title: A case of IgG4-associated cholangitis and autoimmune pancreatitis responsive to corticosteroids.
abstract: BACKGROUND
  A 72-year-old male presented to the emergency department with epigastric pain, anorexia and progressive jaundice of 1 week's duration. He had no prior history of gastrointestinal illness, diabetes or cancer. He did not smoke or consume alcohol. He did have a family history of colon and bone cancer.
  
  
  METHODS
  Biochemical and serologic studies, CT scan, abdominal ultrasound, endoscopic ultrasound, endoscopic retrograde cholangiopancreatography, biliary cytology, pancreas needle biopsies and immunohistochemical stainings.
  
  
  METHODS
  Autoimmune pancreatitis with IgG(4)-associated sclerosing cholangitis affecting the extrahepatic biliary ducts and mimicking primary sclerosing cholangitis and cholangiocarcinoma.
  
  
  RESULTS
  Corticosteroids and immunomodulatory therapy.
authors.affiliation: Internal Medicine, New York-Presbyterian Hospital/Weill Cornell Medical College, NY, USA.
authors.forename: Aaron J
authors.initials: AJ
authors.lastname: Small
authors.forename: Conor G
authors.initials: CG
authors.lastname: Loftus
authors.forename: Thomas C
authors.initials: TC
authors.lastname: Smyrk
authors.forename: Todd H
authors.initials: TH
authors.lastname: Baron
mesh_terms: D000368:Aged; D001327:Autoimmune Diseases; D018281:Cholangiocarcinoma / Q000175:diagnosis*; D015209:Cholangitis, Sclerosing / Q000188:drug therapy / Q000276:immunology*; D003937:Diagnosis, Differential; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D007074:Immunoglobulin G / Q000276:immunology*; D008297:Male; D010195:Pancreatitis / Q000188:drug therapy / Q000276:immunology*; D016896:Treatment Outcome
chemical_list: D005938:Glucocorticoids; D007074:Immunoglobulin G