title: Management of bilateral congenital bronchial stenosis in an infant.
abstract: Congenital bronchial stenosis is a very uncommon condition in children. A full-term neonate showed severe respiratory distress soon after birth. Bronchoscopy and spiral computed tomography with multiplanar reconstruction disclosed a short stenosis of the left main bronchus, next to the carina, and another stenosis in the intermediate bronchus with air trapping in the right middle and lower lobes. The child underwent resection and reconstruction of the left main bronchus, and right middle and lower lobectomies after a failed attempt of bronchoscopic dilatation of the intermediate bronchus. A temporary silicon tracheal stent was necessary to achieve permanent extubation. The patient was discharged in good condition without any oxygen dependency and remains asymptomatic 1 year after surgery. Management of children with airway stenosis is complex, and surgeons involved in it should be familiar with multiple surgical and endoscopic techniques. A team approach in a referral center is the best option to achieve an optimal result.
authors.affiliation: Pediatric Airway Unit and Division of Pediatric Surgery, Madrid, Spain. janton.hdoc@salud.madrid.org
authors.forename: Juan L
authors.initials: JL
authors.lastname: Antón-Pacheco
authors.forename: Lorenzo
authors.initials: L
authors.lastname: Galletti
authors.forename: Daniel
authors.initials: D
authors.lastname: Cabezalí
authors.forename: Carmen
authors.initials: C
authors.lastname: Luna
authors.forename: Gabino
authors.initials: G
authors.lastname: González de Orbe
authors.forename: Manuel
authors.initials: M
authors.lastname: Sánchez-Solis de Querol
mesh_terms: D000402:Airway Obstruction / Q000151:congenital / Q000175:diagnosis / Q000601:surgery; D001980:Bronchi / Q000002:abnormalities*; D001982:Bronchial Diseases / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery*; D001999:Bronchoscopy / Q000379:methods; D002315:Cardiopulmonary Bypass / Q000379:methods; D003251:Constriction, Pathologic / Q000151:congenital / Q000175:diagnosis / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D011013:Pneumonectomy / Q000379:methods*; D035583:Rare Diseases; D019651:Plastic Surgery Procedures / Q000379:methods*; D015619:Respiratory System Abnormalities / Q000175:diagnosis / Q000601:surgery*; D018570:Risk Assessment; D013908:Thoracotomy / Q000379:methods; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome