title: [Nasal dermoid sinus cyst: accidental coincidence or syndrome association?].
abstract: BACKGROUND
  Peters anomaly is a rare congenital glaucoma disease. The Peters' plus syndrome is characterized by distinct malformations. As some of the common craniofacial malformations like cleft lip and palate are frequent in Peters' plus syndrome, no nasal dermoid sinus cysts has been reported so far. Nasal dermoid sinus cysts usually present in isolation, although associations to other anomalies or syndromes are possible. The occurrence of such an anomaly may be either accidental, or present a syndrome association.
  
  
  METHODS
  One patient with an unilateral cleft lip and Peters' plus syndrome had undergone removal of nasal dermoid sinus cyst previously and was referred for management of recurrent disease. Complete surgical removal and plastic reconstruction was performed.
  
  
  RESULTS
  Concerning the common (lateral) cleft lip nasal deformity with no midline nasal masses, there are reasons for the assumption that a coincidence of both anomalies might be accidental. Especially in Peters' plus syndrome no occurrence of nasal dermoids has thus far been documented. However, the embryological pathway of the frontonasal region differs from lip and palate development in time and location: So unique formation of both lesions seems inconsistent. Complete surgical removal and plastic reconstruction simultaneously or in a second step are recommended.
  
  
  CONCLUSIONS
  As two cases of arhinia and Peters anomaly have been described in 1978, midline nasal masses might be a possible appearance of Peters' plus syndrome.
authors.affiliation: Klinik für Mund-, Kiefer- und Plastische Gesichtschirurgie, Universität Leipzig.
authors.forename: N C
authors.initials: NC
authors.lastname: Pausch
authors.forename: B
authors.initials: B
authors.lastname: Frerich
authors.forename: A
authors.initials: A
authors.lastname: Hemprich
authors.forename: E
authors.initials: E
authors.lastname: Brylla
authors.forename: I
authors.initials: I
authors.lastname: Sterker
authors.forename: A
authors.initials: A
authors.lastname: Merkenschlager
mesh_terms: D000015:Abnormalities, Multiple / Q000601:surgery; D000293:Adolescent; D000367:Age Factors; D002675:Child, Preschool; D002971:Cleft Lip; D002972:Cleft Palate; D019465:Craniofacial Abnormalities; D003884:Dermoid Cyst / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery; D005124:Eye Abnormalities; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D009364:Neoplasm Recurrence, Local / Q000601:surgery; D009669:Nose Neoplasms / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery; D013577:Syndrome; D014057:Tomography, X-Ray Computed