Primary atrial fibrosarcoma of the heart.
The primary fibrosarcoma of the heart is a rare tumor. There are no exact numbers about its incidence, but even among malignant cardiac tumors, only around 3% are fibrosarcomata. Symptoms are nonspecific with signs of right or left heart failure depending on localization. Diagnosis is thereby often delayed. Primary treatment of choice is surgery, followed by several possible postsurgical adjuvant strategies. Survival is poor with a mean of about 11 months.
Van Veer
Hans
H
Department of Cardiac Surgery, University Hospitals Leuven, Herestraat 49, 3000 Leuven, Belgium. hansvanveer@scarlet.be
Meuris
Bart
B
Verbeken
Eric
E
Herijgers
Paul
P
D000970:Antineoplastic Agents / Q000627:therapeutic use; D013504:Cardiovascular Surgical Procedures; D017024:Chemotherapy, Adjuvant; D017809:Fatal Outcome; D005260:Female; D005354:Fibrosarcoma / Q000473:pathology* / Q000628:therapy; D006325:Heart Atria / Q000473:pathology*; D006338:Heart Neoplasms / Q000473:pathology* / Q000628:therapy; D006801:Humans; D007150:Immunohistochemistry; D008875:Middle Aged; D008943:Mitral Valve / Q000473:pathology / Q000601:surgery; D009364:Neoplasm Recurrence, Local / Q000188:drug therapy
D000970:Antineoplastic Agents