Extramammary Paget disease in a retrorectal dermoid cyst: report of a unique case.
Retrorectal (presacral) dermoid cysts are rare entities, also described as mature cystic or monodermal teratomas. We present a unique case arising in a 64-year-old man, in which the lining squamous epithelium showed marked expansion by Paget disease of extramammary type, and discuss the clinical, radiologic, and pathologic findings.
Thway
Khin
K
Department of Histopathology, Royal Marsden Hospital, London, UK.
Polson
Alexander
A
Pope
Romney
R
Thomas
Joseph Meirion
JM
Fisher
Cyril
C
D003884:Dermoid Cyst / Q000473:pathology* / Q000601:surgery; D004847:Epithelial Cells / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D010145:Paget Disease, Extramammary / Q000473:pathology*; D012004:Rectal Neoplasms / Q000473:pathology* / Q000601:surgery; D013724:Teratoma / Q000473:pathology* / Q000601:surgery; D016896:Treatment Outcome