title: A rare spontaneous osteosarcoma of the calvarium in a patient with long-standing fibrous dysplasia: CT and MR findings.
abstract: A 52-year-old man with long-standing craniofacial polyostotic fibrous dysplasia (FD) and no history of prior radiation therapy developed a spontaneous right temporal bone osteosarcoma. Such spontaneous sarcomatous degeneration of FD is rare, particularly in the calvarium/skull, where, to our knowledge, only six prior cases have been reported in the literature. We report this case because it is a rare entity with well-documented CT and MR images, and to emphasize the importance of depicting imaging features of sarcomatous degeneration among the complex imaging findings of FD.
authors.affiliation: Department of Neuroradiology, S. João University Hospital, Porto, Portugal. reis_carina@yahoo.com
authors.forename: C
authors.initials: C
authors.lastname: Reis
authors.forename: E M
authors.initials: EM
authors.lastname: Genden
authors.forename: J B
authors.initials: JB
authors.lastname: Bederson
authors.forename: P M
authors.initials: PM
authors.lastname: Som
mesh_terms: D005147:Facial Bones / Q000002:abnormalities; D005359:Fibrous Dysplasia, Polyostotic / Q000150:complications; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D012516:Osteosarcoma / Q000150:complications / Q000175:diagnosis*; D012886:Skull / Q000002:abnormalities; D012888:Skull Neoplasms / Q000150:complications / Q000175:diagnosis*; D013701:Temporal Bone; D014057:Tomography, X-Ray Computed