Profound hypoxemia and pulmonary hypertension in a 7-month-old infant: late presentation of alveolar capillary dysplasia.
OBJECTIVE
To report a case of an oldest previously asymptomatic infant diagnosed with alveolar capillary dysplasia who lived a relatively normal life until 7 months of age.


METHODS
Descriptive case report.


METHODS
Intensive care unit of a tertiary care children's hospital.


METHODS
Seven-month-old female infant with profound hypoxemia and pulmonary hypertension.


CONCLUSIONS
Alveolar capillary dysplasia should be considered with a high index of suspicion in an infant who presents with pulmonary hypertension beyond the neonatal period and for which no anatomical cause can be found. Early consideration of open lung biopsy may prevent using costly, invasive, and probably ineffective procedures such as extracorporeal membrane oxygenation.
Ahmed
Sheikh
S
Department of Pediatric Critical Care, , James Whitcomb Riley Hospital for Children, Indianapolis, IN, USA. ssahmed@iupui.ed
Ackerman
Veda
V
Faught
Philip
P
Langston
Claire
C
D001706:Biopsy; D002196:Capillaries / Q000473:pathology*; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications*; D000860:Hypoxia / Q000150:complications*; D007223:Infant; D011650:Pulmonary Alveoli / Q000098:blood supply* / Q000473:pathology