Plexiform neurofibroma of the penis associated with erectile dysfunction due to arterial steeling.
BACKGROUND
Solitary involvement of the genitourinary tract by Von Recklinghousen disease (VRD) is extremely rare.


OBJECTIVE
This report documents the management of a case of a plexiform neurofibroma on the penile shaft associated with erectile dysfunction. The literature surrounding VRD and its effects on the genital area was also investigated. Methods. After a complete preoperative investigation of the nature of the mass and of the erectile dysfunction, the neurofibroma was completely excised with preservation of the neurovascular bundle.


RESULTS
At 6-months postoperative follow-up, there was no sign of tumor recurrence and the glans sensation was maintained. The erectile dysfunction persisted postoperatively and failed to respond to medical treatment.


CONCLUSIONS
A complete excision of penile neurofibromas is mandatory to prevent recurrence or malignant degeneration and can be safely performed preserving the neurovascular bundle.
Garaffa
Giulio
G
St Peter's Department of Andrology, University College London Hospitals, London, UK. giuliogaraffa@libero.it
Bettocchi
Carlo
C
Christopher
Nim
N
Ralph
David
D
D000328:Adult; D019080:Cafe-au-Lait Spots / Q000209:etiology; D007172:Erectile Dysfunction / Q000209:etiology* / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D009456:Neurofibromatosis 1 / Q000175:diagnosis / Q000601:surgery*; D010412:Penile Neoplasms / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D010413:Penis / Q000294:innervation*; D016896:Treatment Outcome