Congenital cystic adenomatoid malformation type 0-a rare cause of neonatal death.
OBJECTIVE
We give the first account of failure of extracorporeal membrane oxygenation therapy secondary to congenital cystic malformation of the lung (CCAM) type 0.


METHODS
Case report.


METHODS
Pediatric intensive care unit.


METHODS
A female neonate, appropriate for gestational age, with respiratory failure immediately after delivery.


METHODS
: Cardiopulmonary support with venoarterial extracorporeal membrane oxygenation.


RESULTS
There was no improvement of pulmonary function, and the patient died. CCAM type 0 was diagnosed postmortem.


CONCLUSIONS
CCAM type 0 should be considered as a rare differential diagnosis of irreversible lung pathologies leading to failure of extracorporeal membrane oxygenation therapy for neonatal respiratory failure.
Stuhrmann
Stefan
S
Department of Pediatric Cardiology (SS, LB, MCS), Pediatric Cardiac Surgery (JS, JVJ), and Pathology (BHS), RWTH Aachen University, Aachen, Germany. sstuhrmann@ukaachen.de
Sachweh
Jörg
J
Bindl
Lutz
L
Vázquez-Jiménez
Jaime
J
Hermanns-Sachweh
Benita
B
Seghaye
Marie-Christine
MC
D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000175:diagnosis*; D015199:Extracorporeal Membrane Oxygenation; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007363:Intensive Care Units, Neonatal; D008168:Lung / Q000002:abnormalities / Q000473:pathology; D011379:Prognosis; D012131:Respiratory Insufficiency / Q000235:genetics* / Q000628:therapy; D017211:Treatment Failure