Non-vascular vision loss in pseudoxanthoma elasticum.
Pseudoxanthoma elasticum patients with angioid streaks are well-known to have acute vision loss due to choroidal bleeding. However, chronic vision loss due to macular atrophy is less well characterized. We describe a patient with sub-acute vision loss in one eye due to loss of macular retinal pigment epithelium function. Autofluorescence and pattern electroretinogram were useful adjuncts to help diagnose the source of her vision loss.
Tsui
Irena
I
Department of Ophthalmology, Edward Harkness Eye Institute, 635 West 165th Street, New York, NY 10032, USA. irena.tsui@gmail.com
Fuchs
Brian S
BS
Chou
Chai Lin
CL
Chang
Stanley
S
Tsang
Stephen H
SH
D000368:Aged; D000793:Angioid Streaks / Q000150:complications / Q000175:diagnosis; D001284:Atrophy; D004596:Electroretinography; D005260:Female; D005451:Fluorescein Angiography; D006801:Humans; D010857:Pigment Epithelium of Eye / Q000473:pathology*; D011561:Pseudoxanthoma Elasticum / Q000150:complications* / Q000175:diagnosis; D014786:Vision Disorders / Q000175:diagnosis / Q000209:etiology*; D014792:Visual Acuity