Disseminated clustered juvenile xanthogranuloma: an unusual morphological variant of a common condition.
Juvenile xanthogranuloma (JXG) is a benign, self-healing non-Langerhans cell histiocytosis of unknown aetiology, most commonly occurring in infants and children. JXG is characterized by solitary or multiple yellowish cutaneous nodules, the two common clinical variants being a small nodular form and large nodular form, which frequently coexist. Unusual morphological presentations include keratotic, lichenoid, pedunculated, subcutaneous, clustered, plaque-like and giant lesions. We describe the first reported case of 'disseminated' clustered juvenile xanthogranuloma presenting in an infant.
Kaur
M R
MR
Department of Dermatology, Birmingham Children's Hospital, Birmingham, UK. manjitkaur77@hotmail.com
Brundler
M A
MA
Stevenson
O
O
Moss
C
C
D003937:Diagnosis, Differential; D006801:Humans; D007223:Infant; D014972:Xanthogranuloma, Juvenile / Q000473:pathology*