title: Unsuccessful cochlear implantation in two patients with superficial siderosis of the central nervous system.
abstract: OBJECTIVE
  To highlight the potential adverse outcomes with cochlear implantation (CI) in patients with superficial siderosis.
  
  
  METHODS
  Two patients with superficial siderosis of the central nervous system with secondary sensorineural hearing loss.
  
  
  METHODS
  Cochlear implantation.
  
  
  METHODS
  Postimplantation speech discrimination scores.
  
  
  RESULTS
  In both cases, initial results after implantation were promising. However, in 1 case, their ability to use the CI rapidly declined after 1 week because of major difficulties adapting to electrical stimulation. For the other case, hearing rapidly declined over a 6-month period.
  
  
  CONCLUSIONS
  The 2 patients reported did not benefit from CI in superficial siderosis that is in contrast to several previously published cases. Adequate counseling of patients with superficial siderosis is important when considering cochlear implantation as results are variable.
authors.affiliation: Department of Otolaryngology, Christchurch Hospital, Christchurch, New Zealand. verity.wood@gmail.com
authors.forename: Verity H
authors.initials: VH
authors.lastname: Wood
authors.forename: Philip A
authors.initials: PA
authors.lastname: Bird
authors.forename: Ellen C
authors.initials: EC
authors.lastname: Giles
authors.forename: William J
authors.initials: WJ
authors.lastname: Baber
mesh_terms: D001301:Audiometry, Pure-Tone; D002490:Central Nervous System / Q000473:pathology*; D019929:Cochlear Implantation; D018450:Disease Progression; D006310:Hearing Aids; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000601:surgery* / Q000628:therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D011183:Postoperative Complications; D012806:Siderosis / Q000473:pathology*; D013063:Speech Discrimination Tests; D013067:Speech Perception / Q000502:physiology