Primary intracranial low-grade fibromyxoid sarcoma (Evans tumor).
Low-grade fibromyxoid sarcoma was first described in 1987 as a rare soft tissue neoplasm characterized by a bland and deceptively benign histological appearance but with aggressive behavior. A 20-year-old male patient presented with a recent history of headache and seizure. A right frontal mass was detected on MRI and he was operated upon to remove the intracranial mass. Histological examination revealed mildly atypical fibroblastic cells embedded within a myxoid matrix. Nuclear atypia and pleomorphism were minimal, and necrosis was not present. The lesion was diagnosed as a low-grade fibromyxoid sarcoma. Although primary intracranial low-grade fibromyxoid sarcoma has characteristic histological features, clinical and radiological correlation is necessary to make the correct diagnosis.
Tun
Kagan
K
Department of Neurosurgery, Ankara Numune Education and Research Hospital, Ankara, Turkey. kagantun@yahoo.com
Ozen
Ozlem
O
Kaptanoglu
Erkan
E
Gurcan
Oktay
O
Beskonakli
Ethem
E
Celasun
Bulent
B
D005354:Fibrosarcoma / Q000473:pathology* / Q000628:therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D012983:Soft Tissue Neoplasms / Q000473:pathology* / Q000628:therapy; D055815:Young Adult