A case of noncompaction of the ventricular myocardium combined with situs ambiguous with polysplenia.
A 33-year-old man was admitted to our hospital with chest pain and exertional dyspnea. Two-dimensional echocardiography showed prominent trabeculations and deep intertrabecular recesses, findings consistent with noncompaction of the ventricular myocardium. Thoracoabdominal CT and cardiac magnetic resonance imaging (CMR) revealed situs ambiguous with polysplenia and noncompaction of the left ventricular myocardium. CMR also demonstrated delayed enhancement of the trabeculations located at the apical portion of the left ventricle. The coronary angiogram was normal. This is the first case of noncompaction of the ventricular myocardium associated with situs ambiguous with polysplenia.
Cho
Yun-Heyong
YH
Cardiology Division. Yondong Severance Hospital, Yonsei University College of Medicine, 146-92 Dogok-dong, Gangnam-gu, Seoul 135-720, Korea.
Jin
Sung Joon
SJ
Je
Hyun Chul
HC
Yoon
Young-Won
YW
Hong
Bum-Kee
BK
Kwon
Hyuck Moon
HM
Kim
Tae Hoon
TH
Rim
Se-Joong
SJ
D000015:Abnormalities, Multiple / Q000473:pathology*; D000328:Adult; D004452:Echocardiography; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009206:Myocardium / Q000473:pathology*; D013154:Spleen / Q000002:abnormalities*; D013577:Syndrome; D014057:Tomography, X-Ray Computed