Intraorbital and intracranial soft-tissue glomus tumor in an 8-year-old child. Case report.
Soft-tissue glomus tumors (or glomangiomas) are unrelated to neuroendocrine paragangliomas (glomus tympanicum, jugulare, and vagale). The authors present the first reported case of an orbital soft-tissue glomus tumor in a child. An 8-year-old girl developed rapidly progressive right-eye blindness, proptosis, and a sixth cranial nerve palsy. Magnetic resonance imaging demonstrated a homogeneously enhancing lesion extending from the right orbit through the superior orbital fissure to the cavernous sinus and middle cranial fossa. A biopsy specimen demonstrated the lesion to be a soft-tissue glomus tumor. Following angiography and embolization, a gross-total resection of the tumor was achieved. The patient was treated with adjuvant proton-beam radiotherapy. At 24 months follow-up her proptosis and sixth cranial nerve palsy had resolved and there was no evidence of tumor recurrence.
Hankinson
Todd C
TC
Department of Neurosurgery, Columbia University, College of Physicians and Surgeons, New York, New York 10032, USA. tch12@columbia.edu
Ogden
Alfred T
AT
Canoll
Peter
P
Garvin
James H
JH
Kazim
Michael
M
Bruce
Jeffrey N
JN
Feldstein
Neil A
NA
Anderson
Richard C E
RC
D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D005918:Glomus Tumor / Q000473:pathology* / Q000628:therapy; D006801:Humans; D009918:Orbital Neoplasms / Q000473:pathology* / Q000628:therapy; D010235:Paraganglioma / Q000175:diagnosis