title: [Tracheal cartilaginous sleeve in craniosynostosis].
abstract: Tracheal cartilaginous sleeve (TCS) is a congenital malformation involving fusion of the tracheal arches that may be isolated to a few tracheal arches, include the entire trachea, or extend beyond the carina into the bronchi. Tracheotomy was required in 9 of 23 craniosynostosis cases undergoing gradual distraction at Osaka City General Hospital from March 2002 to April 2006. TCS was diagnosed in 5 of 9 cases-four Pfeiffer patients and one Crouzon patient. Diagnosis was made intraoperatively during tracheotomy or at autopsy. 3D-CT was not useful in diagnosing TCS. Aggressive management of respiratory infection and pulmonary secretion, selection of appropriate tracheostomy tubes, and endoscopic evaluation are very important to care in managing TCS patients.
authors.affiliation: Department of Pediatric Otorhinolaryngology, Osaka City General Hospital, Osaka.
authors.forename: Tomoaki
authors.initials: T
authors.lastname: Nakano
authors.forename: Tsunemasa
authors.initials: T
authors.lastname: Aiba
authors.forename: Takeshi
authors.initials: T
authors.lastname: Kubo
authors.forename: Makoto
authors.initials: M
authors.lastname: Kusuki
authors.forename: Ayako
authors.initials: A
authors.lastname: Hirano
authors.forename: Naoki
authors.initials: N
authors.lastname: Matsushita
mesh_terms: D000168:Acrocephalosyndactylia / Q000628:therapy; D003394:Craniofacial Dysostosis / Q000628:therapy; D003398:Craniosynostoses / Q000628:therapy*; D005260:Female; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D014132:Trachea / Q000002:abnormalities* / Q000473:pathology / Q000601:surgery; D014139:Tracheostomy; D014140:Tracheotomy / Q000379:methods