title: Intraorbital and intracranial soft-tissue glomus tumor in an 8-year-old child. Case report.
abstract: Soft-tissue glomus tumors (or glomangiomas) are unrelated to neuroendocrine paragangliomas (glomus tympanicum, jugulare, and vagale). The authors present the first reported case of an orbital soft-tissue glomus tumor in a child. An 8-year-old girl developed rapidly progressive right-eye blindness, proptosis, and a sixth cranial nerve palsy. Magnetic resonance imaging demonstrated a homogeneously enhancing lesion extending from the right orbit through the superior orbital fissure to the cavernous sinus and middle cranial fossa. A biopsy specimen demonstrated the lesion to be a soft-tissue glomus tumor. Following angiography and embolization, a gross-total resection of the tumor was achieved. The patient was treated with adjuvant proton-beam radiotherapy. At 24 months follow-up her proptosis and sixth cranial nerve palsy had resolved and there was no evidence of tumor recurrence.
authors.affiliation: Department of Neurosurgery, Columbia University, College of Physicians and Surgeons, New York, New York 10032, USA. tch12@columbia.edu
authors.forename: Todd C
authors.initials: TC
authors.lastname: Hankinson
authors.forename: Alfred T
authors.initials: AT
authors.lastname: Ogden
authors.forename: Peter
authors.initials: P
authors.lastname: Canoll
authors.forename: James H
authors.initials: JH
authors.lastname: Garvin
authors.forename: Michael
authors.initials: M
authors.lastname: Kazim
authors.forename: Jeffrey N
authors.initials: JN
authors.lastname: Bruce
authors.forename: Neil A
authors.initials: NA
authors.lastname: Feldstein
authors.forename: Richard C E
authors.initials: RC
authors.lastname: Anderson
mesh_terms: D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D005918:Glomus Tumor / Q000473:pathology* / Q000628:therapy; D006801:Humans; D009918:Orbital Neoplasms / Q000473:pathology* / Q000628:therapy; D010235:Paraganglioma / Q000175:diagnosis