Dabska tumor arising in lymphangioma circumscriptum.
We describe a case of Dabska tumor (DT) occurring within a large congenital lymphangioma circumscriptum on the thigh of a 14-year-old female. Diagnostic biopsy showed numerous intravascular papillary projections lined by atypical endothelial cells within the anastomosing vascular channels of a lymphangioma circumscriptum. DT is regarded as a vascular tumor of intermediate malignant potential, most probably of lymphatic origin. Although it has been described in pre-existing lymphangiomas, to the best of our knowledge this is the first case to be described in a pre-existing lymphangioma circumscriptum. During a follow-up of 9 years, the lymphangioma circumscriptum has recurred, but there has been no evidence of DT recurrence or metastasis.
Emanuel
Patrick O
PO
Department of Dermatopathology, Mount Sinai Medical Center, New York, NY 10128, USA. patrick.emanuel@mssm.edu
Lin
Robert
R
Silver
Lester
L
Birge
Miriam B
MB
Shim
Helen
H
Phelps
Robert G
RG
D000293:Adolescent; D005260:Female; D005500:Follow-Up Studies; D006394:Hemangiosarcoma / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008202:Lymphangioma / Q000473:pathology* / Q000601:surgery; D009364:Neoplasm Recurrence, Local; D009378:Neoplasms, Multiple Primary