title: Association of idiopathic retroperitoneal fibrosis, rapidly progressive glomerulonephritis and antiproteinase 3 antineutrophil cytoplasmic antibodies (anti PR3-ANCA).
abstract: We report a case of idiopathic retroperitoneal fibrosis and rapidly progressive glomerulonephritis with serum antiproteinase 3 antineutrophil cytoplasmic antibodies (anti-PR3-ANCA), without clinical or histological signs of Wegener's granulomatosis, in a 46-year-old man. Our case and previously reported cases showing the same association support the hypothesis that the association is not fortuitous, but reflects a common immunological mechanism.
authors.affiliation: Internal Medicine Department, Hospital de Basurto, Bilbao, Spain.
authors.forename: P
authors.initials: P
authors.lastname: Martínez-Odriozola
authors.forename: A
authors.initials: A
authors.lastname: Gutiérrez-Macías
authors.forename: I
authors.initials: I
authors.lastname: Moina Eguren
authors.forename: J
authors.initials: J
authors.lastname: Arrieta Lezama
mesh_terms: D019268:Antibodies, Antineutrophil Cytoplasmic / Q000097:blood*; D005921:Glomerulonephritis / Q000150:complications* / Q000276:immunology; D006801:Humans; D008297:Male; D008875:Middle Aged; D053146:Myeloblastin / Q000276:immunology*; D012185:Retroperitoneal Fibrosis / Q000150:complications* / Q000276:immunology
chemical_list: D019268:Antibodies, Antineutrophil Cytoplasmic; D053146:Myeloblastin