Association of idiopathic retroperitoneal fibrosis, rapidly progressive glomerulonephritis and antiproteinase 3 antineutrophil cytoplasmic antibodies (anti PR3-ANCA).
We report a case of idiopathic retroperitoneal fibrosis and rapidly progressive glomerulonephritis with serum antiproteinase 3 antineutrophil cytoplasmic antibodies (anti-PR3-ANCA), without clinical or histological signs of Wegener's granulomatosis, in a 46-year-old man. Our case and previously reported cases showing the same association support the hypothesis that the association is not fortuitous, but reflects a common immunological mechanism.
Martínez-Odriozola
P
P
Internal Medicine Department, Hospital de Basurto, Bilbao, Spain.
Gutiérrez-Macías
A
A
Moina Eguren
I
I
Arrieta Lezama
J
J
D019268:Antibodies, Antineutrophil Cytoplasmic / Q000097:blood*; D005921:Glomerulonephritis / Q000150:complications* / Q000276:immunology; D006801:Humans; D008297:Male; D008875:Middle Aged; D053146:Myeloblastin / Q000276:immunology*; D012185:Retroperitoneal Fibrosis / Q000150:complications* / Q000276:immunology
D019268:Antibodies, Antineutrophil Cytoplasmic; D053146:Myeloblastin