title: Aberrant right coronary artery occlusion during the percutaneous pulmonary trunk stenting in a patient with tetralogy of Fallot.
abstract: Aberrant coronary arteries are frequently observed in patients presenting with Fallot's tetralogy (TOF). Before the complete surgical repair of the TOF, the percutaneously performed pulmonary trunk (PT) angioplasty is often performed in order to temporarily increase the pulmonary circulation, thus increasing the pulmonary vessel size, finally improving surgical outcome. This case reports a 12-year-old boy with a TOF insufficiently improved by surgical correction, in whom a PT angioplasty with stent implantation was complicated by an extrinsic compression of an aberrant right coronary artery (RCA) causing a myocardial ischemia with severe hypotension. The RCA, originating from the left anterior descending coronary artery, passed through the aortic root and the PT and was thus compressed by the PT-stent. Finally the RCA was successfully treated with standard coronary balloon angioplasty and stenting, improving myocardial perfusion and the hemodynamics of the patient, who finally died several days thereafter due to septic shock and massive pulmonary embolism.
authors.affiliation: Cardiology Center, University Hospital of Geneva, Rue Micheli du Crest 24, 1211, Geneva 14, Switzerland.
authors.forename: Xavier
authors.initials: X
authors.lastname: Perret
authors.forename: Robert F
authors.initials: RF
authors.lastname: Bonvini
authors.forename: Yacine
authors.initials: Y
authors.lastname: Aggoun
authors.forename: Vitali
authors.initials: V
authors.lastname: Verin
mesh_terms: D000800:Angioplasty, Balloon / Q000009:adverse effects* / Q000295:instrumentation; D015906:Angioplasty, Balloon, Coronary / Q000295:instrumentation; D006348:Cardiac Surgical Procedures; D002648:Child; D017023:Coronary Angiography; D003326:Coronary Circulation; D023921:Coronary Stenosis / Q000000981:diagnostic imaging / Q000209:etiology* / Q000628:therapy; D003330:Coronary Vessel Anomalies / Q000150:complications* / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000628:therapy; D017809:Fatal Outcome; D006801:Humans; D007022:Hypotension / Q000209:etiology; D008297:Male; D017202:Myocardial Ischemia / Q000209:etiology; D011652:Pulmonary Circulation; D011666:Pulmonary Valve Stenosis / Q000150:complications / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000628:therapy*; D015607:Stents; D013771:Tetralogy of Fallot / Q000150:complications / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000628:therapy*