Small omphalocele with umbilical evagination of the bladder: a distinct entity?
A neonatal case of umbilical evagination of the bladder combined with a small omphalocele is presented. This rare congenital malformation has previously been described in only three cases. Umbilical evagination can be understood as a disturbance of development of both the vitelline and allantoic ducts, resulting in a non-descended but otherwise normal bladder opening to the inferior margin of a small omphalocele. Diagnosis is made by clinical inspection and ultrasound. Since other malformations are not present, this entity may be regarded as a minor form of a lower midline defect with excellent prognosis.
Werner
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T
Department of Surgical Pediatrics, Children's Hospital, Inselspital, University of Berne, CH-3010 Bern, Switzerland.
Engel
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Berger
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