title: Inflammatory myofibroblastic tumor presenting with esophageal obstruction and an inflammatory syndrome.
abstract: Inflammatory myofibroblastic tumor is a rare neoplasm of intermediate malignant potential. Although inflammatory myofibroblastic tumor occurs at multiple anatomic locations, an esophageal lesion is extremely rare. We describe a 43-year-old man who presented with severe dysphagia and an inflammatory syndrome, secondary to esophageal inflammatory myofibroblastic tumor. The patient was treated successfully with esophagectomy and remains disease free at 1 year. This case illustrates the complexities involved in managing a large esophageal myofibroblastic tumor and highlights that esophagectomy, rather than enucleation, should be the treatment of choice.
authors.affiliation: Department of Surgery, Fletcher Allen Health Care/University of Vermont, Burlington, Vermont 06401, USA. alicia.privette@vtmednet.org
authors.forename: Alicia
authors.initials: A
authors.lastname: Privette
authors.forename: Peter
authors.initials: P
authors.lastname: Fisk
authors.forename: Bruce
authors.initials: B
authors.lastname: Leavitt
authors.forename: Kumarasen
authors.initials: K
authors.lastname: Cooper
authors.forename: Laurence
authors.initials: L
authors.lastname: McCahill
mesh_terms: D000328:Adult; D000714:Anastomosis, Surgical / Q000379:methods; D003937:Diagnosis, Differential; D004935:Esophageal Diseases / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D004938:Esophageal Neoplasms / Q000175:diagnosis; D004940:Esophageal Stenosis / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D016629:Esophagectomy / Q000379:methods; D005500:Follow-Up Studies; D006104:Granuloma, Plasma Cell / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D006801:Humans; D007249:Inflammation / Q000175:diagnosis; D008297:Male; D035583:Rare Diseases; D018570:Risk Assessment; D012720:Severity of Illness Index; D013577:Syndrome; D016896:Treatment Outcome