Intracranial epithelioid hemangioendothelioma.
BACKGROUND
Epithelioid hemangioendothelioma (EHE) is an uncommon soft-tissue vascular neoplasm. Although a well-defined entity outside the neuraxis, its intracranial occurrence is rare. Literature review revealed 35 reported cases till date.


METHODS
The authors report a case of intracranial EHE in a 15-year-old girl, who presented with a short history and unusual radiology. Following radical removal, the lesion recurred within 1 month and progressed to terminal stages. This tumor is thought to have an indolent intermediate malignancy potential and such rapid progression has not been reported so far.
Mohan S
Murali
M
Post Graduate Institute of Neurological Surgery, ALNC, VHS Hospital, Taramani, Chennai, 600 113, India. drmurali78@rediffmail.com
Symss
Nigel Peter
NP
Pande
Anil
A
Chakravarthy
Vasudevan M
VM
Ramamurthi
Ravi
R
D000293:Adolescent; D018952:Antigens, CD34 / Q000378:metabolism; D005260:Female; D018323:Hemangioendothelioma, Epithelioid / Q000378:metabolism / Q000473:pathology / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods; D014057:Tomography, X-Ray Computed / Q000379:methods; D019043:Vascular Neoplasms / Q000378:metabolism / Q000473:pathology / Q000601:surgery
D018952:Antigens, CD34