Talon cusps presenting in a child with Alagille's syndrome--a case report.
Talon cusp is a rare dental anomaly often associated with systemic conditions such as Rubenstein-Taybi Syndrome, Ellis-van Crevald Syndrome and Incontentia pigmenti achromians. It has not been previously reported as occurring in Alagille Syndrome. Early diagnosis of talon cusps is crucial for the correct management and avoidance of complications. This case highlights the need for careful dental examination when treating children with syndromes, as new phenotypes that can have an effect on the dentition.
Chatterjee
Mahua
M
Consultant department of Pediatric Dentistry, Great Ormond Street Hospital, London, UK. mahua77@tiscali.co.uk
Mason
Carol
C
D016738:Alagille Syndrome / Q000150:complications*; D002648:Child; D019229:Dentition, Permanent; D005260:Female; D006801:Humans; D007180:Incisor / Q000002:abnormalities*; D008437:Maxilla; D014071:Tooth Abnormalities / Q000150:complications*; D019228:Tooth Crown / Q000002:abnormalities*