title: Primary intestinal lymphangiectasia as a component of autoimmune polyglandular syndrome type I: a report of 2 cases.
abstract: Chronic diarrhea and steatorrhea occur frequently in patients with autoimmune polyglandular syndrome (APS) type I. Intestinal lymphangiectasia has been reported earlier as a cause of steatorrhea in a young girl with APS Type I. We describe 2 patients with APS Type I who were found to have intestinal lymphangiectasia, one of whom had symptomatic protein-losing enteropathy.
authors.affiliation: Department of Gastroenterology and Human Nutrition, All India Institute of Medical Sciences, New Delhi 110 029, India. govindmakharia@gmail.com
authors.forename: Govind K
authors.initials: GK
authors.lastname: Makharia
authors.forename: Nikhil
authors.initials: N
authors.lastname: Tandon
authors.forename: Neil de Jesus Rangel
authors.initials: Nde J
authors.lastname: Stephen
authors.forename: Siddhartha Datta
authors.initials: SD
authors.lastname: Gupta
authors.forename: Rakesh K
authors.initials: RK
authors.lastname: Tandon
mesh_terms: D000328:Adult; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008201:Lymphangiectasis, Intestinal / Q000175:diagnosis / Q000209:etiology*; D008297:Male; D016884:Polyendocrinopathies, Autoimmune / Q000150:complications* / Q000175:diagnosis