[Cholestasis caused by a choledochal botryoid rhabdomyosarcoma in a 22-month-old boy].
Botrioid rhabdomyosarcoma of the extrahepatic bile ducts is a rare cause of jaundice in children. It has a very poor prognosis and is rarely diagnosed preoperatively. We report a choledochal botrioid rhabdomyosarcoma in a 22-month-old boy who developed an obstructive jaundice. Radiographic explorations suggested cystic lymphangioma. The gallbladder, the cystic duct, the common bile duct and the pancreatic head were resected. The diagnosis was made on pathological examination; adjuvant chemotherapy followed. The patient was disease free 20 months following treatment.
Sassi
Samia Hannachi
SH
Service d'anatomie et de cytologie pathologiques, institut Salah Azaeiz, Bab Saadoun, 1006 Tunis, Tunisie. samia.hannachi@rns.tn
Charfi
Lamia
L
Abbes
Imen
I
Mrad
Karima
K
Dhouib
Rim
R
Hamida
Naziha Ben
NB
Oubiche
Faical
F
Barsaoui
Sihem
S
Romdhane
Khaled Ben
KB
D001650:Bile Duct Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery; D002675:Child, Preschool; D015529:Choledochal Cyst / Q000150:complications / Q000473:pathology* / Q000601:surgery; D002779:Cholestasis / Q000209:etiology*; D006801:Humans; D041781:Jaundice, Obstructive / Q000150:complications / Q000473:pathology*; D018191:Lymphangioma, Cystic / Q000150:complications / Q000473:pathology* / Q000601:surgery; D008297:Male; D012208:Rhabdomyosarcoma / Q000150:complications / Q000473:pathology*; D016896:Treatment Outcome