Management of primary pulmonary artery sarcoma: experience of a single center.
Primary sarcoma of the pulmonary artery (PSPA) is extremely rare. Many cases are misdiagnosed as pulmonary arterial hypertension (PAH) because of chronic thromboembolic disease (CTD). Four cases of PSPA with the initial misdiagnosis are reported. The presence of a unique mass in the main pulmonary artery or proximal branches, rapidly progressive dyspnea, and constitutional symptoms should raise the suspicion of PSPA. The pathological diagnosis is usually confirmed during surgery, which is done along with adjuvant chemotherapy, the treatment of choice.
Fernández-Golfín
Covadonga
C
Department of Cardiology, Hospital Virgen de la Salud, Toledo, Spain.
Escribano
Pilar
P
Cortina
José
J
Tello
Rocío
R
Hernández
Felipe
F
López-Rios
Fernando
F
Delgado Jiménez
Juan
J
Saenz de la Calzada
Carlos
C
D000328:Adult; D017024:Chemotherapy, Adjuvant; D003951:Diagnostic Errors; D004417:Dyspnea / Q000209:etiology; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000556:secondary; D008297:Male; D008875:Middle Aged; D011651:Pulmonary Artery / Q000473:pathology* / Q000601:surgery; D012509:Sarcoma / Q000175:diagnosis* / Q000628:therapy; D019043:Vascular Neoplasms / Q000175:diagnosis* / Q000628:therapy