title: Supernumerary nipples in association with Hailey-Hailey disease in a Tunisian family.
abstract: Supernumerary nipples (SNs) or polythelia are developmental abnormalities of breast tissue. They are located along the embryonic mammary lines. Polythelia usually occurs as a sporadic abnormality, although familial aggregation has been occasionally reported. Hailey-Hailey disease is a rare autosomal genodermatosis characterized by disturbed keratinocyte adhesion. These cutaneous disorders have been described in correlation with many other abnormalities. We report here the association of Hailey-Hailey disease and supernumerary nipples in a Northern Tunisian family. To our knowledge, this is the first report of such a clinical association.
authors: Dermatology Department, Habib Thameur Hospital, Tunis, Tunisia. rym.benmously@rns.tn
authors: R
authors: R
authors: Benmously-Mlika
authors: S
authors: S
authors: Deghais
authors: M
authors: M
authors: Bchetnia
authors: C
authors: C
authors: Charfeddine
authors: M
authors: M
authors: Mokni
authors: S
authors: S
authors: Kassar
authors: S
authors: S
authors: Haouet
authors: S
authors: S
authors: Boubaker
authors: I
authors: I
authors: Mokhtar
authors: S
authors: S
authors: Abdelhak
authors: A Ben Osman
authors: AB
authors: Dhahri
mesh_terms: D000328:Adult; D001940:Breast; D005260:Female; D005799:Genes, Dominant; D006801:Humans; D008875:Middle Aged; D009558:Nipples / Q000002:abnormalities*; D010375:Pedigree; D016506:Pemphigus, Benign Familial / Q000150:complications* / Q000235:genetics / Q000473:pathology; D012867:Skin / Q000473:pathology