Renal angiomyolipoma with intravascular extension into the inferior vena cava: a case report and review of the literature.
A 42-year-old woman with tuberous sclerosis (TS) presented with acute right-sided flank pain. Imaging studies demonstrated numerous bilateral renal angiomyolipomas (AML), the largest located within the right upper pole, extending into the venous system to the level of the infra-hepatic inferior vena cava (IVC). Intravascular extension of AML is quite rare, however, may potentially result in fatal complications if not appropriately treated. We present a case report and a description of the surgical management, and provide a review of the literature concerning this rare finding.
Schade
George R
GR
Section of Urology, University of Chicago Medical Center, Chicago, Illinois 60637, USA.
Gofrit
Ofer N
ON
Zorn
Kevin C
KC
D000328:Adult; D018207:Angiomyolipoma / Q000453:epidemiology / Q000473:pathology* / Q000601:surgery; D015897:Comorbidity; D005260:Female; D021501:Flank Pain / Q000209:etiology; D006801:Humans; D007680:Kidney Neoplasms / Q000453:epidemiology / Q000473:pathology* / Q000601:surgery; D008279:Magnetic Resonance Imaging; D009361:Neoplasm Invasiveness; D014402:Tuberous Sclerosis / Q000453:epidemiology; D019043:Vascular Neoplasms / Q000473:pathology*; D014682:Vena Cava, Inferior / Q000473:pathology*