[A rare differential diagnosis of chylothorax].
We present the case report of a 17-year-old patient with right pleural effusion and pre-existing lymphangiomas of the chest wall. Thoracentesis revealed a salmon-milky effusion containing chylomicrones defining a chylothorax (with blood intermixture). A CT scan and MRI showed multiple osteolysis. After excluding malignancy as well as infectious and traumatic causes of the chylothorax, we made the diagnosis of a Gorham-Stout syndrome. A minimal-invasive pleurectomy and decortication were done successfully and prevented a relapse of the pleural effusion for at least one year.
Bernstein
J
J
Klinik für Pneumologie, HELIOS Kliniken Schwerin. petra.laubner@helios-kliniken.de
Engelhardt
M
M
Retzlaff
S
S
D000293:Adolescent; D002916:Chylothorax / Q000175:diagnosis* / Q000628:therapy*; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D010015:Osteolysis, Essential / Q000175:diagnosis* / Q000628:therapy*; D010996:Pleural Effusion / Q000175:diagnosis* / Q000628:therapy*; D035583:Rare Diseases / Q000175:diagnosis; D013577:Syndrome