Progressive facial hemiatrophy with associated osseous lesions.
Progressive facial hemiatrophy (PFH) is a rare condition characterized by the slow, progressive appearance of a unilateral facial atrophy that affects the skin, subcutaneous tissue, muscle and bone. We report the case of a 60-year-old female patient whose cutaneous symptoms commenced in 1987 in the form of a purplish erythema on the left side of her face and neck, which subsequently remitted giving rise to an indurated region in the left maxillary region. Since 1995 until the present day, she has developed facial hemiatrophy on the left side accompanied by progressive osseous reabsorption of the upper maxilla and left mandible with atrophy of soft tissue. The association of the onset of PFH with progressive osteolysis of the maxilla has not been previously reported in an adult patient.
Médico-adjunto, Servicio de Dermatología.
Santiago Gómez
SG
Gomez-Diez
Lorena Gallego
LG
López
María López
ML
Escobar
Luis Junquera
LJ
Gutiérrez
Narciso Pérez
NP
Oliva
D000368:Aged; D001862:Bone Resorption / Q000209:etiology*; D005150:Facial Hemiatrophy / Q000150:complications*; D005260:Female; D006801:Humans; D007571:Jaw Diseases / Q000209:etiology*; D008875:Middle Aged