Case report: "auditory neuropathy" in a newborn caused by a cerebellopontine angle arachnoid cyst.
We present a 6-week-old girl, referred because of failed newborn hearing screening in the right ear. Click-evoked oto-acoustic emissions were present in both ears, auditory brainstem responses (ABR) were present in the left but totally absent in the right ear. A magnetic resonance imaging (MRI) study revealed a large arachnoid cyst in the right cerebellopontine angle (CPA) and a diagnosis of "auditory neuropathy/auditory dyssynchrony" was established. A microsurgical resection of the cyst wall and fenestration was performed by a retro sigmoid approach. This is the first case in the literature of auditory neuropathy (AN) in an infant caused by a cerebellopontine angle arachnoid cyst.
Boudewyns
A N
AN
Department of Otorhinolaryngology, Head and Neck Surgery, Antwerp University Hospital, University of Antwerp, Wilrijkstraat 10, 2650 Edegem, Belgium. An.Boudewyns@uza.be
Declau
F
F
De Ridder
D
D
Parizel
P M
PM
van den Ende
J
J
Van de Heyning
P H
PH
D016080:Arachnoid Cysts / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D001309:Auditory Threshold / Q000502:physiology; D002530:Cerebellopontine Angle / Q000473:pathology / Q000601:surgery*; D016057:Evoked Potentials, Auditory, Brain Stem / Q000502:physiology*; D005260:Female; D006312:Hearing Loss, Bilateral / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D000160:Vestibulocochlear Nerve Diseases / Q000503:physiopathology* / Q000601:surgery