title: An incidental coexistence of Mayer-Rokitansky-Kuster-Hauser syndrome with pelvic ectopic kidney and perirenal endometrioma.
abstract: In this case report, a Mayer-Rokitansky-Kuster-Hauser syndrome with pelvic ectopic kidney and a perirenal cyst with endometrial tissue inside is demonstrated. A 17 year old patient admitted with primary amenorrhea. Pubertal stages were completed. In pelvic ultrasonography; uterus could not be detected, a 6 x 11 cm sized cystic lesion was seen on the right adnexal area. A centrally located 5.5 x 9 cm sized ectopic pelvic kidney was detected. Hormones and tumor markers were normal. Laparoscopy was planned. In the laparoscopic observation, uterus and both tubes could not be detected, ovaries were normal. There was a 6 x 7 cm sized cyst located in the retroperitoneal area, the origin of the cyst could not be identified. Laparatomy was considered, retroperitoneal space was entered, an 8 x 11 cm sized smooth contoured perirenal cyst adjacent to the pelvic kidney was detected. Cyst was extirpated. The pathology result was reported to include endometrial tissue and hemorrhage inside.
authors.affiliation: Department of Obstetrics and Gynecology, Meram Medicine Faculty, Selcuk University, Akyokus, 42080 Konya, Turkey. drobalci@yahoo.com
authors.forename: Osman
authors.initials: O
authors.lastname: Balci
authors.forename: Rengin
authors.initials: R
authors.lastname: Karatayli
authors.forename: Metin
authors.initials: M
authors.lastname: Capar
mesh_terms: D000015:Abnormalities, Multiple; D000293:Adolescent; D004715:Endometriosis / Q000150:complications*; D005260:Female; D006801:Humans; D007668:Kidney / Q000002:abnormalities*; D009095:Mullerian Ducts / Q000002:abnormalities*; D010532:Peritoneal Diseases / Q000150:complications*; D014599:Uterus / Q000002:abnormalities*; D014621:Vagina / Q000002:abnormalities*