title: Primary desmoplastic small round cell tumor of the kidney in a 7-year-old girl.
abstract: Desmoplastic small round cell tumor (DSRCT) is a rare pathologic entity that most frequently affects the peritoneal cavity and presents in adolescent boys. It often presents at an advanced stage and has a generally poor prognosis. We present an unusual case of DSRCT of the kidney presenting in a young girl. This is the first report of DSRCT of the kidney in the pediatric population, and it suggests that this condition should be a diagnostic consideration when assessing a child with a kidney mass.
authors.affiliation: Department of Urology, Children's Hospital Boston, 300 Longwood Avenue, HU-390, Boston, MA 02115, USA.
authors.forename: Samuel H
authors.initials: SH
authors.lastname: Eaton
authors.forename: Marc A
authors.initials: MA
authors.lastname: Cendron