Case study: a minimally invasive approach to the treatment of Klippel-Trenaunay syndrome.
Klippel-Trenaunay syndrome (KTS) is a congenital developmental disorder characterized by port wine stain, venous abnormalities, soft tissue, and bony deformities of the affected extremity. It is usually diagnosed in early childhood and has many long-term sequelae. Patients not only have physical health problems but also must learn to cope with psychosocial factors that will affect their self-esteem and interpersonal relationships. This article describes the syndrome of KTS and the minimally invasive techniques used in the treatment of superficial varicosities in patients with reasonably mild KTS with an intact deep venous system. Treating the varicosities relatively early to avoid the long-term complications of chronic venous insufficiency may improve the quality of life, maintain limb function, and decrease the risk of long-term venous complications.
Heart and Vascular Institute, Lenox Hill Hospital, 130 East 77th Street, New York, NY 10021, USA. VLatessa@LENOXHILL.NET
Victoria
V
Latessa
Krista
K
Frasier
D000223:Adaptation, Psychological; D000293:Adolescent; D001294:Attitude to Health; D001828:Body Image; D017115:Catheter Ablation; D005260:Female; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000175:diagnosis / Q000209:etiology / Q000628:therapy*; D053685:Laser Therapy; D019060:Minimally Invasive Surgical Procedures / Q000379:methods* / Q000451:nursing; D009722:Nurse Practitioners / Q000458:organization & administration; D024802:Nurse's Role / Q000523:psychology; D010348:Patient Care Team / Q000458:organization & administration; D011320:Primary Health Care; D035583:Rare Diseases; D012017:Referral and Consultation; D015911:Sclerotherapy; D018084:Ultrasonography, Interventional