title: Restrictive cardiomyopathy in a child.
abstract: Restrictive cardiomyopathy in young children is rare and carries a poor prognosis. We report an 18-month-old girl with poor feeding and abdominal distension. Except for hepatomegaly, no other gastrointestinal abnormalities were found. She had normal-sized ventricles but biatrial enlargement. Echocardiography demonstrated normal systolic but impaired diastolic function. Cardiac catheterization revealed a characteristic dip-and-plateau configuration of the right ventricular pressure tracing. The diagnosis turned out to be typical restrictive cardiomyopathy. The patient was maintained on aspirin while awaiting cardiac transplant.
authors.affiliation: Department of Pediatrics, Mackay Memorial Hospital, Taipei, Taiwan.
authors.forename: Shan-Miao
authors.initials: SM
authors.lastname: Lin
authors.forename: Haw-Kwei
authors.initials: HK
authors.lastname: Hwang
authors.forename: Ming-Ren
authors.initials: MR
authors.lastname: Chen
mesh_terms: D002313:Cardiomyopathy, Restrictive / Q000175:diagnosis* / Q000503:physiopathology; D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006801:Humans; D007223:Infant