[Congenital cystic adenomatoid malformation of the lung. Report of 3 cases with late presentation].
Congenital cystic adenomatoid malformation (CCAM) of the lung is a rare congenital developmental abnormality, representing about 25% of all congenital lung lesions. In many cases, respiratory distress occurs during the neonatal period, and in about 80- 85% of patients, CCAM is diagnosed before the age of two years due to respiratory infection. It is very rare that presentation is delayed until adulthood. We report three cases of CCAM presenting in adults. The diagnosis was based on clinical and radiological findings in one case and two patients were not diagnosed until surgery. The lesion was present in the right lung in two and in left lung in one patient. All patients underwent surgical resection. The result of histopathological examination confirmed CCAM Stocker type 1, without malignancy. The post operative follow up showed an excellent recovery. Clinicians and pathologists need to be aware of the fact that CCAM can be present for the first time in adolescents or in adults. The clinical diagnosis is suggested by radiographic findings and is confirmed at pathology as surgery is generally indicated.
Ayadi-Kaddour
A
A
Service d'Anatomie et de cytologie pathologiques, Hôpital Abderrahman-Mami, Ariana, Tunisie. kaddour1fr@yahoo.fr
Chaabouni
S
S
Meraï
S
S
Ben Mrad
S
S
Djilani
H
H
Tritar
F
F
El Mezni
F
F
D000293:Adolescent; D000328:Adult; D003371:Cough / Q000209:etiology; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000175:diagnosis* / Q000601:surgery; D004417:Dyspnea / Q000209:etiology; D006801:Humans; D008297:Male