Massive hematuria due to portal hypertension in a child with bladder augmentation for vesical exstrophy.
We report a case of a 17-year-old patient with severe hematuria from an ileocystoplasty-augmented bladder for vesical exstrophy, with associated cirrhosis secondary to autoimmune hepatitis, diagnosed years later. Varix development and further bleeding from ectopic varices, related to cirrhosis and portal hypertension, are a rare cause of hematuria in patients with surgically augmented bladder volume. This child was successfully treated with a transjugular intrahepatic portosystemic shunt procedure as a bridge to hepatic transplantation.
Lipsich
José
J
Department of Interventional Radiology, Hospital de Pediatría Prof JP Garrahan, Combate de los Pozos 1881 (1245), Buenos Aires, Argentina.
Rojas
Luis
L
Alonso
José
J
Teplisky
Darío
D
Halac
Alicia
A
Alvarez
Fernando
F
Sierre
Sergio
S
D000293:Adolescent; D001746:Bladder Exstrophy / Q000601:surgery*; D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006417:Hematuria / Q000175:diagnosis / Q000209:etiology*; D006801:Humans; D006975:Hypertension, Portal / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D008297:Male; D010690:Phlebography; D019168:Portasystemic Shunt, Transjugular Intrahepatic / Q000379:methods; D018615:Ultrasonography, Doppler, Color; D014547:Urinary Diversion / Q000009:adverse effects*