Supernumerary nipples in association with Hailey-Hailey disease in a Tunisian family.
Supernumerary nipples (SNs) or polythelia are developmental abnormalities of breast tissue. They are located along the embryonic mammary lines. Polythelia usually occurs as a sporadic abnormality, although familial aggregation has been occasionally reported. Hailey-Hailey disease is a rare autosomal genodermatosis characterized by disturbed keratinocyte adhesion. These cutaneous disorders have been described in correlation with many other abnormalities. We report here the association of Hailey-Hailey disease and supernumerary nipples in a Northern Tunisian family. To our knowledge, this is the first report of such a clinical association.
Benmously-Mlika
R
R
Dermatology Department, Habib Thameur Hospital, Tunis, Tunisia. rym.benmously@rns.tn
Deghais
S
S
Bchetnia
M
M
Charfeddine
C
C
Mokni
M
M
Kassar
S
S
Haouet
S
S
Boubaker
S
S
Mokhtar
I
I
Abdelhak
S
S
Dhahri
A Ben Osman
AB
D000328:Adult; D001940:Breast; D005260:Female; D005799:Genes, Dominant; D006801:Humans; D008875:Middle Aged; D009558:Nipples / Q000002:abnormalities*; D010375:Pedigree; D016506:Pemphigus, Benign Familial / Q000150:complications* / Q000235:genetics / Q000473:pathology; D012867:Skin / Q000473:pathology