title: A case of congenital peripheral primitive neuroectodermal tumor presenting with multiple metastases.
abstract: The report describes a case of a newborn with a huge congenital abdominal peripheral primitive neuroectodermal tumor, with peritoneal dissemination and cutaneous involvement, and discusses literature data. Peripheral primitive neuroectodermal tumor is an exceedingly uncommon tumor in this age group and is characterized by very aggressive behavior and poor prognosis.
authors.affiliation: Pathology Department, Istituto Nazionale Tumori, Milan, Italy. cristina.meazza@istitutotumori.mi.it
authors.forename: Cristina
authors.initials: C
authors.lastname: Meazza
authors.forename: Andrea
authors.initials: A
authors.lastname: Ferrari
authors.forename: Monica
authors.initials: M
authors.lastname: Fumagalli
authors.forename: Paola
authors.initials: P
authors.lastname: Collini
authors.forename: Michela
authors.initials: M
authors.lastname: Casanova
authors.forename: Lorenza
authors.initials: L
authors.lastname: Pugni
authors.forename: Mariarosa
authors.initials: M
authors.lastname: Colnaghi
authors.forename: Elena
authors.initials: E
authors.lastname: Zaffignani
authors.forename: Marta
authors.initials: M
authors.lastname: Podda
authors.forename: Fabio
authors.initials: F
authors.lastname: Mosca
mesh_terms: D000328:Adult; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007232:Infant, Newborn, Diseases / Q000188:drug therapy / Q000378:metabolism / Q000473:pathology*; D018241:Neuroectodermal Tumors, Primitive, Peripheral / Q000151:congenital / Q000188:drug therapy / Q000378:metabolism / Q000473:pathology*; D010534:Peritoneal Neoplasms / Q000151:congenital / Q000188:drug therapy / Q000378:metabolism / Q000473:pathology*; D012878:Skin Neoplasms / Q000151:congenital / Q000188:drug therapy / Q000378:metabolism / Q000473:pathology*