Ventricular septal defect closure in a patient with VACTERL syndrome: anticipating sequelae in a rare genetic disorder.
Noncardiac components of genetic disorders can complicate the operative and postoperative courses of pediatric cardiac surgery patients. Prolonged hospital stay, increased treatment cost, morbidity, and death are more likely in this subgroup of patients. Ventricular septal defect, which is a component of various genetic disorders, has a 22.3% incidence in VACTERL syndrome--a rare, nonrandom pattern of birth defects. Herein, we discuss the impact of ventricular septal defect closure in a 4-month-old girl who was diagnosed after birth with VACTERL syndrome.
Hatemi
Ali Can
AC
Department of Cardiovascular Surgery, Institute of Cardiology, Istanbul University, Haseki, Istanbul 34304, Turkey. hatemi@superonline.com
Gursoy
Mete
M
Ceviker
Kadir
K
Tongut
Aybala
A
Cetin
Gurkan
G
Celebi
Serdar
S
Kansiz
Erhan
E
D000015:Abnormalities, Multiple; D004065:Digestive System Abnormalities; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D006801:Humans; D007223:Infant; D009139:Musculoskeletal Abnormalities; D011183:Postoperative Complications; D013577:Syndrome