Churg-Strauss syndrome presenting as an abdominal mass in a non-asthmatic child.
A 2-year-old boy presented with an abdominal mass and was diagnosed as Churg-Strauss syndrome (CSS). There was no history of asthma. He developed fatal gastro-intestinal disease, despite treatment with corticosteroids and cyclophosphamide. CSS is extremely rare in young children and gastro-intestinal involvement might carry a worse prognosis than in adults.
Hamdan
Mohamed A
MA
Department of Paediatrics, Tawam-Johns Hopkins Hospital, UAE University, Al Ain, United Arab Emirates. mhamdan@tawam-hosp.gov.ae
Al-Rumaithi
Sareea
S
Tolaymat
Naser
N
Ionescu
Gabriel
G
Al-Ashari
Moueid
M
El-Teraifi
Hassan
H
D000893:Anti-Inflammatory Agents / Q000627:therapeutic use; D002675:Child, Preschool; D015267:Churg-Strauss Syndrome / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D003520:Cyclophosphamide / Q000627:therapeutic use; D004359:Drug Therapy, Combination; D017809:Fatal Outcome; D005767:Gastrointestinal Diseases / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use; D008297:Male; D008775:Methylprednisolone / Q000627:therapeutic use; D011379:Prognosis; D012772:Shock, Septic / Q000209:etiology
D000893:Anti-Inflammatory Agents; D007166:Immunosuppressive Agents; D003520:Cyclophosphamide; D008775:Methylprednisolone