title: Pediatric lung transplantation for cystic fibrosis.
abstract: Pediatric lung transplantation for cystic fibrosis has uncertain survival effects. Three retrospective studies disagree on survival benefit. The US Lung Allocation Score has changed patient selection for lung transplantation but confounds the analysis of survival outcomes. A prospective trial is needed to resolve clinical equipoise and explore quality-of-life effects.
authors.affiliation: Department of Internal Medicine, University of Utah, Salt Lake City, UT, USA. ted.liou@utah.edu
authors.forename: Theodore G
authors.initials: TG
authors.lastname: Liou
authors.forename: Barbara C
authors.initials: BC
authors.lastname: Cahill
mesh_terms: D002648:Child; D003550:Cystic Fibrosis / Q000601:surgery*; D006085:Graft Survival; D006801:Humans; D016040:Lung Transplantation; D018579:Patient Selection; D016896:Treatment Outcome
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