title: Atypical Ormond's disease associated with bile duct stricture mimicking cholangiocarcinoma.
abstract: A 55-year-old woman with suspected hilar cholangiocarcinoma presented with jaundice and dilated intrahepatic bile ducts owing to high-grade hepatic duct confluence stenosis. The suspected tumour and the entire extrahepatic bile duct system were resected and Roux-en-Y hepaticojejunostomy was performed. Histological investigations showed perihepatic fibrosis but no signs of malignancy. One year later the patient developed bilateral hydronephrosis caused by ureteral obstruction. Since the patient had a gynaecological history of widespread inflammation, she was referred for transabdominal operative ureterolysis combined with hysterectomy and adnexectomy. Histological investigations as well as fluorodeoxyglucose-positron emission tomography (FDG-PET) and computed tomography (CT) findings were compatible with retroperitoneal fibrosis (Ormond's disease). Treatment with tamoxifen was initiated. To the best of our knowledge, only a few cases of intraperitoneal fibroses mimicking cholangiocarcinoma followed by the typical symptoms of retroperitoneal Ormond's disease have been reported.
authors.affiliation: Department of Medicine I, University Hospital Bonn, Germany. Michael.quante@ukb.uni-bonn.de
authors.forename: Michael
authors.initials: M
authors.lastname: Quante
authors.forename: Beate
authors.initials: B
authors.lastname: Appenrodt
authors.forename: Simone
authors.initials: S
authors.lastname: Randerath
authors.forename: Martin
authors.initials: M
authors.lastname: Wolff
authors.forename: Hans-Peter
authors.initials: HP
authors.lastname: Fischer
authors.forename: Tilman
authors.initials: T
authors.lastname: Sauerbruch