Seminal vesicle cysts with unilateral renal agenesis and contralateral ureteral stenosis in a beta-thalassemic patient: an unknown association by incomplete development of the mesonephric duct.
We report the case of a 13-year-old male patient with beta-thalassemic trait who presented for a colic pain. An ultrasound of the abdomen revealed absence of the right kidney with a complex hypoechogenic pelvic mass causing mild pressure on the posterior bladder wall. Urography showed hypertrophy of the left kidney with moderate ureteral enlargement of the distal third due to an insertion defect in the bladder suggestive of a primary segmental nonobstructing megaureter. MR studies showed right multilocular seminal vesicle cysts. One year later an MR examination of the pelvis showed an increase in size of seminal vesicle cysts and open surgery was performed to remove the cystic retrovesical mass. Our case represents a very rare association of seminal vesicle cysts, unilateral renal agenesis and alteration in contralateral ureteral insertion in a patient with beta-thalassemic trait.
Savica
V
V
Chair of Nephrology, University of Messina, Messina, Italy.
Santoro
D
D
Monardo
P
P
Ciolino
F
F
Magistro
A
A
Blandino
A
A
Bellinghieri
G
G
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D000293:Adolescent; D003560:Cysts / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D007668:Kidney / Q000002:abnormalities / Q000601:surgery; D010535:Laparoscopy / Q000379:methods; D008279:Magnetic Resonance Imaging; D008297:Male; D012669:Seminal Vesicles / Q000002:abnormalities* / Q000601:surgery; D014057:Tomography, X-Ray Computed; D018608:Ultrasonography, Doppler; D014517:Ureteral Obstruction / Q000150:complications / Q000175:diagnosis*; D014564:Urogenital Abnormalities / Q000175:diagnosis; D014567:Urography; D014928:Wolffian Ducts / Q000002:abnormalities*; D017086:beta-Thalassemia / Q000150:complications / Q000175:diagnosis*