Intrathoracic malignant peripheral nerve sheath tumor with angiosarcoma in a child with NF1.
Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST associated with NF1.
Elli
Murat
M
Department of Pediatric Oncology, Faculty of Medicine, Ondokuz Mayis University, Samsun, Turkey. ellimurat@yahoo.com
Can
Bilge
B
Ceyhan
Meltem
M
Pinarli
Faruk Güçlü
FG
Dagdemir
Ayhan
A
Ayyildiz
Halil Suat
HS
Gürsel
Bilge
B
Dagçinar
Adnan
A
D000293:Adolescent; D006394:Hemangiosarcoma / Q000473:pathology; D006801:Humans; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000473:pathology; D018317:Nerve Sheath Neoplasms / Q000473:pathology; D009456:Neurofibromatosis 1 / Q000473:pathology