Thrombosis of temporal artery and renal vein in Kimura-disease-related nephrotic syndrome.
Kimura disease (KD) is an angiolymphoid proliferative disorder of unknown etiology, occurs mainly in Asian patients, presenting with subcutaneous slowly growing masses, with a predilection for preauricular and submandibular regions. The clinical course of the disease is thought to be benign. Concomitant peripheral blood eosinophilia and elevated serum immunoglobulin E levels are often observed. Main systemic manifestation of the KD is renal involvement. Renal abnormalities, notably proteinuria and nephrotic syndrome have been found to be associated with KD. We report a 42-year-old man with KD and a steroid-sensitive membraneous nephrotic syndrome with bilaterally temporal artery and renal vein thrombosis. This is the first reported case of KD associated nephrotic syndrome complicated with wide arterial and venous thrombosis from Anatolia.
Danis
Ramazan
R
Department of Nephrology, Internal Medicine, Medicine Faculty, Dicle University, 21280, Diyarbakir, Turkey. drdanis@dicle.edu.tr
Ozmen
Sehmus
S
Akin
Davut
D
Ozekinci
Selver
S
Altintas
Abdullah
A
Cil
Timucin
T
Pasa
Semir
S
Kilinc
Ilhan
I
D000796:Angiolymphoid Hyperplasia with Eosinophilia / Q000097:blood / Q000150:complications / Q000175:diagnosis*; D001157:Arterial Occlusive Diseases / Q000209:etiology* / Q000601:surgery; D003937:Diagnosis, Differential; D004802:Eosinophilia / Q000209:etiology; D015433:Glomerulonephritis, Membranous / Q000209:etiology*; D006801:Humans; D007073:Immunoglobulin E / Q000097:blood; D008279:Magnetic Resonance Imaging; D009404:Nephrotic Syndrome / Q000209:etiology*; D012082:Renal Veins / Q000473:pathology*; D013699:Temporal Arteries / Q000473:pathology* / Q000601:surgery; D013927:Thrombosis / Q000209:etiology*; D014421:Turkey / Q000453:epidemiology; D020246:Venous Thrombosis / Q000209:etiology
D007073:Immunoglobulin E