Unsuccessful cochlear implantation in two patients with superficial siderosis of the central nervous system.
OBJECTIVE
To highlight the potential adverse outcomes with cochlear implantation (CI) in patients with superficial siderosis.


METHODS
Two patients with superficial siderosis of the central nervous system with secondary sensorineural hearing loss.


METHODS
Cochlear implantation.


METHODS
Postimplantation speech discrimination scores.


RESULTS
In both cases, initial results after implantation were promising. However, in 1 case, their ability to use the CI rapidly declined after 1 week because of major difficulties adapting to electrical stimulation. For the other case, hearing rapidly declined over a 6-month period.


CONCLUSIONS
The 2 patients reported did not benefit from CI in superficial siderosis that is in contrast to several previously published cases. Adequate counseling of patients with superficial siderosis is important when considering cochlear implantation as results are variable.
Wood
Verity H
VH
Department of Otolaryngology, Christchurch Hospital, Christchurch, New Zealand. verity.wood@gmail.com
Bird
Philip A
PA
Giles
Ellen C
EC
Baber
William J
WJ
D001301:Audiometry, Pure-Tone; D002490:Central Nervous System / Q000473:pathology*; D019929:Cochlear Implantation; D018450:Disease Progression; D006310:Hearing Aids; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000601:surgery* / Q000628:therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D011183:Postoperative Complications; D012806:Siderosis / Q000473:pathology*; D013063:Speech Discrimination Tests; D013067:Speech Perception / Q000502:physiology