Primary intestinal lymphangiectasia as a component of autoimmune polyglandular syndrome type I: a report of 2 cases.
Chronic diarrhea and steatorrhea occur frequently in patients with autoimmune polyglandular syndrome (APS) type I. Intestinal lymphangiectasia has been reported earlier as a cause of steatorrhea in a young girl with APS Type I. We describe 2 patients with APS Type I who were found to have intestinal lymphangiectasia, one of whom had symptomatic protein-losing enteropathy.
Makharia
Govind K
GK
Department of Gastroenterology and Human Nutrition, All India Institute of Medical Sciences, New Delhi 110 029, India. govindmakharia@gmail.com
Tandon
Nikhil
N
Stephen
Neil de Jesus Rangel
Nde J
Gupta
Siddhartha Datta
SD
Tandon
Rakesh K
RK
D000328:Adult; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008201:Lymphangiectasis, Intestinal / Q000175:diagnosis / Q000209:etiology*; D008297:Male; D016884:Polyendocrinopathies, Autoimmune / Q000150:complications* / Q000175:diagnosis