Heart-lung transplantation in a 14-year-old boy with Alström syndrome.
We present a 14-year-old boy who suffered from progressive biventricular cardiac failure and secondary pulmonary artery hypertension associated with the rarely seen Alström syndrome. The boy underwent successful heart-lung transplantation. We conclude from this report that heart-lung transplantation in patients with Alström syndrome is a viable therapeutic option in select cases.
Goerler
Heidi
H
Division of Cardiac, Thoracic, Transplantation and Vascular Surgery, Hannover Medical School, Hannover, Germany. goerler.adelheid@mh-hannover.de
Warnecke
Gregor
G
Winterhalter
Michael
M
Müller
Carsten
C
Ballmann
Manfred
M
Wessel
Armin
A
Haverich
Axel
A
Strüber
Martin
M
Simon
Andre
A
D000293:Adolescent; D002311:Cardiomyopathy, Dilated / Q000150:complications* / Q000235:genetics; D003638:Deafness / Q000150:complications / Q000235:genetics; D006333:Heart Failure / Q000209:etiology* / Q000601:surgery*; D016041:Heart-Lung Transplantation; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology* / Q000601:surgery*; D008297:Male; D009765:Obesity / Q000150:complications / Q000235:genetics; D012162:Retinal Degeneration / Q000150:complications / Q000235:genetics; D013577:Syndrome