title: Management of primary pulmonary artery sarcoma: experience of a single center.
abstract: Primary sarcoma of the pulmonary artery (PSPA) is extremely rare. Many cases are misdiagnosed as pulmonary arterial hypertension (PAH) because of chronic thromboembolic disease (CTD). Four cases of PSPA with the initial misdiagnosis are reported. The presence of a unique mass in the main pulmonary artery or proximal branches, rapidly progressive dyspnea, and constitutional symptoms should raise the suspicion of PSPA. The pathological diagnosis is usually confirmed during surgery, which is done along with adjuvant chemotherapy, the treatment of choice.
authors.affiliation: Department of Cardiology, Hospital Virgen de la Salud, Toledo, Spain.
authors.forename: Covadonga
authors.initials: C
authors.lastname: Fernández-Golfín
authors.forename: Pilar
authors.initials: P
authors.lastname: Escribano
authors.forename: José
authors.initials: J
authors.lastname: Cortina
authors.forename: Rocío
authors.initials: R
authors.lastname: Tello
authors.forename: Felipe
authors.initials: F
authors.lastname: Hernández
authors.forename: Fernando
authors.initials: F
authors.lastname: López-Rios
authors.forename: Juan
authors.initials: J
authors.lastname: Delgado Jiménez
authors.forename: Carlos
authors.initials: C
authors.lastname: Saenz de la Calzada
mesh_terms: D000328:Adult; D017024:Chemotherapy, Adjuvant; D003951:Diagnostic Errors; D004417:Dyspnea / Q000209:etiology; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000556:secondary; D008297:Male; D008875:Middle Aged; D011651:Pulmonary Artery / Q000473:pathology* / Q000601:surgery; D012509:Sarcoma / Q000175:diagnosis* / Q000628:therapy; D019043:Vascular Neoplasms / Q000175:diagnosis* / Q000628:therapy