[Adult-onset Still's disease and hepatic angiosarcoma, a fortuitous association or a paraneoplastic syndrome: a case-report].
Adult-onset Still's disease is a systemic disorder without specific histological feature. Diagnosis requires to rule out any other disorder including neoplasia. Nevertheless, patients with paraneoplastic adult-onset Still's disease have been reported. We report a patient with an adult-onset Still's disease who presented with a liver involvement at onset. Two years later, a liver angiosarcoma was diagnosed. This report underlines the difficulty of the diagnosis of the adult-onset Still's disease even in the presence of Yamaguchi et al.'s [J Rheumatol 19 (1992) 424-30] and Fautrel et al.'s [Medicine 81 (2002) 194-200] classification criteria and may suggest a link between the initial clinical picture and the discovery nearly two years later, of a liver angiosarcoma.
Mekinian
A
A
Service de médecine interne, hôpital Huriez, CHRU de Lille, place de Verdun, rue Polonovski, 59037 Lille, France.
Lambert
M
M
Queyrel
V
V
Launay
D
D
Morell-Dubois
S
S
Hachulla
E
E
Mathurin
P
P
Hatron
P-Y
PY
D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D006394:Hemangiosarcoma / Q000473:pathology*; D006801:Humans; D008113:Liver Neoplasms / Q000473:pathology*; D008279:Magnetic Resonance Imaging; D010257:Paraneoplastic Syndromes / Q000145:classification / Q000473:pathology*; D016706:Still's Disease, Adult-Onset / Q000145:classification / Q000473:pathology*