[Extensive portocava thrombosis revealing a primary antiphospholipid syndrome: a case report].
We report a 20-year-old woman who presented with a massive portal thrombosis that rapidly extended to the superior and inferior vein cava system causing an acute Budd-Chiari syndrome. The investigations concluded to a primary antiphospholipid syndrome without any other prothrombotic factors. The outcome was fatal, 18 months later, despite anticoagulation, with hepatorenal syndrome and severe liver failure.
Belkahla
N
N
Service de gastroentérologie B, hôpital La Rabta, 1007 Tunis Jabbari, Tunisie. dcneziha@yahoo.fr
Maamouri
N
N
Ouerghi
H
H
Cheikh
I
I
Hamida
S Ben
SB
Bouzid
H
H
Ammar
A B
AB
D000328:Adult; D017153:Antibodies, Anticardiolipin / Q000097:blood; D017152:Antibodies, Antiphospholipid / Q000097:blood; D016736:Antiphospholipid Syndrome / Q000150:complications / Q000175:diagnosis* / Q000276:immunology; D006502:Budd-Chiari Syndrome / Q000175:diagnosis* / Q000209:etiology / Q000276:immunology; D017809:Fatal Outcome; D005260:Female; D006530:Hepatorenal Syndrome / Q000209:etiology; D006801:Humans; D017093:Liver Failure / Q000209:etiology; D011169:Portal Vein / Q000473:pathology; D014682:Vena Cava, Inferior / Q000473:pathology; D020246:Venous Thrombosis / Q000175:diagnosis* / Q000209:etiology
D017153:Antibodies, Anticardiolipin; D017152:Antibodies, Antiphospholipid