[Chronic inflammatory demyelinating polyneuropathy (CIDP) revealing an associated disease diagnostic and therapeutic pitfalls].
The objective of this case report is to illustrate the problem's diagnosis of a CIDP revealing a associated disease. The patient had initially a sensory CIDP wich respond to prednisone. After 2 years, he worsened with motor deficit, pain and atypical skin's lesions. The diagnosis of POEMS syndrome was made only in the fourth research of monoclonal gammopathy. A specific treatment was realised but too late and a important motor deficit with axonal loss unfortunately persisted.
Maisonobe
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Fédération de Neurophysiologie Clinique, Hôpital Pitié-Salpêtrière, AP-HP et Université Paris VI, 47-83, boulevard de l'Hôpital, 75013 Paris, France. thierry.maisonobe@psl.aphp.fr
Jaccard
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D000890:Anti-Infective Agents / Q000627:therapeutic use; D004568:Electrodiagnosis; D006801:Humans; D006983:Hypertrichosis / Q000150:complications / Q000473:pathology; D008297:Male; D008475:Median Nerve / Q000503:physiopathology; D008875:Middle Aged; D009046:Motor Neurons / Q000502:physiology; D009431:Neural Conduction / Q000502:physiology; D010000:Osteitis / Q000150:complications / Q000000981:diagnostic imaging; D016878:POEMS Syndrome / Q000175:diagnosis* / Q000000981:diagnostic imaging; D020277:Polyradiculoneuropathy, Chronic Inflammatory Demyelinating / Q000150:complications* / Q000175:diagnosis* / Q000188:drug therapy; D011241:Prednisone / Q000627:therapeutic use; D011859:Radiography; D012867:Skin / Q000473:pathology
D000890:Anti-Infective Agents; D011241:Prednisone