Scleral infiltration in orbitotemporal plexiform neurofibromatosis.
We report a case of severe orbitotemporal plexiform neurofibromatosis with a unique observation of clinically evident scleral infiltration, without uveal involvement, in a non-buphthalmic eye. We emphasize the importance of recognizing this before debulking surgery.
Then
Siew-Yin
SY
De Sousa
Jean-Louis
JL
Chandrasekharan
Lekha
L
Francis
Ian
I
Malhotra
Raman
R
D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D033401:Microscopy, Acoustic; D008875:Middle Aged; D009361:Neoplasm Invasiveness; D009456:Neurofibromatosis 1 / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D013508:Ophthalmologic Surgical Procedures; D009918:Orbital Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D015422:Scleral Diseases / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D012888:Skull Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D013701:Temporal Bone / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D014057:Tomography, X-Ray Computed