Life-long follow-up in congenitally corrected transposition.
A male patient with congenitally corrected transposition, with no associated cardiac malformations, was diagnosed in childhood and followed until his death at age 28. He underwent two cardiac gated single photon emission computed tomographies over a two year period, which demonstrated progression of ischaemia and reduction of systolic function. The findings suggest that, when the systemic ventricle is perfused by the morphologically right coronary artery, there may be inadequate perfusion to supply any subsequent extensive hypertrophy.
Shih
Wei-Jen
WJ
Nuclear Medicine Service, Lexington Veterans Administration Medical Center, Lexington, KY 40502, USA. wshih0@uky.edu
Noonan
Jacqueline A
JA
Mazzoleni
Alberto
A
D006328:Cardiac Catheterization; D002648:Child; D003937:Diagnosis, Differential; D004452:Echocardiography; D004562:Electrocardiography; D017809:Fatal Outcome; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D049268:Positron-Emission Tomography; D012720:Severity of Illness Index; D013997:Time Factors; D014188:Transposition of Great Vessels / Q000175:diagnosis*