Congenital unilateral facial palsy and internal auditory canal stenosis.
Congenital stenosis of the internal auditory canal is a rare clinical entity. The majority of patients exhibit sensorineural hearing loss, and preserve facial-nerve function. We present a patient who manifested congenital unilateral facial palsy and ipsilateral sensorineural hearing loss clinically. Neuroimaging demonstrated stenosis of the unilateral internal auditory canal and hypoplasia of the ipsilateral trigeminal, facial, and vestibulocochlear nerves, despite normal function of the trigeminal nerves. The functional prognosis of facial and vestibulocochlear nerves was poor, and cognitive development demonstrated borderline delay.
Lin
Kao-Min
KM
Department of Pediatric Neurology, Chiayi Christian Hospital, Chiayi, Taiwan. horuslin@yahoo.com.tw
Huang
Chao-Ching
CC
Leung
Joseph Hang
JH
D002675:Child, Preschool; D003251:Constriction, Pathologic / Q000150:complications*; D004424:Ear Canal / Q000473:pathology*; D005158:Facial Paralysis / Q000150:complications* / Q000473:pathology; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000150:complications* / Q000473:pathology; D006801:Humans; D021621:Imaging, Three-Dimensional / Q000379:methods; D008279:Magnetic Resonance Imaging / Q000379:methods