Exudative retinal detachment following cataract surgery in Hallermann-Streiff syndrome.
OBJECTIVE
To report two cases of Hallermann-Streiff syndrome with exudative retinal detachment after cataract surgery.


METHODS
Case report.


RESULTS
Four eyes of two patients with Hallermann-Streiff syndrome developed exudative retinal detachments after lensectomy and anterior vitrectomy at 2 and 4 months of age. Both patients had extreme microphthalmia. The exudative retinal detachment regressed spontaneously in three of the four eyes; however, one eye required subscleral sclerectomy. In one patient, the best-corrected visual acuity was 20/200 at 3 years of age; the other patient had good fixation and following behavior in each eye at 1 year of age.


CONCLUSIONS
Early surgery to treat congenital cataracts in extremely microphthalmic eyes associated with the Hallermann-Streiff syndrome may induce exudative retinal detachment. However, the retinal detachments tend to regress and may not cause severe visual impairment.
Nishina
Sachiko
S
Department of Ophthalmology, National Center for Child Health and Development, 2-10-1 Ohkura, Setagaya-ku, Tokyo 157-8535, Japan. nishina-s@ncchd.go.jp
Suzuki
Yumi
Y
Azuma
Noriyuki
N
D002386:Cataract / Q000151:congenital*; D002387:Cataract Extraction / Q000009:adverse effects*; D005122:Exudates and Transudates; D005260:Female; D006210:Hallermann's Syndrome / Q000150:complications*; D006801:Humans; D007223:Infant; D008297:Male; D008850:Microphthalmos / Q000150:complications; D012075:Remission, Spontaneous; D012163:Retinal Detachment / Q000000981:diagnostic imaging / Q000209:etiology* / Q000503:physiopathology; D014463:Ultrasonography; D014792:Visual Acuity