title: Extracardiac Fontan with T-shape conduit in non-confluent pulmonary arteries.
abstract: A 34 months-old male patient with double inlet right ventricle with nonconfluent pulmonary arteries who underwent successful extracardiac fenestarated Fontan procedure using pre-designed T-shaped PTFE vascular graft after multi-step rehabilitation of the diminutive hilar pulmonary arteries. At first we performed 6 mm confluent pulmonary artery vascular graft implantation with 4 mm BT shunt at patient's 4 weeks old. At 9 months of patient, we upsized the confluent pulmonary arterial graft to 8 mm with bidirectional cavopulmonary connection, and, at 34 months, we performed extracardiac conduit Fontan procedure with pre-designed T-shape conduit including the confluent pulmonary arterial portion at last. Patient shows excellent functional status and development.
authors.affiliation: Department of Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul National University College of Medicine, Seoul National University Clinical Research Institute, Seoul, South Korea. leri418@gmail.com
authors.forename: Jae Gun
authors.initials: JG
authors.lastname: Kwak
authors.forename: Jeong Ryul
authors.initials: JR
authors.lastname: Lee
authors.forename: Woo-Sung
authors.initials: WS
authors.lastname: Jang
authors.forename: Eun Jung
authors.initials: EJ
authors.lastname: Bae
mesh_terms: D001807:Blood Vessel Prosthesis; D002675:Child, Preschool; D005500:Follow-Up Studies; D018729:Fontan Procedure / Q000379:methods*; D006330:Heart Defects, Congenital / Q000601:surgery*; D006352:Heart Ventricles / Q000002:abnormalities / Q000601:surgery; D006801:Humans; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery*