A variant of Poland syndrome associated with dextroposition.
Poland syndrome is characterized by partial or complete absence of pectoralis muscles, ipsilateral syndactyly, and occasionally other malformations of the anterior chest wall and breast. Other associated anomalies, including dextrocardia, renal malformations, and vertebral anomalies, have been reported in rare cases. The condition is more frequent among males, and usually occurs on the right hemithorax in the unilateral form. The syndrome is believed to be caused by a genetic disorder that reduces the embryonal circulation in the subclavian and vertebral arteries. We report a 20-year-old man with Poland syndrome on the left hemithorax, which is rarely associated with dextroposition.
Mutlu
Hakan
H
Gulhane Military Medical Academy, Haydarpasa Teaching Hospital, Department of Radiology, Istanbul, Turkey. hakanmutlu1@yahoo.com
Sildiroglu
Onur
O
Basekim
Cinar C
CC
Kizilkaya
Esref
E
D000328:Adult; D003914:Dextrocardia / Q000000981:diagnostic imaging*; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D011045:Poland Syndrome / Q000000981:diagnostic imaging*; D014057:Tomography, X-Ray Computed