An unusual presentation of malignant hepatic epithelioid haemangioendothelioma with left pleural and pulmonary localization.
Hepatic epithelioid haemangioendothelioma (HEHE) is extremely rare in children. We present an adolescent who presented with a scoliosis due to left thoracic pain. Multifocal HEHE was incidentally found during CT scan of the thorax, and confirmed with a multiphase CT scan of the abdomen, biopsy and immunochemistry. Left pleural and pulmonary involvement was suspected and later confirmed with biopsy and histopathological examination. The patient died 1 year after diagnosis. To the best of our knowledge, scoliosis has not previously been reported as the first symptom of EHE.
Department of Radiology, Mediterranean Institute for Transplantation and Advanced Specialized Therapies (IsMeTT), Via Ernesto Tricomi 1, Palermo, Italy. secaruso@ismett.edu
Settimo
S
Caruso
Roberto
R
Miraglia
Luigi
L
Maruzzelli
Marco
M
Spada
Patrizio
P
Vitulo
Marta Ida
MI
Minervini
Angelo
A
Luca
Bruno
B
Gridelli
D000293:Adolescent; D003287:Contrast Media; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D018323:Hemangioendothelioma, Epithelioid / Q000000981:diagnostic imaging*; D006801:Humans; D033162:Incidental Findings; D008175:Lung Neoplasms / Q000000981:diagnostic imaging*; D010997:Pleural Neoplasms / Q000000981:diagnostic imaging*; D012600:Scoliosis / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed / Q000379:methods*
D003287:Contrast Media