Unusual coarctation-the PHACE syndrome: report of three cases.
OBJECTIVE
To report the clinical features, nature of vasculopathy observed and the management instituted in three cases of PHACE syndrome.


RESULTS
All three patients were noted to have diffuse vasculopathy and aortic arch hypoplasia in addition to aortic coarctation adding substantial surgical risk or making surgery palliative.


CONCLUSIONS
PHACE syndrome should be considered in the differential diagnosis of aortic coarctation associated with aortic arch hypoplasia.
Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, Kerala, India. bijulalsasidharan@gmail.com
Sasidharan
S
Bijulal
Sivasubramanian
S
Sivasankaran
Kavassery M
KM
Krishnamoorthy
Thomas
T
Titus
Jaganmohan A
JA
Tharakan
Soman R
SR
Krishnamanohar
D000015:Abnormalities, Multiple; D000328:Adult; D001013:Aorta, Thoracic / Q000601:surgery; D001017:Aortic Coarctation / Q000150:complications / Q000000981:diagnostic imaging* / Q000601:surgery; D001018:Aortic Diseases / Q000150:complications / Q000000981:diagnostic imaging* / Q000601:surgery; D001027:Aortography; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007223:Infant