title: Clinical diagnosis and oral rehabilitation of a patient with amelogenesis imperfecta: a case report.
abstract: OBJECTIVE
  This clinical report describes the oral rehabilitation of a young female patient diagnosed with the hypocalcified, autosomal recessive type of Amelogenesis imperfecta (AI). A brief discussion on diagnosis of AI is also included.
  
  
  BACKGROUND
  AI has been defined as a group of hereditary enamel defects not associated with evidence of systemic disease. It can be characterized by enamel hypoplasia and/or hypomaturation or hypocalcification of the existing teeth. Restoration for patients with this condition should be oriented toward the functional and esthetic rehabilitation and the protection of these teeth.
  
  
  METHODS
  A 31-year-old female patient presented with concerns including extreme sensitivity; dissatisfaction with size, shape, and shade of teeth; and poor masticatory efficiency. She was very conscious about the appearance of her teeth and reported that her primary dentition was affected in the same manner. The specific objectives of this treatment were to eliminate tooth sensitivity, enhance esthetics, and restore masticatory function. Treatment included crown lengthening procedures and placement of anterior and posterior metal-ceramic crowns. A 12-month follow-up with clinical and radiographic examinations revealed no evidence of any untoward effects of the treatment on the restored teeth or their supporting structures.
  
  
  CONCLUSIONS
  Management of a patient with AI is a challenge for the clinician. The treatment options vary considerably depending on several factors such as the age of the patient, socio-economic status, periodontal condition, loss of tooth structure, severity of the disorder, and, most importantly, the patient's cooperation. The clinician has to consider the long-term prognosis of the treatment outcome. This clinical report describes the fabrication of metal ceramic and all metal crowns for the restoration of severely worn teeth in a patient with AI which requires meticulous maintenance of oral hygiene and patient co-operation.
authors.affiliation: Department of Oral Medicine & Radiology, Manipal College of Dental Sciences, Manipal, Karnataka, India. amar_as2002@yahoo.co.in
authors.forename: Amar A
authors.initials: AA
authors.lastname: Sholapurkar
authors.forename: Robin Mathai
authors.initials: RM
authors.lastname: Joseph
authors.forename: Jothi M
authors.initials: JM
authors.lastname: Varghese
authors.forename: Krishna
authors.initials: K
authors.lastname: Neelagiri
authors.forename: Shashi Rashmi R
authors.initials: SR
authors.lastname: Acharya
authors.forename: Veena
authors.initials: V
authors.lastname: Hegde
authors.forename: Keerthilatha M
authors.initials: KM
authors.lastname: Pai
authors.forename: Mahalinga
authors.initials: M
authors.lastname: Bhat
mesh_terms: D000328:Adult; D000567:Amelogenesis Imperfecta / Q000145:classification / Q000175:diagnosis* / Q000628:therapy; D016556:Crown Lengthening; D003442:Crowns; D003731:Dental Caries / Q000628:therapy; D003776:Dental Porcelain; D017267:Dental Prosthesis Design; D003789:Dental Pulp Exposure / Q000628:therapy; D003807:Dentin Sensitivity / Q000628:therapy; D004955:Esthetics, Dental; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D016876:Metal Ceramic Alloys; D009065:Mouth Rehabilitation; D010347:Patient Care Planning; D019217:Tooth Attrition / Q000628:therapy
chemical_list: D016876:Metal Ceramic Alloys; D003776:Dental Porcelain