Papillary tumor of the pineal region in a child: case report and review of the literature.
METHODS
A 13-year-old boy presented with a history of intracranial hypertension. Radiologic studies revealed triventricular hydrocephalus secondary to a space-occupying lesion in the pineal region. Endoscopic third ventriculostomy was performed to treat hydrocephalus, and the lesion was biopsied. Complete resection of the tumor was subsequently performed. After a period of uncertainty, the diagnosis of papillary tumor of the pineal region was established. Tumor bed radiotherapy at a dose of 50 Gy was associated. With a follow-up of 15 months, the postoperative course was satisfactory with return to school and no residual tumor on magnetic resonance imaging.


CONCLUSIONS
Papillary tumors of the pineal region constitute a rare entity, with a difficult diagnosis, an uncertain prognosis, and a high risk of local recurrence; they must be treated by a combination of surgery and radiotherapy. The only identified prognostic factor is the complete or incomplete nature of surgical resection.
Buffenoir
Kévin
K
Service de Neurochirurgie, CHU de Poitiers, Poitiers, France. k.buffenoir@laposte.net
Rigoard
Philippe
P
Wager
Michel
M
Ferrand
Sarah
S
Coulon
Alix
A
Blanc
Jean Luc
JL
Bataille
Benoit
B
Listrat
Antoine
A
D000231:Adenocarcinoma, Papillary / Q000473:pathology* / Q000601:surgery; D001932:Brain Neoplasms / Q000473:pathology* / Q000601:surgery; D002291:Carcinoma, Papillary / Q000473:pathology* / Q000601:surgery; D002648:Child; D003937:Diagnosis, Differential; D004806:Ependymoma / Q000473:pathology* / Q000601:surgery; D006801:Humans; D019586:Intracranial Hypertension / Q000209:etiology; D008297:Male; D010871:Pinealoma / Q000473:pathology* / Q000601:surgery; D016896:Treatment Outcome