Congenital cholesteatoma of occipital bone or intradiploic epidermoid cyst? One and the same disease.
OBJECTIVE
We report an extremely rare case of congenital cholesteatoma affecting the occipital bone.


METHODS
We present a case report, plus a review of the world literature on similar lesions.


RESULTS
This case report describes the presentation and treatment of a congenital cholesteatoma arising in an apparently unique location within the occipital bone, with no effect on middle-ear structure or function. The different imaging characteristics of this lesion are described and illustrated. The discussion centres on the differentiation of this lesion from intradiploic epidermoid cysts, more commonly described in the neurosurgical literature. The possible methods of pathogenesis are discussed, along with treatment suggestions.


CONCLUSIONS
Congenital cholesteatomas and intradiploic epidermoid cysts are indistinguishable both histologically and radiologically, and would appear to be the same disease.
Clark
M P A
MP
Department of ENT, John Radcliffe Hospital, Oxford, UK. mattanna99@hotmail.com
Pretorius
P M
PM
Beaumont
D
D
Milford
C A
CA
D001847:Bone Diseases / Q000151:congenital* / Q000000981:diagnostic imaging / Q000473:pathology; D002781:Cholesteatoma / Q000151:congenital* / Q000000981:diagnostic imaging / Q000473:pathology; D004814:Epidermal Cyst / Q000000981:diagnostic imaging / Q000473:pathology; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D009777:Occipital Bone / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed