title: [Palliative right ventricular outflow reconstruction in tetralogy of Fallot with pulmonary atresia and aberrant right subclavian artery; report of a case].
abstract: A 1-month-old girl weighting 3.1 kg was diagnosed as tetralogy of Fallot (TOF) with pulmonary artery atresia (PA) and aberrant right subclavian artery. Before the operation, pulmonary blood flow from a ducus arteriosus was maintained by lipo prostaglandin E1 (PGE1). The patient underwent palliative right ventricular outflow tract reconstruction (pRVOTR) because the proximal aberrant right subclavian artery was stenotic and the ductus arteriosus and branch of the left pulmonary artery were so close. Postoperative course was uneventful and pulmonary artery showed good growth. The pRVOTR as 1st procedure is a useful method for hypoplastic pulmonary artery to get equal and good growth. Although there are controversies about the size of right ventricular outflow tract (RVOT), 5 or 6 mm diameter of RVOT is recommended for the operative repair of hypoplastic left heart syndrome. We concluded that the pRVOTR should be one of the options as 1st palliative procedure for TOF with PA and diminutive pulmonary artery.
authors.affiliation: Department of Thoracic and Cardiovascular Surgery, Hirosaki University School of Medicine, Hirosaki, Japan.
authors.forename: Kenichi
authors.initials: K
authors.lastname: Watanabe
authors.forename: K
authors.initials: K
authors.lastname: Daitoku
authors.forename: Y
authors.initials: Y
authors.lastname: Suzuki
authors.forename: T
authors.initials: T
authors.lastname: Kawamura
authors.forename: S
authors.initials: S
authors.lastname: Yamauchi
authors.forename: M
authors.initials: M
authors.lastname: Minakawa
authors.forename: K
authors.initials: K
authors.lastname: Fukui
authors.forename: I
authors.initials: I
authors.lastname: Fukuda
mesh_terms: D000015:Abnormalities, Multiple / Q000601:surgery*; D013504:Cardiovascular Surgical Procedures / Q000379:methods*; D005260:Female; D006352:Heart Ventricles / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D010166:Palliative Care; D011651:Pulmonary Artery / Q000601:surgery; D018633:Pulmonary Atresia / Q000601:surgery*; D013348:Subclavian Artery / Q000002:abnormalities*; D013771:Tetralogy of Fallot / Q000601:surgery*