[Muscle-aponeurotic aggressive fibromatosis management. 10 years of experience].
BACKGROUND
This work presents clinical evolution and functional outcome of patients with histologic diagnosis of Muscle-aponeurotic aggressive fibromatosis in 10 years of follow up in the National Rehabilitation Institute.


METHODS
We performed a descriptive, retrospective, cross sectioned clinical trial in the Bone Tumour Department. We reviewed the clinical and radiological files from 1996 to 2006.


METHODS
both genres, any age, clinical and histological diagnosis.


METHODS
incomplete file, lost to follow up, other diagnosis. Elimination criteria: Death during trial period. Analyzed variables. Age, genre, occupation, birth place, school degree, anatomic situation, signs and symptoms, time of follow up, treatment, relapses. We used statistical computed system Excel 2007, with central trend descriptive variables.


RESULTS
Eleven patients (mean age 24.36; SD 18.32, 1-61 years), 9 female (81.8%) 2 male; birth place: Mexico City 7 (63.63%), Puebla 1, Toluca 1, South Baja California 1 and Chiapas 1. Anatomic situation: Pelvis 6 (54.54%), thoracic and gluteus 3. Pain and presence of a mass 10 (90.9%), range of motion limitation 5, edema and erithema 1. Relapses 6 (55%).


METHODS
broad resection 3 patients, marginal resection 6 patients, radical resection 2 patients.


CONCLUSIONS
If clinical suspicion of Muscle-aponeurotic fibromatosis appears, one should start protocol work up: laboratory, radiographic assessment, nuclear medicine, biopsy and histologic and immune-histochemistry. One should perform broad resections aiming to preserve the most possible extremity tissue disease free.
Roa
Josué Antonio Miranda
JA
Instituto Nacional de Rehabilitación, Servicio de Tumores Oseos, Delegación Tlalpan, México, DF. miranda_roa@hotmail.com
Martínez
Genaro Rico
GR
González
Luis Miguel Linares
LM
Cedillo
Ernesto A Delgado
EA
Pineda
Nelly Flores
NF
D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D003430:Cross-Sectional Studies; D005260:Female; D018222:Desmoid Tumors / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D008875:Middle Aged; D019042:Muscle Neoplasms / Q000175:diagnosis / Q000601:surgery; D012189:Retrospective Studies; D013997:Time Factors