Atresia of proximal coronary arteries in pulmonary atresia with intact ventricular septum - fetal and neonatal findings.
Pulmonary atresia with intact ventricular septum (PA+IVS) is a rare congenital cardiac malformation which is associated with ventriculocoronary arterial communications from the right ventricle. We present a case of PA+IVS with a bilateral atresia of the coronary ostia, and thus, a completely right ventricular-dependent coronary circulation followed up by fetal echocardiography. Eventually the infant died of myocardial infarction at 2 days of age.
Sarkola
Taisto
T
Division of Pediatric Cardiology, Department of Pediatrics, HUCH Hospital for Children and Adolescents, Helsinki, Finland. taisto.sarkola@hus.fi
Boldt
Talvikki
T
Happonen
Juha-Matti
JM
Karikoski
Riitta
R
Eronen
Marianne
M
D000328:Adult; D001706:Biopsy; D017023:Coronary Angiography; D003330:Coronary Vessel Anomalies / Q000000981:diagnostic imaging* / Q000473:pathology; D017809:Fatal Outcome; D005260:Female; D006346:Heart Septum / Q000000981:diagnostic imaging*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D009203:Myocardial Infarction / Q000175:diagnosis; D011247:Pregnancy; D018633:Pulmonary Atresia / Q000000981:diagnostic imaging*; D016216:Ultrasonography, Prenatal