title: Conversion from total cavopulmonary shunt to Fontan circulation: improved cyanosis with an 11-year interval.
abstract: We experienced a conversion case from total cavopulmonary shunt (TCPS) to the Fontan circulation with an 11-year interval in the left isomerism and an interruption of the inferior caval vein. Marked cyanosis (pulse oximetry measuring 74%) progressed 8 years after TCPS because of the prominent development of bilateral pulmonary arteriovenous fistula (PAVF), which was diminished after the Fontan conversion, and recent pulse oximetry measured 95% 22 months after the conversion. We believe that this report is a case with the longest interval from TCPS to Fontan in which PAVF was diminished and marked cyanosis was improved.
authors.affiliation: Department of Thoracic and Cardiovascular Surgery, Wakayama Medical University, Wakayama, Japan.
authors.forename: Takeshi
authors.initials: T
authors.lastname: Hiramatsu
authors.forename: Shigeru
authors.initials: S
authors.lastname: Komori
authors.forename: Yoshiharu
authors.initials: Y
authors.lastname: Nishimura
authors.forename: Yoshitaka
authors.initials: Y
authors.lastname: Okamura
authors.forename: Hiroyuki
authors.initials: H
authors.lastname: Suzuki
authors.forename: Takashi
authors.initials: T
authors.lastname: Takeuchi
mesh_terms: D002648:Child; D003490:Cyanosis / Q000517:prevention & control*; D018450:Disease Progression; D005260:Female; D018729:Fontan Procedure; D018610:Heart Bypass, Right; D006330:Heart Defects, Congenital / Q000601:surgery*; D006801:Humans; D010092:Oximetry