Secondary cutaneous nodular AA amyloidosis in a patient with primary Sjögren syndrome and celiac disease.
We describe a 62-year-old female with primary Sjögren syndrome and myopathy, severe osteoporosis, and vertebral fractures that were attributed to celiac disease. A year after the diagnosis, she developed a skin nodule on the extensor surface of her right elbow, which was due to an amyloid deposit of AA type. Amyloidosis, although relatively common in some chronic inflammatory diseases, has been uncommon in Sjögren syndrome or celiac disease. Visceral amyloid was not found in this patient.
Katsikas
Georgios A
GA
Department of Rheumatology, Evangelismos Hospital, Athens, Greece. ykatsikas@hotmail.com
Maragou
Maria
M
Rontogianni
Demetra
D
Gouma
Paraskevi
P
Koutsouvelis
Ioannis
I
Kappou-Rigatou
Iris
I
D000686:Amyloidosis / Q000150:complications* / Q000473:pathology; D000893:Anti-Inflammatory Agents / Q000627:therapeutic use; D050071:Bone Density Conservation Agents / Q000627:therapeutic use; D002446:Celiac Disease / Q000150:complications* / Q000178:diet therapy; D005260:Female; D006801:Humans; D008875:Middle Aged; D012859:Sjogren's Syndrome / Q000150:complications* / Q000188:drug therapy
D000893:Anti-Inflammatory Agents; D050071:Bone Density Conservation Agents