title: Focal nodular hyperplasia in biliary atresia patient after Kasai hepatic portoenterostomy.
abstract: We present the case of a 10-year-old girl with biliary atresia in whom focal nodular hyperplasia (FNH) of the liver occurred following successful "Kasai" hepatic portoenterostomy at the age of 2 months. Her jaundice completely disappeared a few weeks after the operation. A 4-cm diameter liver tumor in segment IV was found when she was 5-years old. Needle biopsy could not establish a definitive diagnosis. Because the tumor size was not changing, she was conservatively followed by abdominal echo at an outpatient clinic. She showed progressive liver dysfunction and ongoing cirrhosis, and so at the age of 10 years, she received living donor liver transplantation at our institute. The tumor was pathologically diagnosed as a FNH. Though a FNH in biliary atresia patients is extremely rare, there are only two cases reported in the literature; it should be considered in the differential diagnosis for a hepatic nodule during a long follow-up course in patients with biliary atresia.
authors: Department of Gastrointestinal and Pediatric Surgery, Mie University Graduate School of Medicine, Tsu, Mie, 514-8507, Japan. yosinaga@clin.medic.mie-u.ac.jp
authors: Yoshinaga
authors: Y
authors: Okugawa
authors: Keiichi
authors: K
authors: Uchida
authors: Mikihiro
authors: M
authors: Inoue
authors: Aya
authors: A
authors: Kawamoto
authors: Kohei
authors: K
authors: Ohtake
authors: Hiroshi
authors: H
authors: Sakurai
authors: Katsunori
authors: K
authors: Uchida
authors: Shuji
authors: S
authors: Isaji
authors: Chikao
authors: C
authors: Miki
authors: Masato
authors: M
authors: Kusunoki
mesh_terms: D001653:Bile Ducts, Intrahepatic; D001656:Biliary Atresia / Q000601:surgery*; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D020518:Focal Nodular Hyperplasia / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D016031:Liver Transplantation; D008279:Magnetic Resonance Imaging; D011171:Portoenterostomy, Hepatic / Q000009:adverse effects*; D011183:Postoperative Complications