Intrathoracic and pelvic extramedullary haematopoiesis in sickle cell disease: a case report.
Intrathoracic extramedullary haematopoiesis is a rare entity encountered in patients with long standing anaemias such as thalassaemia and congenital spherocytosis. It is rare in patients with homozygous sickle cell disease; only 11 cases of intrathoracic and two cases of pelvic extramedullary haematopoiesis have been documented in the literature. We report the case of a 30-year old man with homozygous sickle cell disease with intrathoracic and pelvic extramedullary haematopoiesis, the first case to be documented from the Caribbean.
Asnani
M
M
Sickle Cell Unit, Tropical Medicine Research Institute, The University of the West Indies, Kingston 7, Jamaica, West Indies. monika.parshadasnani@uwimona.edu.jm
Char
G
G
Reid
M
M
Nanton
P Miller
PM
D000328:Adult; D000755:Anemia, Sickle Cell / Q000503:physiopathology*; D001853:Bone Marrow / Q000502:physiology*; D017809:Fatal Outcome; D006411:Hematopoiesis, Extramedullary / Q000502:physiology*; D006801:Humans; D008297:Male; D010384:Pelvic Bones; D013904:Thoracic Vertebrae