Klippel-Feil syndrome and Sprengel deformity combined with an intraspinal course of the left subclavian artery and a bovine aortic arch variant.
We present a case of Klippel-Feil syndrome and Sprengel deformity with a bovine aortic arch and an aberrant course of the left subclavian artery in a 14-year-old boy. CT and MR imaging of the neck and upper thorax demonstrated a cervical osseous segmentation anomaly, a left common carotid artery originating from the innominate artery, and a left subclavian artery coursing through the intraspinal space at the C6 through T1 level. Possible embryonic mechanisms and clinical significance of this variant are reviewed.
Floemer
F
F
Department of Pediatric Radiology, University Children's Hospital Basel, Basel, Switzerland.
Magerkurth
O
O
Jauckus
C
C
Lütschg
J
J
Schneider
J F
JF
D000293:Adolescent; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology; D002574:Cervical Vertebrae / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology; D006801:Humans; D007714:Klippel-Feil Syndrome / Q000175:diagnosis*; D008279:Magnetic Resonance Imaging; D008297:Male; D012540:Scapula / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology; D013348:Subclavian Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology; D014057:Tomography, X-Ray Computed