Near-total mandible reconstruction with a single fibula flap containing fibrous dysplasia in McCune Albright Syndrome.
We present the case of an 18-year-old girl with McCune Albright Syndrome (MAS) and a near total mandibular defect reconstructed with a free fibula flap. There are three reports of mandibular reconstruction in a patient with MAS using the free fibula flap; however this case is unique for two reasons. One, the continuity defect in our patient was much larger than previously reported, representing nearly the entire length of the mandible (21 cm) and required the entire harvestable length of the fibula. Two, the progression of the patient's disease limited options for reconstruction and dictated the use of a fibula with small dysplastic changes.
Rodriguez
Eduardo D
ED
R Adams Cowley Shock Trauma Center, University of Maryland Medical Center, Baltimore, Maryland 21201, USA. erodriguez@umm.edu
Bluebond-Langner
Rachel
R
Brazio
Philip
P
Collins
Michael
M
D000293:Adolescent; D001860:Bone Plates; D016025:Bone Transplantation; D005260:Female; D005359:Fibrous Dysplasia, Polyostotic / Q000150:complications*; D006801:Humans; D008339:Mandibular Neoplasms / Q000209:etiology* / Q000601:surgery; D009364:Neoplasm Recurrence, Local / Q000601:surgery; D019647:Oral Surgical Procedures / Q000379:methods; D012516:Osteosarcoma / Q000209:etiology* / Q000601:surgery; D019651:Plastic Surgery Procedures / Q000379:methods*; D013524:Surgical Flaps