title: Spontaneous hemopericardium in a patient with hemophilia B: a case report and review of the literature.
abstract: Spontaneous hemopericardium is extremely rare in patients with hemophilia and has never been reported in hemophilia B-factor IX deficiency. We report a patient with hemophilia B who presented with spontaneous hemopericardium and tamponade requiring emergent pericardiocentesis. As advances in therapies improve the longevity and quality of life of patients with hemophilia, it is likely that adult interventional cardiologists will increasingly encounter these patients in the cardiac catheterization laboratory. We review the clinical challenges raised by this group of patients undergoing cardiac procedures and present a stepwise approach to optimal management during the periprocedural period.
authors.affiliation: University of Michigan Health System, Ann Arbor, MI 48109-5368, USA. deedeew@umich.edu
authors.forename: Dee Dee
authors.initials: DD
authors.lastname: Wang
authors.forename: Christos
authors.initials: C
authors.lastname: Kasapis
authors.forename: Brahmajee K
authors.initials: BK
authors.lastname: Nallamothu
mesh_terms: D015658:HIV Infections / Q000503:physiopathology; D002836:Hemophilia B / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D008297:Male; D008875:Middle Aged; D010490:Pericardial Effusion / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D020519:Pericardiocentesis; D013997:Time Factors