title: Atrial and ventricular lead insulation defects with resulting inappropriate shocks and end-of-life of the ICD pulse generator in a young bodybuilder with congenital long-QT-syndrome.
abstract: We report on a 19-year-old male with a congenital Long-QT syndrome who was admitted to our hospital because of insulation defects of both atrial and ventricular ICD leads resulting in inappropriate delivered shocks and a non-responding pulse generator during telemetrical evaluation. The insulation defects led to multiple arc marks within the ICD pocket and there was a short circuit between denuded leads and the electrically active pulse generator. The high current flow generated sufficient heat to damage several circuits of the generator. A new ICD system was implanted successfully and the postoperative course has been remained uneventful for almost 6 years.
authors.affiliation: Department of Cardiothoracic Surgery, Martin-Luther-Universität Halle-Wittenberg, Ernst-Grube-Strasse 40, 06097, Halle/Saale, Germany. claudius.diez@t-online.de
authors.forename: Claudius
authors.initials: C
authors.lastname: Diez
authors.forename: Hans-Stefan
authors.initials: HS
authors.lastname: Hofmann
authors.forename: Jochen
authors.initials: J
authors.lastname: Börgermann
mesh_terms: D017147:Defibrillators, Implantable / Q000009:adverse effects*; D004868:Equipment Failure; D006801:Humans; D008133:Long QT Syndrome / Q000601:surgery*; D008297:Male; D012086:Reoperation; D013686:Telemetry; D014891:Weight Lifting; D055815:Young Adult
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