[A case of simple type Caroli's disease confined to right lobe of the liver].
Caroli's disease is a rare congenital hepatobiliary disease characterized by multifocal segmental dilatation of intrahepatic bile ducts affecting all or parts of the liver. Two forms of Caroli's disease are described, the pure form and that associated with periportal fibrosis. The disease may diffusely affect the liver or be localized to one lobe or segment. Less than 20% of all reported cases of Caroli's disease are monolobar type. We report a case of simple type Caroli's disease confined to right lobe of the liver in a 22 year old man. He was admitted due to right upper abdominal pain and diagnosed by magnetic resonance cholangiopancreatography. He was treated with right hepatic lobectomy and recovered completely.
Kil
Ho
H
Department of Internal Medicine, Chungbuk National University College of Medicine, Cheongju, Korea.
Choi
Eun Young
EY
Jeong
Jee In
JI
Park
Chan Sun
CS
Park
Seon Mee
SM
Kim
Seok Hyung
SH
Park
Kil Sun
KS
Jang
Lee Chan
LC
D000328:Adult; D001653:Bile Ducts, Intrahepatic / Q000473:pathology; D016767:Caroli Disease / Q000175:diagnosis / Q000473:pathology / Q000601:surgery*; D003135:Common Bile Duct / Q000601:surgery; D003937:Diagnosis, Differential; D006498:Hepatectomy; D006801:Humans; D008099:Liver / Q000473:pathology*; D008279:Magnetic Resonance Imaging; D008297:Male; D014057:Tomography, X-Ray Computed