title: Interruption of the ascending aorta: a hitherto undescribed lesion.
abstract: We are describing a most unusual variant of aortic arch interruption. The ascending aorta was atretic above the sinutubular junction forming a blind-ending pouch. The coronary arteries were the only vessels arising from the aortic trunk. All the brachiocephalic vessels were perfused in retrograde fashion through the arterial duct. The aortic valve itself was dysplastic, stenotic, and permitted severe regurgitation. There was no subaortic obstruction. A modified first stage Norwood palliation was performed. Due to myocardial insufficiency transthoracic extracorporeal membrane oxygenation had to be commenced at the end of surgery. Unfortunately the child died due to severe intracranial hemorrhage.
authors: Department of Pediatric Cardiology, Heart Center Leipzig, Leipzig, Germany. michael.weidenbach@medizin.uni-leipzig.de
authors: Michael
authors: M
authors: Weidenbach
authors: Ingo
authors: I
authors: Daehnert
authors: Vit
authors: V
authors: Razek
authors: Alexandra
authors: A
authors: Beller
authors: Jan
authors: J
authors: Janousek
authors: Martin
authors: M
authors: Kostelka
authors: Robert H
authors: RH
authors: Anderson
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery; D017542:Aneurysm, Ruptured / Q000175:diagnosis / Q000601:surgery; D001011:Aorta / Q000002:abnormalities*; D001165:Arteriovenous Malformations / Q000175:diagnosis / Q000601:surgery*; D016122:Brachiocephalic Trunk / Q000002:abnormalities*; D006348:Cardiac Surgical Procedures / Q000379:methods; D018450:Disease Progression; D015199:Extracorporeal Membrane Oxygenation / Q000379:methods; D017809:Fatal Outcome; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D011183:Postoperative Complications / Q000175:diagnosis / Q000628:therapy; D012720:Severity of Illness Index