title: Dural arteriovenous fistula of the greater sphenoid wing region in neurofibromatosis type 1.
abstract: Neurofibromatosis type 1 (NF1) has been infrequently associated with different cerebrovascular conditions that may lead to either ischemic or hemorrhagic stroke. Intracranial dural arteriovenous fistulas have not been described in NF1 patients. In this paper we present a unique case of an 8-year-old child with florid NF1 that presented a greater sphenoid wing dural arteriovenous fistula draining directly through the superior ophthalmic vein and causing exophthalmos. The fistula was cured by direct trans-superior ophthalmic vein approach, by means of detachable coils. Only a few cases of dural fistulas in the lesser sphenoidal wing region have been described in the literature but a fistula of the greater sphenoid wing has not been previously described.
authors.affiliation: Department of Neurosurgery, Hadassah Hebrew University Hospital, Jerusalem, Israel.
authors.forename: Jose E
authors.initials: JE
authors.lastname: Cohen
authors.forename: John Mose
authors.initials: JM
authors.lastname: Gomori
authors.forename: Savvas
authors.initials: S
authors.lastname: Grigoriadis
authors.forename: Sergei
authors.initials: S
authors.lastname: Spektor
authors.forename: Gustavo
authors.initials: G
authors.lastname: Rajz
mesh_terms: D020785:Central Nervous System Vascular Malformations / Q000150:complications / Q000473:pathology*; D002648:Child; D005260:Female; D006801:Humans; D009456:Neurofibromatosis 1 / Q000150:complications / Q000473:pathology*; D013101:Sphenoid Sinus / Q000002:abnormalities / Q000473:pathology*