Pulmonary atresia with intact atrial and ventricular septums, unroofed coronary sinus, and absent aortocoronary arterial connections.
A stillborn fetus with pulmonary valvar atresia and intact atrial and ventricular septums also had absence of coronary arterial connections from the aorta and an unroofed coronary sinus. A left superior caval vein drained to the dilated coronary sinus. The left coronary artery was anomalously connected to the proximal branch of the right pulmonary artery, and a fistula from the right ventricle supplied the right coronary artery.
Erickson
Lance K
LK
Department of Pathology, Primary Children's Medical Center, Salt Lake City, Utah 84113, United States of America. lance.erickson@imail.org
Puchalski
Michael D
MD
Pysher
Theodore J
TJ
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D054326:Coronary Sinus / Q000002:abnormalities*; D003330:Coronary Vessel Anomalies / Q000175:diagnosis*; D003937:Diagnosis, Differential; D004452:Echocardiography; D017809:Fatal Outcome; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D018633:Pulmonary Atresia / Q000175:diagnosis*