Riga-Fede disease associated with postanoxic encephalopathy and trisomy 21: a proposed classification.
We present a new instance of Riga-Fede disease in a 2-year-old boy with Down syndrome and postanoxic encephalopathy. We propose a classification of the disease, as either "precocious," associated with natal or neonatal teeth or "late-onset," associated with neurologic disease.
HUV Macarena, Department of Dermatology, AV Doctor Fedriani no 3, Sevilla, 41071, Spain. drdominguezcruz@yahoo.es
Javier
J
Domingues-Cruz
Alberto
A
Herrera
Pablo
P
Fernandez-Crehuet
Begona
B
Garcia-Bravo
Francisci
F
Camacho
D002675:Child, Preschool; D004314:Down Syndrome / Q000150:complications*; D006099:Granuloma / Q000209:etiology* / Q000473:pathology; D006323:Heart Arrest / Q000150:complications; D006801:Humans; D020925:Hypoxia-Ischemia, Brain / Q000150:complications*; D008046:Lip / Q000293:injuries* / Q000473:pathology; D008297:Male; D009059:Mouth Diseases / Q000145:classification* / Q000209:etiology / Q000473:pathology; D009061:Mouth Mucosa / Q000293:injuries* / Q000473:pathology; D013391:Sucking Behavior; D014081:Tooth Extraction