Sudden death in Steinert's disease.
Steinert's disease is an autosomal dominant neuromuscular disorder. Heart involvement is characterized by conduction system abnormalities, supraventricular and ventricular arrhythmias. Patients with Steinert's disease are reported to have a higher incidence of sudden death. Preventing sudden death is crucial in this disease. It relies on non-invasive and/or invasive approach for risk stratification.
Fayssoil
A
A
Nardi
O
O
D001145:Arrhythmias, Cardiac / Q000401:mortality*; D016757:Death, Sudden, Cardiac / Q000453:epidemiology*; D006801:Humans; D015994:Incidence; D009223:Myotonic Dystrophy / Q000401:mortality*