Uterus didelphys with an obstructed unilateral vagina by a transverse vaginal septum associated with ipsilateral renal agenesis, duplication of inferior vena cava, high-riding aortic bifurcation, and intestinal malrotation: a case report.
OBJECTIVE
To present a case of müllerian defects associated with other anomalies, including ipsilateral renal agenesia, duplication of inferior vena cava, high-riding aortic bifurcation, and intestinal malrotation.


METHODS
Case study.


METHODS
Academic medical center.


METHODS
A 16-year-old woman with müllerian defects associated with vascular and intestinal anomalies.


METHODS
Excision of vaginal septum.


METHODS
Improvement of symptoms caused by obstructed müllerian defect.


RESULTS
After an incision on the vaginal septum, a large amount of chocolate-colored fluid was drained, and the dimensions of the right uterus were diminished. Then the vaginal septum was excised completely; we saw a second distinct cervical portion.


CONCLUSIONS
Uterus didelphys with obstructed hemivagina is almost always associated with renal agenesis ipsilateral to the obstruction. Inferior vena cava duplication associated with müllerian anomalies is an extremely rare condition. In addition, the presented case also had a high-riding aortic bifurcation and intestinal malrotation. To the best of our knowledge, this is the first case to include all of these anomalies.
Coskun
Ayhan
A
Department of Obstetrics and Gynecology, School of Medicine, Sutcu Imam University, Kahramanmaras, Turkey. acoskun@ksu.edu.tr
Okur
Nazan
N
Ozdemir
Ozgur
O
Kiran
Gurkan
G
Arýkan
Deniz Cemgil
DC
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging / Q000601:surgery; D000293:Adolescent; D001011:Aorta / Q000002:abnormalities* / Q000473:pathology; D005260:Female; D006801:Humans; D007422:Intestines / Q000002:abnormalities* / Q000000981:diagnostic imaging; D007668:Kidney / Q000002:abnormalities* / Q000000981:diagnostic imaging; D010535:Laparoscopy; D009095:Mullerian Ducts / Q000002:abnormalities*; D014057:Tomography, X-Ray Computed; D014599:Uterus / Q000002:abnormalities* / Q000473:pathology; D014621:Vagina / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000000981:diagnostic imaging