Intralobar pulmonary sequestration associated with a congenital pulmonary airway malformation type II.
Intralobar pulmonary sequestration (ILPS) is a rare congenital malformation of the lung. It is described as a segment of lung parenchyma with normal pleura and systemic blood supply and it has poor communication with the tracheobronchial tree. Patients usually present in later childhood or adulthood with a history of recurrent pneumonias. The malformation is rarely associated with other congenital anomalies such as a congenital pulmonary airway malformation (CPAM). A CPAM is a congenital cystic lesion of the lung that presents usually in the newborn period as respiratory distress. We describe the case of a 2-month-old female who presented to the local emergency room with the initial diagnosis of pneumonia, surgical diagnosis of ILPS, and a final pathological diagnosis of ILPS with an associated CPAM.
Couluris
Marisa
M
University of South Florida College of Medicine, Tampa, Florida 33606, USA. mcouluri@health.usf.edu
Schnapf
Bruce M
BM
Gilbert-Barness
Enid
E
D001998:Bronchopulmonary Sequestration / Q000150:complications* / Q000473:pathology* / Q000503:physiopathology; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000150:complications* / Q000473:pathology* / Q000503:physiopathology; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007223:Infant; D011014:Pneumonia / Q000473:pathology; D014057:Tomography, X-Ray Computed