title: [Muscle-aponeurotic aggressive fibromatosis management. 10 years of experience].
abstract: BACKGROUND
  This work presents clinical evolution and functional outcome of patients with histologic diagnosis of Muscle-aponeurotic aggressive fibromatosis in 10 years of follow up in the National Rehabilitation Institute.
  
  
  METHODS
  We performed a descriptive, retrospective, cross sectioned clinical trial in the Bone Tumour Department. We reviewed the clinical and radiological files from 1996 to 2006.
  
  
  METHODS
  both genres, any age, clinical and histological diagnosis.
  
  
  METHODS
  incomplete file, lost to follow up, other diagnosis. Elimination criteria: Death during trial period. Analyzed variables. Age, genre, occupation, birth place, school degree, anatomic situation, signs and symptoms, time of follow up, treatment, relapses. We used statistical computed system Excel 2007, with central trend descriptive variables.
  
  
  RESULTS
  Eleven patients (mean age 24.36; SD 18.32, 1-61 years), 9 female (81.8%) 2 male; birth place: Mexico City 7 (63.63%), Puebla 1, Toluca 1, South Baja California 1 and Chiapas 1. Anatomic situation: Pelvis 6 (54.54%), thoracic and gluteus 3. Pain and presence of a mass 10 (90.9%), range of motion limitation 5, edema and erithema 1. Relapses 6 (55%).
  
  
  METHODS
  broad resection 3 patients, marginal resection 6 patients, radical resection 2 patients.
  
  
  CONCLUSIONS
  If clinical suspicion of Muscle-aponeurotic fibromatosis appears, one should start protocol work up: laboratory, radiographic assessment, nuclear medicine, biopsy and histologic and immune-histochemistry. One should perform broad resections aiming to preserve the most possible extremity tissue disease free.
authors.affiliation: Instituto Nacional de Rehabilitación, Servicio de Tumores Oseos, Delegación Tlalpan, México, DF. miranda_roa@hotmail.com
authors.forename: Josué Antonio Miranda
authors.initials: JA
authors.lastname: Roa
authors.forename: Genaro Rico
authors.initials: GR
authors.lastname: Martínez
authors.forename: Luis Miguel Linares
authors.initials: LM
authors.lastname: González
authors.forename: Ernesto A Delgado
authors.initials: EA
authors.lastname: Cedillo
authors.forename: Nelly Flores
authors.initials: NF
authors.lastname: Pineda
mesh_terms: D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D003430:Cross-Sectional Studies; D005260:Female; D018222:Desmoid Tumors / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D008875:Middle Aged; D019042:Muscle Neoplasms / Q000175:diagnosis / Q000601:surgery; D012189:Retrospective Studies; D013997:Time Factors