title: Case report: "auditory neuropathy" in a newborn caused by a cerebellopontine angle arachnoid cyst.
abstract: We present a 6-week-old girl, referred because of failed newborn hearing screening in the right ear. Click-evoked oto-acoustic emissions were present in both ears, auditory brainstem responses (ABR) were present in the left but totally absent in the right ear. A magnetic resonance imaging (MRI) study revealed a large arachnoid cyst in the right cerebellopontine angle (CPA) and a diagnosis of "auditory neuropathy/auditory dyssynchrony" was established. A microsurgical resection of the cyst wall and fenestration was performed by a retro sigmoid approach. This is the first case in the literature of auditory neuropathy (AN) in an infant caused by a cerebellopontine angle arachnoid cyst.
authors: Department of Otorhinolaryngology, Head and Neck Surgery, Antwerp University Hospital, University of Antwerp, Wilrijkstraat 10, 2650 Edegem, Belgium. An.Boudewyns@uza.be
authors: A N
authors: AN
authors: Boudewyns
authors: F
authors: F
authors: Declau
authors: D
authors: D
authors: De Ridder
authors: P M
authors: PM
authors: Parizel
authors: J
authors: J
authors: van den Ende
authors: P H
authors: PH
authors: Van de Heyning
mesh_terms: D016080:Arachnoid Cysts / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D001309:Auditory Threshold / Q000502:physiology; D002530:Cerebellopontine Angle / Q000473:pathology / Q000601:surgery*; D016057:Evoked Potentials, Auditory, Brain Stem / Q000502:physiology*; D005260:Female; D006312:Hearing Loss, Bilateral / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D000160:Vestibulocochlear Nerve Diseases / Q000503:physiopathology* / Q000601:surgery