Basal encephalocele associated with morning glory syndrome: case report.
The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagnosed transsphenoidal encephalocele associated with morning glory syndrome, showing the alterations found in retinography, computed tomography and magnetic resonance imaging.
Minotto
Ivanete
I
Neuroradiology Ward, Image Diagnoses Department, Federal University of São Paulo, SP, Brazil.
Abdala
Nitamar
N
Miachon
Adriana Aparecida Siviero
AA
Spinola e Castro
Angela Maria
AM
Imamura
Paulo
P
Nogueira
Roberto Gomes
RG
D002648:Child; D004393:Dwarfism, Pituitary / Q000150:complications* / Q000175:diagnosis; D004677:Encephalocele / Q000150:complications* / Q000175:diagnosis; D005654:Fundus Oculi; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009898:Optic Disk / Q000002:abnormalities* / Q000473:pathology; D013577:Syndrome; D014057:Tomography, X-Ray Computed