Unilateral congenital facial nerve paralysis secondary to a benign epithelioid peripheral nerve sheath tumor.
OBJECTIVE
A benign epithelioid peripheral nerve sheath tumor is described in the setting of congenital facial nerve (FN) paralysis. This is the first reported case in the English literature.


METHODS
A 10-month-old girl with unilateral congenital FN paralysis.


METHODS
Auditory brainstem evoked potential study, gadolinium-enhanced magnetic resonance imaging, temporal bone computed tomography, and transmastoid FN decompression with tumor resection.


METHODS
Follow-up for tumor recurrence and postoperative FN function.


RESULTS
The child underwent a transmastoid FN exploration with resection of a 0.6-cm spherical tumor analyzed to be a benign epithelioid peripheral nerve sheath tumor. There is no evidence of recurrence, and FN function was unchanged at 1 year postoperatively.


CONCLUSIONS
Benign epithelioid peripheral nerve sheath tumor can cause congenital facial nerve palsy.
Ondik
Michael P
MP
Division of Otolaryngology-Head and Neck Surgery, Penn State Milton S. Hershey Medical Center, Hershey, Pennsylvania, USA.
Preston
Todd
T
Towfighi
Javad
J
Isaacson
Jon E
JE
D019299:Decompression, Surgical; D016057:Evoked Potentials, Auditory, Brain Stem / Q000502:physiology; D005154:Facial Nerve / Q000502:physiology; D005155:Facial Nerve Diseases / Q000151:congenital* / Q000209:etiology*; D005158:Facial Paralysis / Q000151:congenital / Q000209:etiology; D005260:Female; D005682:Gadolinium; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D009375:Neoplasms, Glandular and Epithelial / Q000150:complications* / Q000151:congenital* / Q000473:pathology; D018317:Nerve Sheath Neoplasms / Q000150:complications* / Q000151:congenital* / Q000473:pathology; D011859:Radiography; D013701:Temporal Bone / Q000000981:diagnostic imaging
D005682:Gadolinium