Massive gastrointestinal bleeding: an unusual case of asymptomatic extrarenal, visceral, fibromuscular dysplasia.
Extrarenal fibromuscular dysplasia causing gastro-intestinal bleeding without other manifestations and especially sparing renal vasculature is uncommon. The diagnosis of this entity is usually made by radiographic appearance and the treatment is controversial. To our knowledge only seven cases of visceral fibromuscular dysplasia as a primary manifestation of the disease have been described, symptoms range from abdominal pain to gangrene. This is the first case of visceral fibromuscular dysplasia presenting with otherwise asymptomatic gastrointestinal bleeding, without bowel necrosis or ischemic changes. We provide a review of the literature.
Rodriguez Urrego
Paula Andrea
PA
Pathology Department, New Brunswick NJ 08901, One Robert Wood Johnson PL. MEB 212, United States. rodrigp2@umdnj.edu
Flanagan
Mark
M
Tsai
Wilson S
WS
Rezac
Craig
C
Barnard
Nicola
N
D000328:Adult; D005352:Fibromuscular Dysplasia / Q000150:complications* / Q000175:diagnosis; D006471:Gastrointestinal Hemorrhage / Q000175:diagnosis / Q000209:etiology*; D006801:Humans; D006965:Hyperplasia; D007583:Jejunum / Q000098:blood supply / Q000473:pathology / Q000601:surgery; D008297:Male; D017539:Tunica Intima / Q000473:pathology