[Polysplenia syndrome: two cases in adults revealed by biliary and pancreatic malformations].
Polysplenia Syndrome (PS) associates multiple spleens with other malformations usually cardiac, vascular, visceral and biliary. The diversity of these malformations and their embryological mechanisms are described in relation to two cases of PS that were diagnosed in adults.
Puche
Pierre
P
Service médicochirurgical des maladies de l'appareil digestif et transplantation hépatique, Hôpital Saint-Eloi, 80 avenue Augustin-Fliche, Montpellier Cedex 5. p-puche@chu-montpellier.fr
Jacquet
Eric
E
Godlewski
Guilhem
G
Carabalona
Jean-Pierre
JP
Domergue
Jacques
J
Navarro
Francis
F
Prudhomme
Michel
M
D001656:Biliary Atresia / Q000175:diagnosis; D005260:Female; D006801:Humans; D033162:Incidental Findings; D008297:Male; D008875:Middle Aged; D010179:Pancreas / Q000002:abnormalities; D013154:Spleen / Q000002:abnormalities*; D013577:Syndrome