title: Quadricuspid aortic valve with ascending aortic aneurysm: report of a case and discussion of embryological mechanisms.
abstract: Congenital quadricuspid aortic valves (QAVs) are rare phenomena. They are often associated with aortic insufficiency and significant morbidity. A QAV with an associated ascending aortic aneurysm is extremely rare, and these conditions might have a shared embryonic etiology. We describe the case of a patient with a QAV associated with aortic aneurysm. Pertinent literature on the QAV is reviewed, and embryological factors that may contribute to its pathogenesis are discussed.
authors.affiliation: Sarver Heart Center, University of Arizona, Tucson, AZ 85724, USA. rattaran@email.arizona.edu
authors.forename: Robert R
authors.initials: RR
authors.lastname: Attaran
authors.forename: Mohammad R
authors.initials: MR
authors.lastname: Habibzadeh
authors.forename: Gurpreet
authors.initials: G
authors.lastname: Baweja
authors.forename: Marvin J
authors.initials: MJ
authors.lastname: Slepian
mesh_terms: D000328:Adult; D001011:Aorta / Q000473:pathology*; D001014:Aortic Aneurysm / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D001021:Aortic Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology*; D001022:Aortic Valve Insufficiency / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D001027:Aortography; D018376:Cardiovascular Abnormalities / Q000209:etiology; D013504:Cardiovascular Surgical Procedures; D017548:Echocardiography, Transesophageal; D005260:Female; D006801:Humans; D035583:Rare Diseases; D017540:Tunica Media / Q000473:pathology