Topsy-turvy heart with associated congenital tracheobronchial stenosis and airway compression requiring surgical reconstruction.
We describe a case of "topsy-turvy heart" that necessitated simultaneous left tracheobronchial repair, aortic arch reconstruction, and bronchial stenting in an 11-month-old girl. This case highlights the significant therapeutic dilemmas clinicians are faced with when dealing with conditions having an unknown natural history and unpredictable surgical outcomes, and reinforces the need for these patients to be managed by a multidisciplinary team approach.
Division of Cardiovascular Surgery, Hospital for Sick Children, Toronto, Ontario, Canada.
Patricio
P
Herrera
Christopher A
CA
Caldarone
Vito
V
Forte
Helen
H
Holtby
Peter
P
Cox
Priscilla
P
Chiu
Peter C W
PC
Kim
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery*; D000402:Airway Obstruction / Q000175:diagnosis / Q000601:surgery; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000601:surgery; D001980:Bronchi / Q000002:abnormalities; D001999:Bronchoscopy; D006348:Cardiac Surgical Procedures / Q000379:methods*; D003131:Combined Modality Therapy; D003251:Constriction, Pathologic / Q000151:congenital / Q000601:surgery; D015150:Echocardiography, Doppler; D005260:Female; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D007223:Infant; D035583:Rare Diseases; D019651:Plastic Surgery Procedures / Q000379:methods*; D015619:Respiratory System Abnormalities / Q000175:diagnosis / Q000601:surgery*; D018570:Risk Assessment; D012720:Severity of Illness Index; D013908:Thoracotomy / Q000379:methods; D014057:Tomography, X-Ray Computed; D014132:Trachea / Q000002:abnormalities; D016896:Treatment Outcome