title: Portopulmonary hypertension in a case of non-cirrhotic portal fibrosis.
abstract: Portopulmonary hypertension (PPHT) is the unusual association of portal hypertension (HT) with pulmonary HT. We report a case of noncirrhotic portal fibrosis (NCPF) leading to PPHT which is exceedingly rare with only very few cases reported in the literature. This is an autopsy report of a 30 years old man, a known case of portal HT who died suddenly due to a syncopal attack. Autopsy revealed massive pulmonary thromobembolism with pulmonary HT. Liver showed changes of NCPF. The rarity of NCPF causing PPHT prompted this case report.
authors.affiliation: Department of Pathology, T.N. Medical College and B.Y.L. Nair Hospital, Mumbai. ppamonkar@hotmail.com
authors.forename: Amonkar P
authors.initials: AP
authors.lastname: Gayathri
authors.forename: Deshpande R
authors.initials: DR
authors.lastname: Jaya
authors.forename: Amarapurkar D
authors.initials: AD
authors.lastname: Anjali
authors.forename: Karpate
authors.initials: K
authors.lastname: Arti
mesh_terms: D000328:Adult; D001344:Autopsy; D017809:Fatal Outcome; D006801:Humans; D006975:Hypertension, Portal / Q000150:complications* / Q000175:diagnosis*; D006976:Hypertension, Pulmonary / Q000150:complications* / Q000175:diagnosis*; D008103:Liver Cirrhosis / Q000473:pathology; D008297:Male; D011655:Pulmonary Embolism / Q000175:diagnosis*; D013575:Syncope