title: A case of split notochord syndrome with congenital ileal atresia, the total absence of a colon, and a dorsal enteric cyst communicating to the retroperitoneal isolated ceca with a vesical fistula.
abstract: Split notochord syndrome (SNS) is an extremely rare anomaly. This report presents the case of a male infant with SNS associated with congenital ileal atresia and a dorsal enteric cyst communicating to the retroperitoneal isolated ceca with a vesical fistula. Dorsal fistulography and vesicography were useful and essential for the detailed study of the topology in this patient. The embryological mechanism and etiologic theories are discussed with a review of 19 cases reported in the literature.
authors.affiliation: Department of Pediatric Surgery, School of Medicine, Kurume University, 67 Asahimachi, Kurume, Fukuoka 830-0011, Japan. asagiri@med.kurume-u.ac.jp
authors.forename: Kimio
authors.initials: K
authors.lastname: Asagiri
authors.forename: Minoru
authors.initials: M
authors.lastname: Yagi
authors.forename: Yoshiaki
authors.initials: Y
authors.lastname: Tanaka
authors.forename: Masao
authors.initials: M
authors.lastname: Akaiwa
authors.forename: Takahiro
authors.initials: T
authors.lastname: Asakawa
authors.forename: Akiko
authors.initials: A
authors.lastname: Kaida
authors.forename: Hidefumi
authors.initials: H
authors.lastname: Kobayashi
authors.forename: Hiroaki
authors.initials: H
authors.lastname: Tanaka
mesh_terms: D000015:Abnormalities, Multiple / Q000601:surgery; D002432:Cecum / Q000002:abnormalities* / Q000601:surgery; D003106:Colon / Q000002:abnormalities* / Q000601:surgery; D017809:Fatal Outcome; D006801:Humans; D007082:Ileum / Q000002:abnormalities* / Q000601:surgery; D007231:Infant, Newborn; D008297:Male; D009436:Neural Tube Defects / Q000150:complications* / Q000601:surgery; D009672:Notochord / Q000002:abnormalities* / Q000601:surgery; D012187:Retroperitoneal Space; D013577:Syndrome; D001747:Urinary Bladder Fistula / Q000150:complications* / Q000601:surgery