[Autoimmune polyglandular syndrome in a 13-year old girl].
Autoimmune polyglandular syndrome (APS) is an entity, defined by autoimmunity towards two or more endocrine organs. APS is classified in 3 subgroups (type-1, type-2a, type-2b), according to the organs involved. A case is presented of a 13-year old girl referred to the Department of Paediatrics with hypothyroidism, subsequently diagnosed adrenocortical insufficiency and impending Addison crisis, typical for APS-type 2a. In the paper we discuss the need for more attention to APS in clinical work.
Borgwardt
Line
L
Paediatrisk Afdeling, Hvidovre Hospital, DK-2650 Hvidovre. Line_borgwardt@hotmail.com
Pedersen
Pernille
P
Peitersen
Birgit
B
D000293:Adolescent; D003937:Diagnosis, Differential; D005221:Fatigue / Q000175:diagnosis; D005260:Female; D006801:Humans; D007037:Hypothyroidism / Q000175:diagnosis; D016884:Polyendocrinopathies, Autoimmune / Q000175:diagnosis* / Q000188:drug therapy