title: Dentinogenesis imperfecta: a case report.
abstract: Dentinogenesis imperfecta is an autosomal dominant disorder of tooth development characterized by the presence of opalescent dentin, resulting in a dusky blue to brownish discoloration of the teeth. This condition is genetically and clinically heterogeneous; it may affect only the teeth or it may be associated with the osteogenesis imperfecta. Dentinogenesis imperfecta has been subdivided into three types: type I is associated with osteogenesis imperfecta; in type II there is no associated osteogenesis imperfecta; and when the condition is associated with the Brandywine triracial isolate and large pulp chambers it is classified as type III. This report describes a 16-year-old female patient who showed the characteristic dental features of dentinogenesis imperfecta type II. The etiology and prevalence of the disorder, and a comprehensive treatment plan, will be briefly reviewed.
authors.affiliation: Department of Pedodontics, The Oxford Dental College and Hospital, Bangalore, India.
authors.forename: P
authors.initials: P
authors.lastname: Subramaniam
authors.forename: S
authors.initials: S
authors.lastname: Mathew
authors.forename: S N
authors.initials: SN
authors.lastname: Sugnani
mesh_terms: D000293:Adolescent; D003442:Crowns; D003811:Dentinogenesis Imperfecta / Q000145:classification / Q000503:physiopathology / Q000628:therapy*; D005260:Female; D006801:Humans; D017060:Patient Satisfaction; D012390:Root Canal Therapy / Q000379:methods*; D016896:Treatment Outcome