[Classification of systemic vasculitides].
Systemic vasculitides are characterized by different histological aspects: fibrinoid necrosis of the arterial wall, giant cell arteritis, non-necrotizing arteritides without granuloma or giant cell infiltration. Each histological form is associated with a spectrum of diseases with variable clinical expression: giant cell angeitides, such as Takayasu's arteritis and giant cell arteritis, necrotizing angeitides, such as polyarteritis nodosa, Kawasaki disease, Wegener's granulomatosis, Henoch-Schönlein purpura or Churg-Strauss syndrome. The detection of anti-neutrophilic cytoplasmic antibodies (ANCA) also makes it possible to classify necrotizing vasculitides by isolating a group of diseases different from necrotizing vasculitidies without ANCA (Wegener's granulomatosis, microscopic polyangitis, allergic granulomatous angiitis).
Service de médecine interne, Centre de référence maladies rares Vascularites et Sclérodermies systémiques, hôpital Cochin, Université Paris-V-René-Descartes, Paris. loic.guillevin@cch.aphp.fr
Loïc
L
Guillevin
Christian
C
Pagnoux
D000328:Adult; D000792:Angiography; D019268:Antibodies, Antineutrophil Cytoplasmic / Q000276:immunology; D015267:Churg-Strauss Syndrome / Q000175:diagnosis / Q000473:pathology; D003449:Cryoglobulinemia / Q000175:diagnosis; D003937:Diagnosis, Differential; D005260:Female; D013700:Giant Cell Arteritis / Q000175:diagnosis / Q000209:etiology / Q000473:pathology; D014890:Granulomatosis with Polyangiitis / Q000175:diagnosis / Q000473:pathology; D006402:Hematologic Diseases / Q000150:complications; D006801:Humans; D011695:IgA Vasculitis / Q000175:diagnosis / Q000473:pathology; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D009080:Mucocutaneous Lymph Node Syndrome / Q000175:diagnosis; D010257:Paraneoplastic Syndromes / Q000175:diagnosis; D010488:Polyarteritis Nodosa / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000473:pathology; D013625:Takayasu Arteritis / Q000175:diagnosis; D013919:Thromboangiitis Obliterans / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000473:pathology; D014657:Vasculitis / Q000145:classification* / Q000175:diagnosis / Q000209:etiology / Q000276:immunology / Q000473:pathology
D019268:Antibodies, Antineutrophil Cytoplasmic