Rare venous connection causing severe hypoxia after Fontan operation.
We describe a rare case of cyanosis following the Fontan operation with right-to-left shunting at the venous level, that is, an azygos venous to pulmonary venous connection. Few cases with partial anomalous pulmonary venous connection to azygos vein have been reported; however, there have been no reports describing the connection from azygos vein to pulmonary vein, which results in desaturation after Fontan operation. Multidetector-row computed tomography (MDCT) was a useful tool to depict this vascular malformation.
Hayabuchi
Yasunobu
Y
Department of Pediatrics, University of Tokushima, Kuramoto-cho-3, Tokushima 770-8503, Japan. hayabuchi@clin.med.tokushima-u.ac.jp
Inoue
Miki
M
Kagami
Shoji
S
D001401:Azygos Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D002648:Child; D005260:Female; D018729:Fontan Procedure / Q000009:adverse effects*; D006801:Humans; D000860:Hypoxia / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D008026:Ligation; D010690:Phlebography / Q000379:methods; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging; D012720:Severity of Illness Index; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D054079:Vascular Malformations / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D014656:Vascular Surgical Procedures