Tracheomalacia in a patient with unilateral pulmonary and renal agenesis.
We report the case of an eight-month-old boy with tracheomalacia secondary to impingement by the right pulmonary artery, together with congenital agenesis of the left lung and the left kidney. Aortopexy and right pulmonary arterypexy were successful in improving lung function by more than 100%, and the patient remained free of complications in the long term.
Division of Cardiothoracic Surgery, Department of Surgery, The Aga Khan University Hospital, Karachi, Pakistan.
Saulat
S
Fatimi
Sadaf
S
Sheikh
Zaman
Z
Shah
Sonia
S
Fatimi
D000015:Abnormalities, Multiple / Q000601:surgery; D006801:Humans; D007223:Infant; D007668:Kidney / Q000002:abnormalities*; D008168:Lung / Q000002:abnormalities* / Q000503:physiopathology; D008297:Male; D008482:Mediastinum / Q000601:surgery; D010496:Pericardium / Q000601:surgery; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D012129:Respiratory Function Tests; D014133:Tracheal Diseases / Q000175:diagnosis* / Q000209:etiology / Q000503:physiopathology / Q000601:surgery; D016896:Treatment Outcome