[Unilateral pigmented paravenous retinochoroidal atrophy].
We report the case of an asymptomatic unilateral pigmented paravenous retinochoroidal atrophy (PPRCA) in a 43-year-old patient. The right eye showed chorioretinal atrophy with bone-spicule-like pigmentations along the retinal veins. Visual acuity was 20 / 20 and perimetry revealed scotomas correlating to the chorioretinal atrophy. Electrophysiological examination showed decreased signals in ERG and EOG. Fundus autofluorescence and angiography findings are presented. Pathogenetically, a classification as hereditary retinal dystrophy (as in retinitis pigmentosa) as well as a post-inflammatory residuum are discussed.
Charbel Issa
P
P
Universitäts-Augenklinik, Rheinische Friedrich-Wilhelms-Universität Bonn, Ernst-Abbe-Strasse 2, Bonn.
Scholl
H P
HP
Helb
H-M
HM
Fleckenstein
M
M
Inhetvin-Hutter
C
C
Holz
F G
FG
D000328:Adult; D001284:Atrophy; D002829:Choroid / Q000473:pathology*; D002921:Cicatrix / Q000473:pathology; D004596:Electroretinography; D005260:Female; D005451:Fluorescein Angiography; D005654:Fundus Oculi; D006801:Humans; D017495:Hyperpigmentation / Q000473:pathology*; D012160:Retina / Q000473:pathology*; D012169:Retinal Vein / Q000473:pathology*; D012170:Retinal Vein Occlusion / Q000473:pathology; D014794:Visual Fields / Q000502:physiology