Atrial and ventricular lead insulation defects with resulting inappropriate shocks and end-of-life of the ICD pulse generator in a young bodybuilder with congenital long-QT-syndrome.
We report on a 19-year-old male with a congenital Long-QT syndrome who was admitted to our hospital because of insulation defects of both atrial and ventricular ICD leads resulting in inappropriate delivered shocks and a non-responding pulse generator during telemetrical evaluation. The insulation defects led to multiple arc marks within the ICD pocket and there was a short circuit between denuded leads and the electrically active pulse generator. The high current flow generated sufficient heat to damage several circuits of the generator. A new ICD system was implanted successfully and the postoperative course has been remained uneventful for almost 6 years.
Diez
Claudius
C
Department of Cardiothoracic Surgery, Martin-Luther-Universität Halle-Wittenberg, Ernst-Grube-Strasse 40, 06097, Halle/Saale, Germany. claudius.diez@t-online.de
Hofmann
Hans-Stefan
HS
Börgermann
Jochen
J
D017147:Defibrillators, Implantable / Q000009:adverse effects*; D004868:Equipment Failure; D006801:Humans; D008133:Long QT Syndrome / Q000601:surgery*; D008297:Male; D012086:Reoperation; D013686:Telemetry; D014891:Weight Lifting; D055815:Young Adult
Europace. 2002 Jan;4(1):19-24
11858151
Circulation. 2007 May 15;115(19):2474-80
17470696
Pacing Clin Electrophysiol. 2003 Feb;26(2 Pt 1):649-57
12710331
Cardiol Clin. 2007 Aug;25(3):467-82, vii
17961801
Circ J. 2006 Mar;70(3):273-7
16501292
J Am Coll Cardiol. 2003 Jan 1;41(1):73-80
12570948