title: Airway management in Nager Syndrome.
abstract: Nager acrofacial dysostosis is a rare congenital syndrome characterized by malformed mandibulofacial structures and pre-axial upper limbs. Trismus and glossoptosis from mandibular abnormalities predisposes infants to life-threatening respiratory distress. A case of a Nager Syndrome mother delivering a similarly afflicted fetus is presented, with approaches to maintaining both tenuous airways described. Distinguishing this condition from similar syndromes is critical for care and prognosis.
authors.affiliation: Division of Pediatric Otolaryngology, Department of Otolaryngology-Head and Neck Surgery, Stanford University School of Medicine, 801 Welch Road, Stanford, CA 94305, United States.
authors.forename: Allen S
authors.initials: AS
authors.lastname: Ho
authors.forename: Pedram
authors.initials: P
authors.lastname: Aleshi
authors.forename: Sheila E
authors.initials: SE
authors.lastname: Cohen
authors.forename: Peter J
authors.initials: PJ
authors.lastname: Koltai
authors.forename: Alan G
authors.initials: AG
authors.lastname: Cheng
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008342:Mandibulofacial Dysostosis / Q000150:complications*; D012127:Respiratory Distress Syndrome, Newborn / Q000209:etiology* / Q000628:therapy*; D013577:Syndrome; D014140:Tracheotomy