Longitudinal epiphyseal bracket.
A longitudinal epiphyseal bracket (LEB) is a defect of the tubular bones and has been primarily described in the hands and feet, especially the proximal phalanges, metacarpals, and metatarsals. The LEB results from a defective C-shaped secondary ossification center that brackets the diaphysis and metaphysis, causing restricted longitudinal growth in these bones with resultant shortening and angular deformities. Deformities associated with metatarsal epiphyseal bracket include a short, broad metatarsal and medial deviation of the metatarsophalangeal joint (hallux varus deformity). Excision of the cartilaginous LEB has been proposed to prevent future soft tissue contractures and osseous deformities. The LEB has been associated with numerous syndromes including Rubinstein-Taybi syndrome, Cenani-Lenz syndactyly, isolated oligosyndactyly, and Nievergelt syndrome. We describe a two-month-old patient in whom plain film and MR imaging demonstrated bilateral bracketed first metatarsals with associated hallux varus deformities. Bilateral bracket excision was performed with excellent clinical results.
Nguyen
Jimmy Q
JQ
Gatewood
Jason B
JB
Beall
Douglas
D
Herndon
William
W
Puffinberger
William R
WR
Ly
Justin
J
Fish
Jon R
JR
D001848:Bone Diseases, Developmental; D004838:Epiphyses / Q000002:abnormalities* / Q000601:surgery; D005260:Female; D050488:Hallux Varus / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008682:Metatarsal Bones / Q000002:abnormalities*; D009999:Ossification, Heterotopic