[McCune Albright syndrome - diffuse orbital involvement due to fibrous dysplasia: a case report].
Fibrous dysplasia is a benign, slowly progressive bone disorder, in which normal bone is replaced by fibrous tissue. It is called McCune Albright syndrome when associated with skin hyperpigmentation and endocrinological disorders. We report a rare case of McCune Albright syndrome in a boy, who presented bilateral and diffuse involvement of orbits but few external craniofacial distortions.
Costanzi
Márcio Alberto
MA
Departamento de Oftalmologia, Otorrinolaringologia e Cirurgia de Cabeça e Pescoço, Faculdade de Medicina, Universidade de São Paulo, Ribeirão Preto, SP, Brasil. marciocostanzi@bol.com.br
Velasco e Cruz
Antonio Augusto
AA
D002648:Child; D019465:Craniofacial Abnormalities / Q000000981:diagnostic imaging; D005359:Fibrous Dysplasia, Polyostotic / Q000150:complications / Q000175:diagnosis*; D006801:Humans; D008297:Male; D009916:Orbital Diseases / Q000000981:diagnostic imaging / Q000209:etiology*; D014057:Tomography, X-Ray Computed