Orthodontic treatment of a patient with recessive dystrophic epidermolysis bullosa: a case report.
Epidermolysis bullosa (EB) represents a heterogeneous group of hereditary, chronic, non-inflammatory skin pathologies. Recessive dystrophic epidermolysis bullosa (RDEB) is characterized by sub-lamina dura separation, due to blistering below the lamina densa of the basement membrane zone, and is associated with the absence of Type VII collagen fibers. The mouth, pharyngeal, and esophageal mucosa are compromised by scarring and tissue contraction. The purpose of this article was to present a case report on an orthodontic patient with RDEB.
Pacheco
Wellington
W
Pontific Catholic University of Minas Gerais, Belo Horizonte, Brazil. wllpacheco@gmail.com
Marques de Sousa Araugio
Rafael
R
D000328:Adult; D017742:Dental Care for Chronically Ill; D003830:Denture, Partial, Fixed; D016108:Epidermolysis Bullosa Dystrophica / Q000150:complications; D005260:Female; D006801:Humans; D008310:Malocclusion / Q000209:etiology / Q000628:therapy*; D009971:Orthodontics, Corrective / Q000379:methods*; D011502:Protein-Energy Malnutrition / Q000209:etiology; D014081:Tooth Extraction; D014313:Trismus / Q000150:complications / Q000209:etiology