title: [Oropharyngeal kaposiform hemangioendothelioma].
abstract: The kaposiform hemangioendothelioma is a very infrequent tumor proceeding from the endothelial-derived spindle cells, more often found on the limbs, although peritoneal, retroperitoneal and sacrum locations are also prevailing. Head and neck are exceptional locations. The kaposiform hemangioendothelioma is almost exclusively found in children and early adolescents, and it is highly associated with the Kasabach-Merritt syndrome and lymphangiomatosis. The main treatment is the tumor surgical removal, including wide margins, plus supporting therapy when Kasabach-Merritt syndrome is linked. We report an isolated oropharyngeal kaposiform hemangioendothelioma 9-10-year old male case.
authors.affiliation: Servicio de Otorrinolaringología, Hospital San Agustín, SESPA, Avilés, España.
authors.forename: Eduardo
authors.initials: E
authors.lastname: Maseda
authors.forename: Rafael
authors.initials: R
authors.lastname: Blanco
authors.forename: Armando
authors.initials: A
authors.lastname: Ablanedo
authors.forename: Eduardo
authors.initials: E
authors.lastname: Iglesias
mesh_terms: D000328:Adult; D001706:Biopsy; D003937:Diagnosis, Differential; D006390:Hemangioendothelioma / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008297:Male; D009959:Oropharyngeal Neoplasms / Q000473:pathology* / Q000601:surgery; D014067:Tonsillar Neoplasms / Q000473:pathology* / Q000601:surgery; D014983:Xeroderma Pigmentosum / Q000473:pathology*