Long-term survival of an infant with gliomatosis cerebelli.
Gliomatosis cerebri is an uncommon but well-established central nervous system neoplasm that occurs primarily in adults. Although the neoplastic process typically arises in the cerebrum, it often spreads to brainstem, cerebellum, or even the spinal cord. In this report the authors document the surgical treatment of a 13-month-old boy whose tumor arose in the cerebellum and over time extended to the thalamus where its growth halted at age 3 years and 10 months. Aside from 2 partial resections the patient underwent neither radiotherapy nor chemotherapy. He is now 21 years old and functions independently.
Rorke-Adams
Lucy B
LB
Department of Pathology and Laboratory Medicine, Division of Neuropathology, The Children's Hospital of Philadelphia, University of Pennsylvania School of Medicine, Philadelphia, Pennsylvania 19104, USA. Rorke@email.chop.edu
Portnoy
Harold
H
D000328:Adult; D002528:Cerebellar Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery*; D018572:Disease-Free Survival; D006801:Humans; D007223:Infant; D008297:Male; D009361:Neoplasm Invasiveness; D018302:Neoplasms, Neuroepithelial / Q000150:complications / Q000473:pathology* / Q000601:surgery*; D016896:Treatment Outcome