title: Case report: cochlear implant in a child with schizencephaly and cortical dysplasia.
abstract: Schizencephaly is a developmental disorder of the cerebral cortex, usually with seizures occurring before the age of 3. We describe pre-implantation considerations and post-implantation outcome in a child with schizencephaly and bilateral profound hearing loss. Cochlear implantation was performed in the right ear when she was 21 months old. At 4 years and 3 months she developed an epileptic pattern on electroencephalogram and had mild attacks of dysesthesia. Now aged 6, she uses the implant successfully and needs no anticonvulsant medication. Language skills, though delayed, are progressing steadily. We consider that the epileptic pattern was unrelated to the electrical stimulation, and conclude that implantation is not contraindicated in children with cortical anomalies.
authors.affiliation: Department of Otolaryngology, Head and Neck Surgery, Bnai-Zion Medical Center, The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
authors.forename: Lena
authors.initials: L
authors.lastname: Koren
authors.forename: Talma
authors.initials: T
authors.lastname: Shpak
authors.forename: Hava
authors.initials: H
authors.lastname: Duchman
authors.forename: Michal
authors.initials: M
authors.lastname: Luntz
mesh_terms: D002648:Child; D002675:Child, Preschool; D003054:Cochlear Implants; D000075202:Contraindications; D003638:Deafness / Q000503:physiopathology / Q000534:rehabilitation*; D004569:Electroencephalography; D017034:Epilepsy, Frontal Lobe / Q000503:physiopathology; D004833:Epilepsy, Temporal Lobe / Q000503:physiopathology; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D054220:Malformations of Cortical Development / Q000175:diagnosis / Q000503:physiopathology*; D010292:Paresthesia / Q000503:physiopathology; D012075:Remission, Spontaneous; D014057:Tomography, X-Ray Computed