Successful living-related liver transplantation in a child with familial yellow nail syndrome and fulminant hepatic failure: report of a case.
An 11-yr-old boy with familial YNS and FHF and who underwent LRLT is presented. LRLT was performed from his father with YNS. The findings of hepatic failure resolved immediately after LRLT, but severe respiratory complications and chylous ascites were observed during the follow-up. At 12 months after successful LT, the patient has good graft function, but findings of YNS including chronic cough, lymphedema and yellow nails are still present. To the best of our knowledge, this is the first case of YNS who underwent LRLT for FHF.
Kuloğlu
Zarife
Z
Department of Pediatric Gastroenterology, School of Medicine, Ankara University, Ankara, Turkey. zarifekuloglu@yahoo.com
Ustündağ
Gonca
G
Kirsaçlioğlu
Ceyda Tuna
CT
Kansu
Aydan
A
Bingol-Kologlu
Meltem
M
Vargun
Rahsan
R
Hazinedaroğlu
Selcuk
S
Karayalçin
Selim
S
Girgin
Nurten
N
D000328:Adult; D001201:Ascites / Q000378:metabolism; D002648:Child; D003371:Cough; D005192:Family Health; D006801:Humans; D007565:Jaundice / Q000150:complications / Q000628:therapy; D008107:Liver Diseases / Q000150:complications* / Q000628:therapy; D017093:Liver Failure / Q000150:complications / Q000628:therapy; D017114:Liver Failure, Acute / Q000150:complications* / Q000628:therapy; D016031:Liver Transplantation / Q000379:methods*; D008209:Lymphedema / Q000628:therapy; D008297:Male; D009262:Nails / Q000473:pathology; D013577:Syndrome