Supracardiac type total anomalous pulmonary venous connection (TAPVC) with oesophageal varices.
Oesophageal varices due to total anomalous pulmonary venous connection (TAPVC) is very rare. Additionally, the infradiaphragmatic type is the most common type of oesophageal varices due to TAPVC. Paraoesophageal varices due to stenosis of the vertical vein of supracardiac TAPVC has not previously been reported. We describe paraoesophageal varices developed as a result of a connection between the left lower pulmonary vein and the umbilicovitelline venous system because of stenosis of the proximal vertical vein in supracardiac type TAPVC in a 3-day-old female newborn who presented with general cyanosis, tachypnoea and dyspnoea.
Park
Ji Ae
JA
Department of Paediatrics, Medical Research Institute, Pusan National University Hospital, Pusan National University School of Medicine, Busan, Republic of Korea.
Lee
Hyoung Doo
HD
Ban
Ji Eun
JE
Jo
Min Jung
MJ
Sung
Si Chan
SC
Chang
Yun Hee
YH
Choo
Ki Seok
KS
D003287:Contrast Media; D017023:Coronary Angiography; D004932:Esophageal and Gastric Varices / Q000151:congenital* / Q000000981:diagnostic imaging* / Q000601:surgery; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging* / Q000601:surgery; D014057:Tomography, X-Ray Computed
D003287:Contrast Media