Malignant peripheral nerve sheath tumour in the ischio-rectal fossa.
Primary sarcomas in the ischiorectal fossa are occasionally reported and represent a significant challenge due to the proximity of rectum, levator muscles and pudendal neurovascular structures. We report a case in which the diagnosis changed between biopsy (desmoid tumour) and resection (malignant peripheral nerve sheath tumour), requiring a multidisciplinary surgical approach involving different sub-specialties. It also illustrates the importance of undertaking sarcoma surgery in a recognized sarcoma centre with sarcoma expertise available across a range of disciplines.
Teoh
K H
KH
Department of Orthopaedic Surgery, University of Edinburgh, Edinburgh. karhao@gmail.com
Reddy
S
S
Beggs
I
I
Al-Nafussi
A
A
Mander
B J
BJ
Porter
D E
DE
D000368:Aged; D002081:Buttocks / Q000473:pathology; D003937:Diagnosis, Differential; D018222:Desmoid Tumors / Q000473:pathology; D006801:Humans; D007512:Ischium; D008279:Magnetic Resonance Imaging; D008297:Male; D018317:Nerve Sheath Neoplasms / Q000473:pathology / Q000601:surgery*; D010348:Patient Care Team / Q000458:organization & administration; D010524:Peripheral Nervous System Neoplasms / Q000473:pathology / Q000601:surgery*; D012007:Rectum