Pericardial PEComa: echocardiographic features.
The patient was a 19 year old man referred to our center due to progressive effort dyspnea and left sided pleuritic chest pain for 1 month. Echocardiographic examination showed a posteriorly located, giant, well demarcated mass, that compresses the left atrium. It was encased by moderate pericardial effusion. Histhopathological analysis disclosed neoplastic cells arranged around blood vessels with immunoreactivity for HMB-45 indicative of PEComa (Perivascular Epitheloid Cell differentiation). Six month follow up was uneventful. Up to the best of our knowledge, this is the first case of pericardial PEComa reported in the literature.
Mollazadeh
Reza
R
Moaref
Ali Reza
AR
Ghazinoor
Mohammad
M
Sefidbakht
Salma
S
Bigi
Mohammad Ali Babai
MA
Geramizadeh
Bita
B
Shahrzad
Shahab
S
Mahmoodi
Yadollah
Y
D002637:Chest Pain; D004417:Dyspnea; D004452:Echocardiography; D017548:Echocardiography, Transesophageal; D017809:Fatal Outcome; D006338:Heart Neoplasms / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D010490:Pericardial Effusion / Q000000981:diagnostic imaging / Q000209:etiology; D010496:Pericardium; D054973:Perivascular Epithelioid Cell Neoplasms / Q000000981:diagnostic imaging*; D055815:Young Adult