Primary pleural synovial sarcoma presenting as a multiloculated cyst in an adolescent.
Primary pleural synovial sarcoma (PPSS) is a rare pleural malignancy with a grave prognosis. Most cases present as a well-circumscribed mass with foci of haemorrhage and necrosis. We present an unusual case in a Nepalese boy that presented as a multiloculated cyst mimicking hydatid disease. The diagnosis was confirmed by histology and cytogenetic analysis.
Department of Paediatric Surgery, John Radcliffe Hospital, Headington, Oxford, OX39DU, UK.
J
J
Tailor
P G
PG
Roy
C
C
Bowker
K
K
Lakhoo
D000293:Adolescent; D003560:Cysts / Q000175:diagnosis*; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D010997:Pleural Neoplasms / Q000175:diagnosis* / Q000601:surgery; D013584:Sarcoma, Synovial / Q000175:diagnosis* / Q000601:surgery; D013908:Thoracotomy / Q000379:methods; D014057:Tomography, X-Ray Computed