demyelinating polyradiculopathy: an atypical pediatric case complicated with phrenic nerve palsy.
An atypical form of chronic inflammatory demyelinating polyneuropathy (CIDP) complicated with phrenic nerve palsy is presented with clinical and electrophysiologic features. A seven-year-old girl had initial presentation mimicking Guillain-Barré syndrome based on electrophysiologic characteristics. Between 7-11 years of age, she had five recurrences of subacute onset of weakness which usually developed over at least 2-4 months and progressed to loss of ambulation and to respiratory insufficiency. Radiologic examinations revealed unilateral phrenic nerve palsy associated with CIDP. Our patient demonstrated the rare association of CIDP and phrenic nerve palsy, resulting in diaphragmatic paralysis and respiratory failure.
Polat
Muzaffer
M
Department of Pediatrics, Ege University Faculty of Medicine, Izmir, Turkey.
Tosun
Aye
A
Serdaroğlu
Gül
G
Cağlayan
Engin
E
Karapinar
Bülent
B
Gökben
Sarenur
S
Tekgül
Hasan
H
D002648:Child; D002908:Chronic Disease; D003711:Demyelinating Diseases / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D004576:Electromyography; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D010243:Paralysis / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D010791:Phrenic Nerve; D011129:Polyradiculoneuropathy / Q000150:complications* / Q000175:diagnosis / Q000628:therapy