Fontan operation through a right lateral thoracotomy to treat Cantrell syndrome with severe ectopia cordis.
A median sternotomy would be very difficult for Cantrell syndrome with severe ectopia cordis. For Cantrell syndrome and tricuspid atresia after left modified Blalock-Taussig shunt with severe ectopia cordis, defect in the middle and inferior portion of the sternum, and the closing of ventriculo-peritoneal shunt, we performed extracardiac total cavopulmonary connection through a right lateral thoracotomy after establishing right modified Blalock-Taussig shunt and performing coil embolization of left modified Blalock-Taussig shunt by cardiologists.
Okamoto
Yuki
Y
Nagano Children's Hospital, 3100 Toyoshina, Azumino city, Nagano, 399-8288 Japan. yamanashimedical@yahoo.co.jp
Harada
Yorikazu
Y
Uchita
Shunji
S
D000015:Abnormalities, Multiple / Q000503:physiopathology / Q000601:surgery*; D001166:Arteriovenous Shunt, Surgical; D006328:Cardiac Catheterization; D002648:Child; D054083:Ectopia Cordis / Q000150:complications / Q000503:physiopathology / Q000601:surgery*; D004621:Embolization, Therapeutic; D005260:Female; D018729:Fontan Procedure; D006439:Hemodynamics; D006554:Hernia, Umbilical / Q000150:complications / Q000601:surgery; D006801:Humans; D011651:Pulmonary Artery / Q000601:surgery; D013577:Syndrome; D013908:Thoracotomy; D016896:Treatment Outcome; D018785:Tricuspid Atresia / Q000150:complications / Q000503:physiopathology / Q000601:surgery*; D014682:Vena Cava, Inferior / Q000601:surgery; D014683:Vena Cava, Superior / Q000601:surgery