title: A case of noncompaction of the ventricular myocardium combined with situs ambiguous with polysplenia.
abstract: A 33-year-old man was admitted to our hospital with chest pain and exertional dyspnea. Two-dimensional echocardiography showed prominent trabeculations and deep intertrabecular recesses, findings consistent with noncompaction of the ventricular myocardium. Thoracoabdominal CT and cardiac magnetic resonance imaging (CMR) revealed situs ambiguous with polysplenia and noncompaction of the left ventricular myocardium. CMR also demonstrated delayed enhancement of the trabeculations located at the apical portion of the left ventricle. The coronary angiogram was normal. This is the first case of noncompaction of the ventricular myocardium associated with situs ambiguous with polysplenia.
authors.affiliation: Cardiology Division. Yondong Severance Hospital, Yonsei University College of Medicine, 146-92 Dogok-dong, Gangnam-gu, Seoul 135-720, Korea.
authors.forename: Yun-Heyong
authors.initials: YH
authors.lastname: Cho
authors.forename: Sung Joon
authors.initials: SJ
authors.lastname: Jin
authors.forename: Hyun Chul
authors.initials: HC
authors.lastname: Je
authors.forename: Young-Won
authors.initials: YW
authors.lastname: Yoon
authors.forename: Bum-Kee
authors.initials: BK
authors.lastname: Hong
authors.forename: Hyuck Moon
authors.initials: HM
authors.lastname: Kwon
authors.forename: Tae Hoon
authors.initials: TH
authors.lastname: Kim
authors.forename: Se-Joong
authors.initials: SJ
authors.lastname: Rim
mesh_terms: D000015:Abnormalities, Multiple / Q000473:pathology*; D000328:Adult; D004452:Echocardiography; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009206:Myocardium / Q000473:pathology*; D013154:Spleen / Q000002:abnormalities*; D013577:Syndrome; D014057:Tomography, X-Ray Computed