Bilateral total hip arthroplasty in Morquio-Brailsford's syndrome: a report of two cases.
We report two cases of bilateral cementless total hip arthroplasty in two young women affected by Morquio-Brailsford syndrome. Morquio-Brailsford disease belongs to the mucopolysaccharidoses; it shows growth retardation with disproportional dwarfism. Usually patients are affected by a severe joint degeneration from their 2nd or 3rd decade. Young age, severe dysplasia, and joint size are the main technical problems for a total hip replacement. Accurate radiographic and CT planning allows the use of standard prostheses instead of custom-made ones.
Tassinari
Enrico
E
1st Division, Istituto Ortopedico Rizzoli, Via Pupilli 1, 40136, Bologna, Italy. enrico.tassinari@ior.it
Boriani
Luca
L
Traina
Francesco
F
Dallari
Dante
D
Toni
Aldo
A
Giunti
Armando
A
D000328:Adult; D000769:Anesthesia, Inhalation / Q000379:methods; D019644:Arthroplasty, Replacement, Hip; D001268:Atlanto-Axial Joint / Q000473:pathology; D001864:Bone Wires; D003198:Computer Simulation; D004392:Dwarfism / Q000209:etiology; D004867:Equipment Design; D005260:Female; D006622:Hip Prosthesis; D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods; D007593:Joint Instability / Q000209:etiology / Q000473:pathology; D009085:Mucopolysaccharidosis IV / Q000150:complications*; D009809:Odontoid Process / Q000473:pathology; D015207:Osteoarthritis, Hip / Q000000981:diagnostic imaging / Q000209:etiology / Q000601:surgery*; D011859:Radiography; D025321:Surgery, Computer-Assisted