A newborn with chylous ascites caused by intestinal malrotation associated with heterotaxia syndrome.
Chylous ascites is a rare entity in infants. An uncommon cause of chylous ascites is intestinal malrotation. We report a case of a neonate with heterotaxia-polysplenia syndrome and intestinal malrotation who presented with chylous ascites and subsequently developed duodenal obstruction from midgut volvulus. He was successfully treated with peritoneal drainage, surgical intervention, and nutritional support. A brief overview of the association of chylous ascites, intestinal rotational anomalies and heterotaxia syndromes is discussed.
Seltz
L Barry
LB
Division of Pediatric Medicine, Hospital for Sick Children, University of Toronto, Toronto, ON, M5G 1X8, Canada. leonard.seltz@sickkids.ca
Kanani
Ronik
R
Zamakhshary
Mohammed
M
Chiu
Priscilla P L
PP
D002915:Chylous Ascites / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D003937:Diagnosis, Differential; D006801:Humans; D007231:Infant, Newborn; D007410:Intestinal Diseases / Q000150:complications* / Q000151:congenital / Q000601:surgery; D007421:Intestine, Small / Q000002:abnormalities*; D007813:Laparotomy / Q000379:methods; D008297:Male; D013577:Syndrome; D014057:Tomography, X-Ray Computed