Kaposiform hemangioendothelioma: a rare cause of spontaneous hemothorax in infancy. Review of the literature.
Kaposiform hemangioendothelioma is a rare vascular tumor found almost exclusively in early childhood often associated with a life-threatening thrombocytopenia and consumptive coagulopathy known as Kasabach-Merritt phenomenon. The natural history of these lesions and treatment remains controversial. We portray a case of a spontaneous hemothorax in a 2-month-old female infant and review of 153 reported cases in attempts to better delineate the available treatment options.
San Miguel
Francisco Luis
FL
Department of General Surgery, William Beaumont Army Medical Center, El Paso, TX 79920, USA. francisco.sanmiguelgerena@amedd.army.mil
Spurbeck
William
W
Budding
Carlos
C
Horton
John
J
D004564:Electrocoagulation / Q000379:methods; D005260:Female; D005500:Follow-Up Studies; D006390:Hemangioendothelioma / Q000150:complications / Q000473:pathology* / Q000601:surgery; D006491:Hemothorax / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006801:Humans; D007223:Infant; D035583:Rare Diseases; D018570:Risk Assessment; D012514:Sarcoma, Kaposi / Q000150:complications / Q000473:pathology* / Q000601:surgery; D012720:Severity of Illness Index; D013908:Thoracotomy / Q000379:methods; D016896:Treatment Outcome; D019043:Vascular Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery