Corneal opacities in the Hallermann-Streiff syndrome.
We present six patients with typical Hallermann-Streiff syndrome. All have microphthalmia and were operated for congenital cataract. Three of the patients developed a severe glaucoma and one patient presented repeated uveal effusions. Five of our patients have the same pattern of corneal stromal opacities. The opacities are ill defined and bilateral; the stroma between the opacities is clear. The opacities are observed in two children around the age of 5. Follow up of 10 years did not reveal a manifest increase of the lesions. The authors believe that corneal stromal opacities are a feature of the Hallermann-Streiff syndrome and they would urge ophthalmologists to look for this.
Roulez
Françoise M
FM
Hopital Universitaire des Enfants Reine Fabiola, U.L.B., Ophthalmology Department, Brussels, Belgium. FRANCOISE.ROULEZ@huderf.be
Schuil
Josée
J
Meire
Françoise M
FM
D000293:Adolescent; D000328:Adult; D002386:Cataract / Q000151:congenital; D002387:Cataract Extraction; D002648:Child; D003318:Corneal Opacity / Q000150:complications* / Q000175:diagnosis / Q000235:genetics; D003319:Corneal Stroma / Q000473:pathology*; D005260:Female; D005451:Fluorescein Angiography; D006210:Hallermann's Syndrome / Q000150:complications* / Q000175:diagnosis / Q000235:genetics; D006801:Humans; D008297:Male; D008850:Microphthalmos / Q000150:complications