title: Sudden death in Steinert's disease.
abstract: Steinert's disease is an autosomal dominant neuromuscular disorder. Heart involvement is characterized by conduction system abnormalities, supraventricular and ventricular arrhythmias. Patients with Steinert's disease are reported to have a higher incidence of sudden death. Preventing sudden death is crucial in this disease. It relies on non-invasive and/or invasive approach for risk stratification.
authors.forename: A
authors.initials: A
authors.lastname: Fayssoil
authors.forename: O
authors.initials: O
authors.lastname: Nardi
mesh_terms: D001145:Arrhythmias, Cardiac / Q000401:mortality*; D016757:Death, Sudden, Cardiac / Q000453:epidemiology*; D006801:Humans; D015994:Incidence; D009223:Myotonic Dystrophy / Q000401:mortality*