Junctional epidermolysis bullosa associated with hypoplastic enamel and pervasive failure of tooth eruption: Oral rehabilitation with use of an overdenture.
This report describes a previously unreported case of generalized hypoplastic enamel and failure of eruption of the permanent maxillary teeth and only partial eruption of the permanent mandibular teeth in an 18-year-old male diagnosed with junctional epidermolysis bullosa. Similar anomalies were reported to have affected the deciduous dentition. Beginning at 4 years of age, oral rehabilitation has been conservatively managed with the fabrication of various maxillary complete overdentures. The use of this prosthesis has provided an economical, nonsurgical treatment option when oral soft tissue permits and with relative ease of construction.
Brooks
John K
JK
Department of Diagnostic Sciences and Pathology, University of Maryland Dental School, Baltimore, Maryland 21201-1586, USA. oralpath5@comcast.net
Bare
Lyndsay C
LC
Davidson
Joseph
J
Taylor
Lisa S
LS
Wright
J Timothy
JT
D000293:Adolescent; D003744:Dental Enamel Hypoplasia / Q000000981:diagnostic imaging / Q000209:etiology / Q000534:rehabilitation*; D019229:Dentition, Permanent; D003827:Denture, Complete, Upper; D003828:Denture, Overlay; D016109:Epidermolysis Bullosa, Junctional / Q000150:complications* / Q000000981:diagnostic imaging; D006801:Humans; D008297:Male; D011859:Radiography; D014094:Tooth, Deciduous; D014097:Tooth, Unerupted / Q000000981:diagnostic imaging / Q000209:etiology / Q000534:rehabilitation*