[Absent pulmonary valve syndrome. Evaluation, surgical treatment and risk factors].
From 1991 to 2003 were studied 33 cases with absent pulmonary valve syndrome (AVPS): 66% were female, with a medium age of 1.5 years old and 11 kg of weight. Twenty seven cases (82%) were associated to Tetralogy of Fallot. Fourteen patients (5 younger than 1 year old) had corrective surgery. After the surgery, one patient required ballon pulmonary valvuloplasty for pulmonary stenosis; another one required surgery for changing the pulmonary prothesis one and five years after the first surgery. The rest of the patients did not present important problems. The five year survival was 95.4% in patients older than 6 months and 30.1% in younger patients (p = 0.000). As factors associated to mortality were the age younger than six months old (p = 0.003) and mechanical ventilation (p = 0.001) in our population. We suggest to delay the surgery in this group of patients because no survival were seen with or without the surgery. In older children with symptoms, the surgery also must be delayed in order to avoid more interventions for changing the pulmonary prothesis.
Chávez
Irma Miranda
IM
Departamento de Cardiologia Pediátrica. Institute Nacional de Cardiologia Ignacio Chavez (INCICH, Juan Badiano No. 1, Col Secci6n XVI, Tllalpan 14080 Mexico, DF. imirch@yahoo.com.mx
Solano
Javier Figueroa
JF
Quispe
Jorge Alberto Morales
JA
de Micheli
Alfredo
A
Hernández
Alfonso Buendía
AB
Marroquín
Samuel Ramírez
SR
D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D000013:Congenital Abnormalities / Q000175:diagnosis; D005260:Female; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000601:surgery*; D012307:Risk Factors