title: Intrathoracic malignant peripheral nerve sheath tumor with angiosarcoma in a child with NF1.
abstract: Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST associated with NF1.
authors.affiliation: Department of Pediatric Oncology, Faculty of Medicine, Ondokuz Mayis University, Samsun, Turkey. ellimurat@yahoo.com
authors.forename: Murat
authors.initials: M
authors.lastname: Elli
authors.forename: Bilge
authors.initials: B
authors.lastname: Can
authors.forename: Meltem
authors.initials: M
authors.lastname: Ceyhan
authors.forename: Faruk Güçlü
authors.initials: FG
authors.lastname: Pinarli
authors.forename: Ayhan
authors.initials: A
authors.lastname: Dagdemir
authors.forename: Halil Suat
authors.initials: HS
authors.lastname: Ayyildiz
authors.forename: Bilge
authors.initials: B
authors.lastname: Gürsel
authors.forename: Adnan
authors.initials: A
authors.lastname: Dagçinar
mesh_terms: D000293:Adolescent; D006394:Hemangiosarcoma / Q000473:pathology; D006801:Humans; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000473:pathology; D018317:Nerve Sheath Neoplasms / Q000473:pathology; D009456:Neurofibromatosis 1 / Q000473:pathology