Right superior vena cava drainage into the left atrium associated with a coronary-cameral fistula occluding an atrial-septal defect: first echocardiographic, angiographic, and surgical description.
Right superior vena cava (SVC) drainage into the left atrium causing hypoxemia is a very rare congenital malformation. This anomaly can result in complications of chronic cyanosis and paradoxical embolism. It rarely is associated with any other congenital malformation. This is the first case report of right SVC drainage into the left atrium associated with a coronary cameral fistula. During surgical repair, the aneurysmal part of the cameral fistula was noted to be occluding a defect in the atrial septum. Repair of the cameral fistula and rerouting of the SVC via the atrial septal defect were performed.
Department of Pediatric Cardiology and Congenital Cardiac Surgery, Indraprastha Apollo Hospital, Sarita Vihar, New Delhi, India.
Azad
A
Sushil
Joshi
J
Raja
Singh
S
Manvinder
Joshi
J
Reena
Kohli
K
Vikas
D006348:Cardiac Surgical Procedures / Q000379:methods; D017023:Coronary Angiography / Q000379:methods*; D003330:Coronary Vessel Anomalies / Q000175:diagnosis* / Q000601:surgery; D003937:Diagnosis, Differential; D004452:Echocardiography / Q000379:methods*; D005260:Female; D006325:Heart Atria / Q000002:abnormalities*; D006344:Heart Septal Defects, Atrial / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007223:Infant; D016157:Vascular Fistula / Q000175:diagnosis* / Q000601:surgery; D014683:Vena Cava, Superior / Q000002:abnormalities*