[Cystic lymphangioma of the spleen in a patient with Klippel-Trenaunay-Weber syndrome: MRI findings].
We present the case of a 22-year-old woman with Klippel-Trenaunay-Weber syndrome who presented with clinical signs and symptoms of gastrointestinal obstruction. Ultrasonography and magnetic resonance imaging showed massive splenomegaly with multiple cysts replacing the normal parenchyma of the spleen. Histologic study after splenectomy confirmed the diagnosis of cystic lymphangioma of the spleen, which is an exceptional manifestation of Klippel-Trenaunay-Weber syndrome.
Montes
M
M
Departamento de Diagnóstico por Imagen, Hospital Clínico San Carlos. Madrid. España. myriammfag@hotmail.com.
Ciudad
M J
MJ
Cabeza
B
B
Méndez
R
R
D000328:Adult; D005260:Female; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D018191:Lymphangioma, Cystic / Q000175:diagnosis* / Q000209:etiology*; D008279:Magnetic Resonance Imaging; D013160:Splenic Neoplasms / Q000175:diagnosis* / Q000209:etiology*