title: Kaposiform hemangioendothelioma: a rare cause of spontaneous hemothorax in infancy. Review of the literature.
abstract: Kaposiform hemangioendothelioma is a rare vascular tumor found almost exclusively in early childhood often associated with a life-threatening thrombocytopenia and consumptive coagulopathy known as Kasabach-Merritt phenomenon. The natural history of these lesions and treatment remains controversial. We portray a case of a spontaneous hemothorax in a 2-month-old female infant and review of 153 reported cases in attempts to better delineate the available treatment options.
authors.affiliation: Department of General Surgery, William Beaumont Army Medical Center, El Paso, TX 79920, USA. francisco.sanmiguelgerena@amedd.army.mil
authors.forename: Francisco Luis
authors.initials: FL
authors.lastname: San Miguel
authors.forename: William
authors.initials: W
authors.lastname: Spurbeck
authors.forename: Carlos
authors.initials: C
authors.lastname: Budding
authors.forename: John
authors.initials: J
authors.lastname: Horton
mesh_terms: D004564:Electrocoagulation / Q000379:methods; D005260:Female; D005500:Follow-Up Studies; D006390:Hemangioendothelioma / Q000150:complications / Q000473:pathology* / Q000601:surgery; D006491:Hemothorax / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006801:Humans; D007223:Infant; D035583:Rare Diseases; D018570:Risk Assessment; D012514:Sarcoma, Kaposi / Q000150:complications / Q000473:pathology* / Q000601:surgery; D012720:Severity of Illness Index; D013908:Thoracotomy / Q000379:methods; D016896:Treatment Outcome; D019043:Vascular Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery