Correction of saddle nose deformity in ectodermal dysplasia.
Ectodermal dysplasia (ED) is a group of disorders affecting ectodermal-derived tissues, mainly the skin and its appendages, including teeth, nails, hair, and sweat glands. Along with unusual and typical craniofacial findings, these patients present with a unique nasal deformity. This consists of wide nasal base, saddle nose deformity, lack of alar grooves, and wide nostrils. We present a case of ED in which the nasal deformity was treated with bilateral nasal osteotomies, costochondral cartilage graft to the dorsum, and reforming of alar grooves by suturing.
Acarturk
Tahsin Oguz
TO
Department of Plastic, Reconstructive and Aesthetic Surgery, Cukurova University School of Medicine, Adana, Turkey. toacarturk@yahoo.com
Kivanc
Onder
O
D000328:Adult; D002356:Cartilage / Q000637:transplantation; D004476:Ectodermal Dysplasia / Q000150:complications* / Q000601:surgery; D005260:Female; D006801:Humans; D009666:Nose / Q000002:abnormalities* / Q000601:surgery; D012225:Rhinoplasty / Q000379:methods*