Hemiazygos venous additional pulmonary flow for successful total cavo-pulmonary connection.
Patients who underwent only Glenn procedure after being deemed unsuitable candidates for Fontan completion are not small in number, and may develop arterio-venous (AV) pulmonary malformations during the follow-up period. We present the case of a 17-year-old woman with severe systemic desaturation 13 years after Glenn procedure and repair of total anomalous pulmonary venous return. Among other anomalies, the patient disclosed hemiazygos continuation to a persistent left superior vena cava. This case supports the concept that returning flow from the abdominal vein plays an important role in the well-balanced growth of the pulmonary artery and in the inhibition of the pulmonary AV malformation.
Sughimoto
Koichi
K
Department of Cardiovascular Surgery, Chiba Cardiovascular Center, Chiba, Japan. sughimotokoichi@yahoo.co.jp
Matsuo
Kozo
K
Niwa
Koichiro
K
Tateno
Shigeru
S
Kawasoe
Yasutaka
Y
Shirai
Takeaki
T
Tatsuno
Katsuhiko
K
D000293:Adolescent; D000714:Anastomosis, Surgical; D000792:Angiography; D001165:Arteriovenous Malformations / Q000175:diagnosis / Q000209:etiology / Q000601:surgery; D001166:Arteriovenous Shunt, Surgical / Q000009:adverse effects; D001807:Blood Vessel Prosthesis; D006328:Cardiac Catheterization; D005260:Female; D006503:Hepatic Veins / Q000601:surgery*; D006801:Humans; D008499:Medical Records; D010100:Oxygen / Q000097:blood; D011651:Pulmonary Artery / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000254:growth & development; D011652:Pulmonary Circulation; D011666:Pulmonary Valve Stenosis / Q000601:surgery; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery*; D013131:Spine / Q000098:blood supply*; D016896:Treatment Outcome; D014680:Veins / Q000002:abnormalities / Q000601:surgery; D014682:Vena Cava, Inferior / Q000601:surgery*
D010100:Oxygen