Dental treatment in a patient with epidermolysis bullosa.
Epidermolysis bullosa (EB) is a rare inherited group of genodermatoses characterized by mucocutaneous fragility and blister formation, either spontaneously or as a result of minimal mechanical trauma. The repetition of these episodes in the oral cavity leads to atrophy of the mucosa, causing microstomia, ankyloglossia, tongue denudation, and vestibule obliteration, characteristics that make dental treatment difficult. Patients with EB are at high risk for caries due to the presence of dental anomalies; they also tend to have a soft diet and difficulties with mechanical removal of the dental biofilm. This case report presents a patient diagnosed with EB and describes the difficulties faced by the clinician during dental treatment as well as the measures adopted to safely manage the patient's dental care.
Siqueira
Maria Alice
MA
Center of Formation of Human Resources Specialized in Dental Care for Special Needs Patients, School of Dentistry of Ribeirão Preto, University of São Paulo, Ribeirão Preto, São Paulo, Brazil.
de Souza Silva
Juliana
J
Silva
Francisco Wanderley Garcia de Paula E
FW
Díaz-Serrano
Kranya Victória
KV
Freitas
Aldevina Campos de
AC
Queiroz
Alexandra Mussolino de
AM
D000328:Adult; D000848:Anodontia / Q000209:etiology* / Q000628:therapy; D002294:Carcinoma, Squamous Cell / Q000150:complications; D017742:Dental Care for Chronically Ill; D003761:Dental Impression Technique; D003830:Denture, Partial, Fixed; D016108:Epidermolysis Bullosa Dystrophica / Q000150:complications*; D017809:Fatal Outcome; D005542:Forearm; D005808:Genes, Recessive; D006801:Humans; D008297:Male; D008865:Microstomia / Q000209:etiology*; D012878:Skin Neoplasms / Q000150:complications