[Clinical characteristics of hemophilic pseudotumor: analysis of 8 cases].
OBJECTIVE
To analyze the clinical manifestations and imaging features of hemophilic pseudotumor.


METHODS
Eight patients with hemophilic pseudotumor, all males, aged 26.1 (18 -38), were hospitalized, underwent resection of pseudotumor and bone reconstruction, and followed up for 38.6 months (7 months to 11 years). The clinical data were analyzed.


RESULTS
Femur was involved in 4 patient, and fifth metacarpus, iliopsoas, quadriceps femoris, and gastrocnemius were involved in 1 patient respectively. No recurrence was found. Excellent healing was seen in 6 cases, claudication occurred in 1 case with shortening femur, while unpleasant outcome happened to 1 case because of formation of clotting factor inhibitor, together with poor wound-healing waiting for amputation.


CONCLUSIONS
Medical history and imaging features are essential for the diagnosis of hemophilic pseudotumor. It is the key for successful treatment to master its clinical characteristics.
Department of Orthopedic Surgery, Peking Union Medical College Hospital, Chinese Academy of Medical Science and Peking Union Medical College, Beijing 100730, China.
Zeng-Xin
ZX
Gao
Xi-Sheng
XS
Weng
Gui-Xing
GX
Qiu
Yong-Qiang
YQ
Zhao
Bai
B
Shao
Jin
J
Lin
Xue-Song
XS
Wang
Xin-Yu
XY
Yang
D000293:Adolescent; D000328:Adult; D001779:Blood Coagulation Factors / Q000378:metabolism; D001847:Bone Diseases / Q000175:diagnosis / Q000209:etiology / Q000601:surgery; D005169:Factor VIII / Q000378:metabolism; D006104:Granuloma, Plasma Cell / Q000175:diagnosis* / Q000209:etiology / Q000601:surgery; D006467:Hemophilia A / Q000097:blood / Q000150:complications*; D006801:Humans; D008297:Male; D016896:Treatment Outcome; D055815:Young Adult
D001779:Blood Coagulation Factors; D005169:Factor VIII