Myxoid chondrosarcoma of the sinonasal cavity in a child: a case report.
Chondrosarcomas are malignant tumors of cartilage that rarely involve the sinonasal region, and myxoid chondrosarcoma is a rare histologic variant of chondrosarcoma that usually occurs in the soft tissue of extremities. Although several case reports and results of small series of chondrosarcomas in the sinonasal region in children are available, myxoid type chondrosarcoma is extremely rare. We recently experienced a case of low grade myxoid chondrosarcoma involving the sinonasal cavity in a 10-year-old boy, and here we report its radiologic-pathologic findings. In this case, chondroid calcification on CT and septal and marginal enhancement on MRI suggested a chondrosarcoma. Whole body PET-CT demonstrated no definite metastatic lesion and a low peak standardized uptake value primary tumor. However, no definite distinguishing imaging features were observed that distinguished low grade myxoid chondrosarcoma from conventional chondrosarcoma.
Kim
Yeo Ju
YJ
Department of Radiology, Kangnam St. Mary's Hospital, The Catholic University of Korea, Seoul, Korea.
Im
Soo Ah
SA
Lim
Gye-Yeon
GY
Chun
Ho Jong
HJ
Park
Hyun Jin
HJ
Kim
Min Sik
MS
Choi
Yeong Jin
YJ
D001859:Bone Neoplasms / Q000175:diagnosis* / Q000532:radiotherapy / Q000601:surgery; D002648:Child; D002813:Chondrosarcoma / Q000175:diagnosis* / Q000532:radiotherapy / Q000601:surgery; D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009236:Myxosarcoma / Q000175:diagnosis* / Q000532:radiotherapy / Q000601:surgery; D009296:Nasal Cavity / Q000000981:diagnostic imaging* / Q000473:pathology* / Q000601:surgery; D010256:Paranasal Sinuses / Q000000981:diagnostic imaging* / Q000473:pathology* / Q000601:surgery; D049268:Positron-Emission Tomography; D035583:Rare Diseases; D014057:Tomography, X-Ray Computed; D051598:Whole Body Imaging