[Verner-Morrison syndrome revealing a ganglioneuroblastoma in an adult].
Most vasoactive intestinal peptide (VIP)-producing tumours are from epithelial origin. Tumours derived from the sympathetic nervous system can produce VIP as well. We report here the case of a Verner-Morrison syndrome in a 40-year-old woman revealing a metastatic ganglioneuroblastoma. The diarrhea resolved after the resection of primary tumour and liver metastases. Neuroblastic tumours occur extremely rarely in adults. Thus, the management of these tumours is poorly defined in adults.
Neuzillet
C
C
Pôle des Maladies de l'Appareil Digestif, Hôpital Beaujon, 100 Boulevard du Général-Leclerc, 92118 Clichy Cedex, France. pascal.hammel@bjn.aphp.fr
Hammel
P
P
Baudin
E
E
Couvelard
A
A
Elias
D
D
Casiraghi
O
O
Cazals-Hatem
D
D
Pelletier
A-L
AL
Lévy
P
P
Ruszniewski
P
P
D000328:Adult; D001859:Bone Neoplasms / Q000473:pathology / Q000628:therapy; D005260:Female; D018305:Ganglioneuroblastoma / Q000473:pathology* / Q000628:therapy; D006801:Humans; D008113:Liver Neoplasms / Q000473:pathology* / Q000628:therapy; D010190:Pancreatic Neoplasms / Q000473:pathology* / Q000628:therapy; D003969:Vipoma / Q000473:pathology* / Q000628:therapy