[A case of the long course of acute intermittent porphyria].
A case of acute intermittent porphyria is described in a 37-year-old female patient treated with normasang, a drug that regulates porphyrin metabolism at the last stages of the disease. Chronic renal failure with the hypertensive syndrome, severe neurological symptoms, and vascular sclerotic changes in all organs were the symptoms of the underlying disease. Infectious complications were the cause of sepsis and favoured deteriorated multiple organ dysfunction that determined lethal exitus.
Glasko
E N
EN
Pustovoĭt
Ia S
IaS
Korolev
A V
AV
Karpova
I V
IV
D000328:Adult; D001808:Blood Vessels / Q000473:pathology; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D009102:Multiple Organ Failure / Q000150:complications; D017118:Porphyria, Acute Intermittent / Q000150:complications / Q000503:physiopathology*; D051436:Renal Insufficiency, Chronic / Q000150:complications; D012598:Sclerosis; D018805:Sepsis / Q000150:complications