Partial anomalous pulmonary venous connection associated with Lutembacher's syndrome.
Lutembacher's syndrome is a rare combination of congenital atrial septal defect and mitral stenosis (almost always rheumatic). The hemodynamic effect of this combination makes the clinical diagnosis difficult due to a wide variation of clinical presentation. Echocardiography and cardiac catheterization are useful tools for proper diagnosis and planning of the therapeutic strategy. We present a 28-year-old female with Lutembacher's syndrome associated with partial anomalous pulmonary venous connection (PAPVC), which was surgically corrected. To our knowledge, this combination has never been reported in the literature.
Anwar
Ashraf M
AM
Department of Cardiology, King Fahd Armed Force Hospital, Jeddah, Saudi-Arabia.
Nosir
Youssef F M
YF
Ajam
Aref
A
Galal
Ahmed N
AN
Ashmeg
Abdullah
A
Chamsi-Pasha
Hassan
H
D000328:Adult; D003937:Diagnosis, Differential; D004452:Echocardiography / Q000379:methods*; D005260:Female; D006801:Humans; D008185:Lutembacher Syndrome / Q000150:complications* / Q000000981:diagnostic imaging; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging; D012720:Severity of Illness Index