Neurofibroma of the porta hepatis.
Neurofibromas are generally well-circumscribed tumors of the nervous system, often found in association with neurofibromatosis 1 (NF1). They uncommonly present as a single sporadic form in the retroperitoneum and in the pancreas. We present a case of a 40-year-old man who presented with a 4- to 5-year history of right upper quadrant pain with associated nausea and vomiting. Medical imaging showed a 3.8 by 3.4-cm mass encasing the hepatic artery and the porta hepatis. Surgical resection was performed, with removal of the gallbladder. The mass was histologically diagnosed as a neurofibroma. At 1 year following his surgery, the patient is doing well.
Poon
Julius C
JC
Faculty of Medicine, University of Calgary, Calgary, AB, Canada.
Ogilvie
Travis
T
Dixon
Elijah
E
D000328:Adult; D006801:Humans; D008113:Liver Neoplasms / Q000473:pathology / Q000601:surgery*; D008297:Male; D009455:Neurofibroma / Q000473:pathology / Q000601:surgery*