Persistence of left supracardinal vein in an adult patient with heart-hand syndrome and cardiac pacemaker.
A patient with a sporadic heart-hand syndrome, which includes thumb hypoplasia, septum primum atrial septal defect, and cleft mitral valve is described. During attempted placement of a pacemaker lead, persistence of left superior and inferior vena cava was found in addition to the right-sided caval veins. This corresponds to persistence of left-sided supracardinal vein present during fetal development.
Nemec
Jan
J
University of Pittsburgh-Cardiovascular Institute, Pittsburgh, PA 15261, USA. limidus@hotmail.com
Heifetz
Steven
S
D000368:Aged; D005260:Female; D006343:Heart Septal Defects; D006344:Heart Septal Defects, Atrial; D006801:Humans; D008943:Mitral Valve / Q000002:abnormalities*; D010138:Pacemaker, Artificial; D013577:Syndrome; D013933:Thumb / Q000002:abnormalities*; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000601:surgery; D014683:Vena Cava, Superior / Q000002:abnormalities* / Q000601:surgery