title: Splenic papillary angioendothelioma in a 6-year-old girl.
abstract: Papillary angioendothelioma is a rare, low-grade neoplasm of lymphatic channels that usually presents intradermally. We report the case of a 6-year-old girl with isolated splenomegaly and symptoms of early satiety and weight loss, whom was found to have a splenic papillary angioendothelioma. Preoperative abdominal computed tomography scan showed an irregular, heterogeneous mass; a tagged red cell scan ruled out a hemangioma, whereas a positron emission tomography scan showed mildly increased uptake. Subsequent surgery and pathologic assessment revealed a papillary angioendothelioma (Dabska tumor) within lymphatic spaces. The child has no evidence of recurrence or metastases 1 year postoperatively.
authors: Department of Radiology , Tulane School of Medicine, New Orleans, LA, USA. b71@bellsouth.net
authors: Brian
authors: B
authors: Rodgers
authors: Sam
authors: S
authors: Zeim
authors: Byron
authors: B
authors: Crawford
authors: Harold
authors: H
authors: Neitzschman
authors: Philip
authors: P
authors: Daroca
authors: Charles D
authors: CD
authors: Scher
mesh_terms: D002648:Child; D005260:Female; D006390:Hemangioendothelioma / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery*; D006801:Humans; D049268:Positron-Emission Tomography; D013160:Splenic Neoplasms / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome