title: Bilateral total hip arthroplasty in Morquio-Brailsford's syndrome: a report of two cases.
abstract: We report two cases of bilateral cementless total hip arthroplasty in two young women affected by Morquio-Brailsford syndrome. Morquio-Brailsford disease belongs to the mucopolysaccharidoses; it shows growth retardation with disproportional dwarfism. Usually patients are affected by a severe joint degeneration from their 2nd or 3rd decade. Young age, severe dysplasia, and joint size are the main technical problems for a total hip replacement. Accurate radiographic and CT planning allows the use of standard prostheses instead of custom-made ones.
authors.affiliation: 1st Division, Istituto Ortopedico Rizzoli, Via Pupilli 1, 40136, Bologna, Italy. enrico.tassinari@ior.it
authors.forename: Enrico
authors.initials: E
authors.lastname: Tassinari
authors.forename: Luca
authors.initials: L
authors.lastname: Boriani
authors.forename: Francesco
authors.initials: F
authors.lastname: Traina
authors.forename: Dante
authors.initials: D
authors.lastname: Dallari
authors.forename: Aldo
authors.initials: A
authors.lastname: Toni
authors.forename: Armando
authors.initials: A
authors.lastname: Giunti
mesh_terms: D000328:Adult; D000769:Anesthesia, Inhalation / Q000379:methods; D019644:Arthroplasty, Replacement, Hip; D001268:Atlanto-Axial Joint / Q000473:pathology; D001864:Bone Wires; D003198:Computer Simulation; D004392:Dwarfism / Q000209:etiology; D004867:Equipment Design; D005260:Female; D006622:Hip Prosthesis; D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods; D007593:Joint Instability / Q000209:etiology / Q000473:pathology; D009085:Mucopolysaccharidosis IV / Q000150:complications*; D009809:Odontoid Process / Q000473:pathology; D015207:Osteoarthritis, Hip / Q000000981:diagnostic imaging / Q000209:etiology / Q000601:surgery*; D011859:Radiography; D025321:Surgery, Computer-Assisted