Central cyanosis due to severe pulmonary hypertension combined with pericarditis as the initial manifestation of systemic lupus erythematosus.
Systemic lupus erythematosus (SLE) is a multisystemic autoimmune disorder. The initial manifestation complicating any organ system either singly or in combination is protean. Herein we report a 26-year-old female patient with fresh SLE whose initial manifestation was central cyanosis caused by severe pulmonary hypertension and acute pericarditis. The symptoms were relieved dramatically after treatment with steroid and bosentan. Accurate and timely diagnosis in SLE-associated pulmonary hypertension may be life saving.
Wang
Ruei-Fang
RF
Emergency Department, Shin-Kong Wu Ho-Su Memorial Hospital, Taipei 111, Taiwan.
Hung
Tzu-Yao
TY
Chong
Chee-Fah
CF
Wang
Tzong-Luen
TL
Chen
Chien-Chih
CC
D000328:Adult; D003490:Cyanosis / Q000209:etiology*; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D008180:Lupus Erythematosus, Systemic / Q000150:complications* / Q000175:diagnosis*; D010493:Pericarditis / Q000209:etiology*