An unusual presentation of malignant hepatic epithelioid haemangioendothelioma with left pleural and pulmonary localization.
Hepatic epithelioid haemangioendothelioma (HEHE) is extremely rare in children. We present an adolescent who presented with a scoliosis due to left thoracic pain. Multifocal HEHE was incidentally found during CT scan of the thorax, and confirmed with a multiphase CT scan of the abdomen, biopsy and immunochemistry. Left pleural and pulmonary involvement was suspected and later confirmed with biopsy and histopathological examination. The patient died 1 year after diagnosis. To the best of our knowledge, scoliosis has not previously been reported as the first symptom of EHE.
Caruso
Settimo
S
Department of Radiology, Mediterranean Institute for Transplantation and Advanced Specialized Therapies (IsMeTT), Via Ernesto Tricomi 1, Palermo, Italy. secaruso@ismett.edu
Miraglia
Roberto
R
Maruzzelli
Luigi
L
Spada
Marco
M
Vitulo
Patrizio
P
Minervini
Marta Ida
MI
Luca
Angelo
A
Gridelli
Bruno
B
D000293:Adolescent; D003287:Contrast Media; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D018323:Hemangioendothelioma, Epithelioid / Q000000981:diagnostic imaging*; D006801:Humans; D033162:Incidental Findings; D008175:Lung Neoplasms / Q000000981:diagnostic imaging*; D010997:Pleural Neoplasms / Q000000981:diagnostic imaging*; D012600:Scoliosis / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed / Q000379:methods*
D003287:Contrast Media