title: Cardiac and great vessel involvement in "Behcet's disease".
abstract: Behcet's disease is a multisystem disorder and classified as "vasculitic syndrome with a wide variety of clinical manifestations." Cardiac involvement is very rare but can occur with different presentations including: pericarditis, cardiomyopathy, endocarditis, endomyocardial fibrosis, intracavitary thrombosis, and coronary artery disease. Great vessel involvement is more common. Recurrent Phlebitis, commonly involving large vessels (superior vena cava, inferior vena cava, hepatic veins) and cerebral veins are the sole presentation in this regard. Arterial involvement is expressed by aneurysm or pseudoaneurysmal formation. Due to the wide variety of cardiovascular manifestations and the resulting high mortality, cardiac surgeons should be familiar with this disease. In this paper we review the articles and introduce our four cases presenting with aneurysm of ascending aorta with free aortic insufficiency, aneurysm of descending aorta, pulmonary artery aneurysm, and pseudoaneurysm of aortic arch.
authors.affiliation: Tehran Heart Center, Medical Sciences, University of Tehran, Tehran, Iran. mehrabmarzban2007@yahoo.com
authors.forename: Mehrab
authors.initials: M
authors.lastname: Marzban
authors.forename: Mohammad Hossein
authors.initials: MH
authors.lastname: Mandegar
authors.forename: Abbasali
authors.initials: A
authors.lastname: Karimi
authors.forename: Kyomars
authors.initials: K
authors.lastname: Abbasi
authors.forename: Namvar
authors.initials: N
authors.lastname: Movahedi
authors.forename: Mohammad Ali
authors.initials: MA
authors.lastname: Navabi
authors.forename: Seyed Hesameddin
authors.initials: SH
authors.lastname: Abbasi
authors.forename: Naghmeh
authors.initials: N
authors.lastname: Moshtaghi
mesh_terms: D000328:Adult; D000783:Aneurysm / Q000209:etiology* / Q000601:surgery; D017541:Aneurysm, False / Q000473:pathology / Q000601:surgery; D001014:Aortic Aneurysm / Q000209:etiology; D017544:Aortic Aneurysm, Abdominal / Q000209:etiology; D017545:Aortic Aneurysm, Thoracic / Q000209:etiology; D001528:Behcet Syndrome / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D006348:Cardiac Surgical Procedures; D002318:Cardiovascular Diseases / Q000209:etiology* / Q000401:mortality / Q000601:surgery; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D011651:Pulmonary Artery / Q000473:pathology