title: Interrupted aortic arch with cardiac heart failure in young adult.
abstract: The interrupted aortic arch (IAA) is a rare cardiopathy, with high morbimortality when treatment is delayed. This study is a case of IAA with atypical clinical behavior in a 19-year-old patient. The history and the clinical assessment were compatible with recent heart failure, associated to syncope episodes and reduction of pulses in the lower limbs. The electrocardiogram showed biventricular and biatrial overload. The echocardiogram showed severe ventricular dysfunction and altered blood flow in the descending aorta. The angiotomography disclosed occlusion of the thoracic aorta after the left subclavian artery. The attained diagnosis was interrupted aortic arch and surgical treatment was indicated.
authors.affiliation: Hospital do Coração, Associação do Sanatório Sírio, Instituto do Coração, INCOR, São Paulo, SP, Brazil. lobato01@ig.com.br
authors.forename: Rogério Fortes
authors.initials: RF
authors.lastname: Lobato
authors.forename: Luis Augusto R
authors.initials: LA
authors.lastname: Saliba
authors.forename: Carlos Regenga
authors.initials: CR
authors.lastname: Ferreiro
authors.forename: Fernando
authors.initials: F
authors.lastname: Bacal
mesh_terms: D001013:Aorta, Thoracic / Q000002:abnormalities*; D003937:Diagnosis, Differential; D004452:Echocardiography; D006333:Heart Failure / Q000175:diagnosis* / Q000209:etiology; D006345:Heart Septal Defects, Ventricular / Q000150:complications / Q000175:diagnosis*; D006801:Humans; D008297:Male; D013348:Subclavian Artery / Q000002:abnormalities; D055815:Young Adult