Allgrove syndrome.
Allgrove syndrome consists of triad of Adrenal hypoplasia, Achalasia cardia and Alacrimia. Often the first manifestation of adrenal hypoplasia is Addisonian crisis precipitated by infection or trauma. We present case of a 9-year-old boy who presented in shock due to adrenal failure later confirmed to have Allgove syndrome.
Kasar
P A
PA
Department of Pediatrics, Bombay Hospital Institute Of Medical Sciences And Research Centre, Mumbai, India.
Khadilkar
V V
VV
Tibrewala
V N
VN
D000224:Addison Disease / Q000175:diagnosis / Q000188:drug therapy / Q000235:genetics*; D002648:Child; D003937:Diagnosis, Differential; D004334:Drug Administration Schedule; D004931:Esophageal Achalasia / Q000175:diagnosis / Q000188:drug therapy / Q000235:genetics*; D006801:Humans; D006854:Hydrocortisone / Q000008:administration & dosage / Q000097:blood; D007766:Lacrimal Apparatus Diseases / Q000175:diagnosis / Q000188:drug therapy / Q000235:genetics*; D008297:Male; D013577:Syndrome
D006854:Hydrocortisone