title: Primary Adenoid Cystic Carcinoma Presenting as an Orbital Apex Tumor.
abstract: Primary adenoid cystic carcinoma occurring in the orbital apex is rare. We present the clinical features of a patient who initially presented with the clinical and radiologic features of an orbital pseudotumor. He developed features of orbital apex syndrome and repeat imaging showed a tumor of the orbital apex with intracranial invasion. He underwent radical skull base surgery and pathologic examination revealed adenoid cystic carcinoma in the orbital apex with a normal lacrimal apparatus. He received post operative radiation and the outcome in the light of a review of available literature is being discussed.
authors.affiliation: Department of Clinical Oncology, Royal Marsden Hospital, Sutton, Surrey.
authors.forename: Ramachandran
authors.initials: R
authors.lastname: Venkitaraman
authors.forename: Jayaprakash
authors.initials: J
authors.lastname: Madhavan
authors.forename: Krishnankuttynair
authors.initials: K
authors.lastname: Ramachandran
authors.forename: Elizabeth
authors.initials: E
authors.lastname: Abraham
authors.forename: Balakrishnan
authors.initials: B
authors.lastname: Rajan