title: Extensive left ventricular to coronary artery connections in hypoplastic left heart syndrome.
abstract: We demonstrate the echocardiographic features of a rare case of very extensive left ventricular to coronary arterial connections (VCC) to both the right and left coronary arteries in a fetus and subsequent neonate with hypoplastic left heart syndrome (HLH). The right coronary artery, after receiving multiple VCC supplied the only antegrade ascending aortic flow. The left main coronary artery was very hypoplastic and the left anterior descending coronary artery was dilated and tortuous with multiple large VCC. The left circumflex coronary artery arose exclusively from its own VCC. To our knowledge this is the first such echocardiographic demonstration of HLH with extensive bilateral VCC and coronary artery stenosis and interruption.
authors.affiliation: The Heart Institute for Children, Hope Children's Hospital, Oak Lawn, Illinois 60453, USA. david@thic.com
authors.forename: David A
authors.initials: DA
authors.lastname: Roberson
authors.forename: Wei
authors.initials: W
authors.lastname: Cui
authors.forename: Bettina F
authors.initials: BF
authors.lastname: Cuneo
authors.forename: Andrew H
authors.initials: AH
authors.lastname: Van Bergen
authors.forename: Alex J
authors.initials: AJ
authors.lastname: Javois
authors.forename: Saroja
authors.initials: S
authors.lastname: Bharati
mesh_terms: D017023:Coronary Angiography; D003330:Coronary Vessel Anomalies / Q000000981:diagnostic imaging*; D004452:Echocardiography; D017809:Fatal Outcome; D005260:Female; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000000981:diagnostic imaging*; D007231:Infant, Newborn; D008297:Male; D011247:Pregnancy; D016216:Ultrasonography, Prenatal