The Binder syndrome: review of the literature and case report.
Binder syndrome or maxillo-nasal dysplasia (nasomaxillary hypoplasia) is an uncommon developmental anomaly affecting primarily the anterior part of the maxilla and nasal complex. A 4-year-old boy with maxillo-nasal dysplasia (Binder's syndrome), featuring maxillary hypoplasia and relative mandibular prognathism, combined with acute leucosis was presented. We review the literature and describe how three-dimensional CT scanning was used to evaluate the facial morphology. The principal features, diagnosis and management of the syndrome are discussed.
Nedev
Plamen Kostov
PK
Department of Neurosurgery, Otorhinolaryngology and Ophthalmology - Medical University Varna, Clinic of Otorhinolaringology - University Hospital "Saint Marina" - Varna 23 E. Georgiev str. B-10, Varna 9010, Bulgaria. drnedev@abv.bg
D001848:Bone Diseases, Developmental / Q000150:complications / Q000000981:diagnostic imaging*; D002675:Child, Preschool; D006801:Humans; D021621:Imaging, Three-Dimensional; D007964:Leukocytosis / Q000150:complications; D008297:Male; D008437:Maxilla / Q000000981:diagnostic imaging*; D019767:Maxillofacial Abnormalities / Q000150:complications / Q000000981:diagnostic imaging*; D009295:Nasal Bone / Q000000981:diagnostic imaging*; D011378:Prognathism / Q000150:complications / Q000000981:diagnostic imaging*; D013577:Syndrome; D014057:Tomography, X-Ray Computed / Q000379:methods