Bronchial anomalies in VACTERL association.
VACTERL association is an acronym made of associated defects including vertebral anomalies, anal atresia, cardiac, tracheal-esophageal fistula, and renal/radial limb anomalies. Tracheal bronchus is a condition characterized by ectopic location of the right upper lobe bronchus at the mid to distal trachea. This condition is associated with congenital anomalies and has been reported in one previous case of VACTERL. We report another infant with VACTERL presenting with respiratory complications due to presence of tracheal bronchus. She also had a narrowed segment of her right main stem bronchus.
Kanu
Adaobi
A
Department of Pediatrics, Texas Tech University, HSC, Lubbock, Texas, USA. adaobi.kanu@ttuhsc.edu
Tegay
David
D
Scriven
Richard
R
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D001003:Anal Canal / Q000002:abnormalities*; D001980:Bronchi / Q000002:abnormalities*; D002828:Choristoma / Q000175:diagnosis*; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis*; D006801:Humans; D007231:Infant, Newborn; D007668:Kidney / Q000002:abnormalities*; D011884:Radius / Q000002:abnormalities*; D013131:Spine / Q000002:abnormalities*; D013577:Syndrome; D014133:Tracheal Diseases / Q000175:diagnosis*; D014138:Tracheoesophageal Fistula / Q000175:diagnosis*