A favorable outcome following 32 vesicocentesis and amnioinfusion procedures in a fetus with severe prune belly syndrome.
Patients with severe prune belly syndrome rarely survive beyond the first days of life. We present a case of prune belly syndrome that initially presented with severe oligohydramnios, megacystis and associated poor urine biochemistries. Due to an anteriorly located placenta the patient was referred to three major centers, but was turned down because of the unfavorable prognostic findings. Therefore, fetal intervention was performed with 32 vesicocentesis and amnioinfusion procedures. Despite the unfavorable prenatal findings, and having undergone numerous fetal interventions, the birth resulted in a viable infant.
Galati
Vincenzo
V
Department of Urology, University of Oklahoma Health Sciences Center, 920 Stanton L. Young Boulevard, WP 3150, Oklahoma City, OK 73104, USA.
Beeson
James H
JH
Confer
Stephen D
SD
Frimberger
Dominic
D
Campbell
Jeffrey B
JB
Ramji
Faridali G
FG
Kropp
Bradley P
BP
D000328:Adult; D005260:Female; D005440:Fluid Therapy / Q000379:methods; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D016104:Oligohydramnios / Q000000981:diagnostic imaging / Q000601:surgery / Q000628:therapy; D011247:Pregnancy; D011379:Prognosis; D011535:Prune Belly Syndrome / Q000000981:diagnostic imaging / Q000601:surgery* / Q000628:therapy*; D012720:Severity of Illness Index; D014463:Ultrasonography; D001743:Urinary Bladder / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery