Cardiac liposarcoma and bilateral ovarian mature teratoma in a patient with congenital heart disease and f-anisosplenia.
A 10-year-old female with atrial septal defect presented with bilateral ovarian mature cystic teratomas. Three spleniculi adjacent to the main spleen were noticed while the endoscopic surgery. Two years later a heart tumor was discovered which led to death. Pathologic examination of samples of the mass proved it to be a liposarcoma. The unusual combination of atrial septal defect, f-anisosplenia (female, congenital heart disease, multiple unevenly-sized spleens, left lung type pulmonary isomerism), bilateral ovarian mature cystic teratomas and liposarcoma of the heart appears to be a unique presentation.
Pollono
Daniel G
DG
Oncology Unit, "Superiora Sor María Ludovica" Children's Hospital, La Plata, Argentina.
Drut
Ricardo
R
D000015:Abnormalities, Multiple; D002648:Child; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications*; D006338:Heart Neoplasms / Q000150:complications*; D006801:Humans; D008080:Liposarcoma / Q000150:complications*; D010051:Ovarian Neoplasms / Q000150:complications*; D013154:Spleen / Q000002:abnormalities*; D013724:Teratoma / Q000150:complications*