title: Hybrid approach in a case of arterial tortuosity syndrome.
abstract: Arterial tortuosity syndrome is a rare connective tissue disorder characterised by elongation, tortuosity, stenosis and aneurysms of the large and middle-sized arteries. The symptomatology is correlated to the artery affected by the pathology with correlated stenosis. We describe our hybrid surgical procedure in the treatment of a case of kinking of the pulmonary branches with significant gradient and hypertension. Aortic arch and supraaortic vessels presented various deviousness without hemodynamic alterations.
authors.affiliation: Department of Cardio-Thoracic and Respiratory Sciences, Second University of Naples, Naples, Italy. marianovicchio@libero.it
authors.forename: Mariano
authors.initials: M
authors.lastname: Vicchio
authors.forename: Giuseppe
authors.initials: G
authors.lastname: Santoro
authors.forename: Marianna
authors.initials: M
authors.lastname: Carrozza
authors.forename: Giuseppe
authors.initials: G
authors.lastname: Caianiello
mesh_terms: D001013:Aorta, Thoracic / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D002315:Cardiopulmonary Bypass; D002675:Child, Preschool; D003240:Connective Tissue Diseases / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D003251:Constriction, Pathologic; D006439:Hemodynamics; D006801:Humans; D010348:Patient Care Team; D010496:Pericardium / Q000601:surgery; D011651:Pulmonary Artery / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D011859:Radiography; D015607:Stents; D013249:Sternum / Q000601:surgery; D013536:Suture Techniques; D013577:Syndrome; D016896:Treatment Outcome; D054079:Vascular Malformations / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D014656:Vascular Surgical Procedures / Q000295:instrumentation