Patient with congenital optic nerve meningocele presenting with left orbital cyst.
BACKGROUND
Meningocele of the optic nerve is a rare condition defined as dilatation of the optic nerve by spinal fluid not due to other pathology, classically presenting with headaches or progressive visual decline and usually follows a rapidly progressive course.


CONCLUSIONS
Surgical decompression is the standard treatment with improvement or arrest of progression in most cases. We describe a case of a child with multiple congenital anomalies including a left optic nerve meningocele that progressively expanded and caused displacement of the orbit laterally resulting in severe cosmetic deformity and complete blindness in the left eye. We describe our surgical decompression as well as review the literature on optic nerve meningocele.
Spooler
Justin C
JC
Department of Neurological Surgery, Loma Linda University Medical Center, 11234 Anderson St, Loma Linda, CA 92354, USA. jspooler@llu.edu
Cho
David
D
Ray
Andrea
A
Zouros
Alexander
A
D001766:Blindness / Q000209:etiology; D002648:Child; D003560:Cysts / Q000209:etiology / Q000473:pathology*; D019299:Decompression, Surgical / Q000379:methods; D006801:Humans; D008279:Magnetic Resonance Imaging; D008588:Meningocele / Q000150:complications / Q000473:pathology / Q000601:surgery*; D009901:Optic Nerve Diseases / Q000150:complications / Q000151:congenital / Q000601:surgery*; D009916:Orbital Diseases / Q000209:etiology / Q000473:pathology*; D016896:Treatment Outcome