Bilateral anterior hip dislocation in a child with Aarskog syndrome: a case report.
Both Aarskog syndrome and atraumatic anterior hip dislocation are rare entities. Aarskog syndrome is an X-linked recessive disorder with facial, digital, and genital anomalies and is associated with varying degrees of ligamentous laxity. This is believed to be the only known reported case of bilateral anterior voluntary dislocating hips in an ambulatory child and the only reported case of hip dislocation in a child with Aarskog syndrome. Staged bilateral varus derotational femoral osteotomies and Dega osteotomies were successfully performed. Hardware was removed 1 year after the second operation. The patient has been asymptomatic at 2 years' follow-up. This article calls attention to the features of Aarskog syndrome and potential orthopaedic concerns.
Zielinski
Julie A
JA
Department of Orthopaedic Surgery, McLaren Regional Medical Center, Flint, MI 48532, USA. platenscrews@yahoo.com
Pack
Larry L
LL
D000015:Abnormalities, Multiple / Q000503:physiopathology*; D002648:Child; D020878:Device Removal / Q000379:methods; D005269:Femur / Q000473:pathology / Q000601:surgery; D005500:Follow-Up Studies; D006618:Hip Dislocation, Congenital / Q000209:etiology / Q000503:physiopathology* / Q000601:surgery; D006801:Humans; D008022:Ligaments / Q000473:pathology; D008297:Male; D010027:Osteotomy / Q000379:methods*; D013577:Syndrome