title: Successful living-related liver transplantation in a child with familial yellow nail syndrome and fulminant hepatic failure: report of a case.
abstract: An 11-yr-old boy with familial YNS and FHF and who underwent LRLT is presented. LRLT was performed from his father with YNS. The findings of hepatic failure resolved immediately after LRLT, but severe respiratory complications and chylous ascites were observed during the follow-up. At 12 months after successful LT, the patient has good graft function, but findings of YNS including chronic cough, lymphedema and yellow nails are still present. To the best of our knowledge, this is the first case of YNS who underwent LRLT for FHF.
authors.affiliation: Department of Pediatric Gastroenterology, School of Medicine, Ankara University, Ankara, Turkey. zarifekuloglu@yahoo.com
authors.forename: Zarife
authors.initials: Z
authors.lastname: Kuloğlu
authors.forename: Gonca
authors.initials: G
authors.lastname: Ustündağ
authors.forename: Ceyda Tuna
authors.initials: CT
authors.lastname: Kirsaçlioğlu
authors.forename: Aydan
authors.initials: A
authors.lastname: Kansu
authors.forename: Meltem
authors.initials: M
authors.lastname: Bingol-Kologlu
authors.forename: Rahsan
authors.initials: R
authors.lastname: Vargun
authors.forename: Selcuk
authors.initials: S
authors.lastname: Hazinedaroğlu
authors.forename: Selim
authors.initials: S
authors.lastname: Karayalçin
authors.forename: Nurten
authors.initials: N
authors.lastname: Girgin
mesh_terms: D000328:Adult; D001201:Ascites / Q000378:metabolism; D002648:Child; D003371:Cough; D005192:Family Health; D006801:Humans; D007565:Jaundice / Q000150:complications / Q000628:therapy; D008107:Liver Diseases / Q000150:complications* / Q000628:therapy; D017093:Liver Failure / Q000150:complications / Q000628:therapy; D017114:Liver Failure, Acute / Q000150:complications* / Q000628:therapy; D016031:Liver Transplantation / Q000379:methods*; D008209:Lymphedema / Q000628:therapy; D008297:Male; D009262:Nails / Q000473:pathology; D013577:Syndrome