title: Lymphocytic bronchiolitis as presenting disorder in an undiagnosed adult patient with chronic granulomatous disease.
abstract: Chronic Granulomatous Disease (CGD) is a rare primary immunodeficiency disease. Although the most affected patients are diagnosed in childhood, there are several reports of the disease presenting in adult patients. Here we present a 40 years old man who was admitted in hospital due to respiratory symptoms and ground glass pattern in high resolution computed tomography of lung. Open lung biopsy revealed lymphocytic bronchiolitis. Because of past medical history of granulomatous lesion in lung and recurrent abscesses of skin and soft tissue, NBT test was conducted which its result revealed that the disorder was compatible with CGD and then it was confirmed by fluorescent cytometry.
authors: National Research Institute of TB and Lung disease, Niavaran-Darabad, Massih Daneshvari Hospital, Tehran, Iran. tabarsi@nritld.ac.ir
authors: Payam
authors: P
authors: Tabarsi
authors: Mehdi
authors: M
authors: Mirsaeidi
authors: Shirin
authors: S
authors: Karimi
authors: Behzad
authors: B
authors: Banieghbal
authors: Nahal
authors: N
authors: Mansouri
authors: Mohammad Reza
authors: MR
authors: Masjedi
authors: Davood
authors: D
authors: Mansouri
mesh_terms: D000328:Adult; D001988:Bronchiolitis / Q000150:complications* / Q000473:pathology; D006105:Granulomatous Disease, Chronic / Q000150:complications* / Q000473:pathology; D006801:Humans; D008168:Lung / Q000473:pathology*; D008214:Lymphocytes / Q000473:pathology*; D008232:Lymphoproliferative Disorders / Q000150:complications* / Q000473:pathology; D008297:Male