[Classification of systemic vasculitides].
Systemic vasculitides are characterized by different histological aspects: fibrinoid necrosis of the arterial wall, giant cell arteritis, non-necrotizing arteritides without granuloma or giant cell infiltration. Each histological form is associated with a spectrum of diseases with variable clinical expression: giant cell angeitides, such as Takayasu's arteritis and giant cell arteritis, necrotizing angeitides, such as polyarteritis nodosa, Kawasaki disease, Wegener's granulomatosis, Henoch-Schönlein purpura or Churg-Strauss syndrome. The detection of anti-neutrophilic cytoplasmic antibodies (ANCA) also makes it possible to classify necrotizing vasculitides by isolating a group of diseases different from necrotizing vasculitidies without ANCA (Wegener's granulomatosis, microscopic polyangitis, allergic granulomatous angiitis).
Guillevin
Loïc
L
Service de médecine interne, Centre de référence maladies rares Vascularites et Sclérodermies systémiques, hôpital Cochin, Université Paris-V-René-Descartes, Paris. loic.guillevin@cch.aphp.fr
Pagnoux
Christian
C
D000328:Adult; D000792:Angiography; D019268:Antibodies, Antineutrophil Cytoplasmic / Q000276:immunology; D015267:Churg-Strauss Syndrome / Q000175:diagnosis / Q000473:pathology; D003449:Cryoglobulinemia / Q000175:diagnosis; D003937:Diagnosis, Differential; D005260:Female; D013700:Giant Cell Arteritis / Q000175:diagnosis / Q000209:etiology / Q000473:pathology; D014890:Granulomatosis with Polyangiitis / Q000175:diagnosis / Q000473:pathology; D006402:Hematologic Diseases / Q000150:complications; D006801:Humans; D011695:IgA Vasculitis / Q000175:diagnosis / Q000473:pathology; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D009080:Mucocutaneous Lymph Node Syndrome / Q000175:diagnosis; D010257:Paraneoplastic Syndromes / Q000175:diagnosis; D010488:Polyarteritis Nodosa / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000473:pathology; D013625:Takayasu Arteritis / Q000175:diagnosis; D013919:Thromboangiitis Obliterans / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000473:pathology; D014657:Vasculitis / Q000145:classification* / Q000175:diagnosis / Q000209:etiology / Q000276:immunology / Q000473:pathology
D019268:Antibodies, Antineutrophil Cytoplasmic