title: [Extensive portocava thrombosis revealing a primary antiphospholipid syndrome: a case report].
abstract: We report a 20-year-old woman who presented with a massive portal thrombosis that rapidly extended to the superior and inferior vein cava system causing an acute Budd-Chiari syndrome. The investigations concluded to a primary antiphospholipid syndrome without any other prothrombotic factors. The outcome was fatal, 18 months later, despite anticoagulation, with hepatorenal syndrome and severe liver failure.
authors.affiliation: Service de gastroentérologie B, hôpital La Rabta, 1007 Tunis Jabbari, Tunisie. dcneziha@yahoo.fr
authors.forename: N
authors.initials: N
authors.lastname: Belkahla
authors.forename: N
authors.initials: N
authors.lastname: Maamouri
authors.forename: H
authors.initials: H
authors.lastname: Ouerghi
authors.forename: I
authors.initials: I
authors.lastname: Cheikh
authors.forename: S Ben
authors.initials: SB
authors.lastname: Hamida
authors.forename: H
authors.initials: H
authors.lastname: Bouzid
authors.forename: A B
authors.initials: AB
authors.lastname: Ammar
mesh_terms: D000328:Adult; D017153:Antibodies, Anticardiolipin / Q000097:blood; D017152:Antibodies, Antiphospholipid / Q000097:blood; D016736:Antiphospholipid Syndrome / Q000150:complications / Q000175:diagnosis* / Q000276:immunology; D006502:Budd-Chiari Syndrome / Q000175:diagnosis* / Q000209:etiology / Q000276:immunology; D017809:Fatal Outcome; D005260:Female; D006530:Hepatorenal Syndrome / Q000209:etiology; D006801:Humans; D017093:Liver Failure / Q000209:etiology; D011169:Portal Vein / Q000473:pathology; D014682:Vena Cava, Inferior / Q000473:pathology; D020246:Venous Thrombosis / Q000175:diagnosis* / Q000209:etiology
chemical_list: D017153:Antibodies, Anticardiolipin; D017152:Antibodies, Antiphospholipid