An unusual presentation of uterus didelphys with obstructed hemivagina with ipsilateral renal agenesis.
OBJECTIVE
To report a rare müllerian anomaly of uterus didelphys with obstructed hemivagina and renal agenesis, and its unusual presentation that mimicked an ischiorectal swelling.


METHODS
Case report.


METHODS
Private clinic and surgical center.


METHODS
A 17-year-old woman referred for evaluation of a suspected müllerian anomaly.


METHODS
Clinical, hysteroscopic, and laparoscopic evaluation of the anomaly, with treatment and follow-up assessments.


METHODS
Assessment of the anomaly according to the standard müllerian classification system with a subsequent literature search.


RESULTS
Successful drainage of hematocolpos and hematometra, and subsequent normal menstruation.


CONCLUSIONS
This rare müllerian anomaly, also known as Herlyn-Werner-Wunderlich syndrome (HWWS), presented as a huge paravaginal mass. Good long-term outcome occurred after vaginal septectomy. This diagnosis should be suspected in women who have a pelvic mass and ipsilateral renal agenesis.
Asha
Baxi
B
Disha Fertility and Surgical Center, Indore, Madhya Pradesh, India.
Manila
Kaushal
K
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D000293:Adolescent; D003937:Diagnosis, Differential; D004487:Edema / Q000175:diagnosis*; D005260:Female; D006801:Humans; D007668:Kidney / Q000002:abnormalities*; D012002:Rectal Diseases / Q000175:diagnosis*; D014599:Uterus / Q000002:abnormalities*; D014621:Vagina / Q000002:abnormalities*