title: Progressive spastic paraplegia: the combination of Scheuermann's disease, a short-segmented kyphosis and dysplastic thoracic spinous processes.
abstract: METHODS
  Case report.
  
  
  OBJECTIVE
  To describe a rare case of paraplegia in a patient with Scheuermann's disease and dysplastic thoracic spinous processes.
  
  
  METHODS
  Spinal Cord Injury Center, Orthopaedic University Hospital Heidelberg, Heidelberg, Germany.
  
  
  METHODS
  The authors report on a 15-year-old boy with progressive incomplete spastic paraplegia presenting segmental dysplastic thoracic spinous processes and Scheuermann's disease. The magnetic resonance imaging showed a kyphotic angulation at T 5/6 and signs of myelopathy. Hypoplastic thoracic processes and hypoplastic paraspinal muscles in the upper thoracic spine were observed intraoperatively. In this case, dorsoventral stabilization from T 4-7 was performed and the neurological outcome improved at follow-up (6 months).
  
  
  CONCLUSIONS
  Paraplegia can be accelerated in patients with Scheuermann's disease, severe kyphotic angulation and dysplastic posterior elements. After operative treatment, neurological recovery and a normal walking pattern were shown.
authors.affiliation: Department of Spine Surgery and Spinal Cord Injury Center, Orthopaedic University Hospital Heidelberg, Heidelberg, Germany. cornelia.putz@ok.uni-heidelberg.de
authors.forename: C
authors.initials: C
authors.lastname: Putz
authors.forename: I
authors.initials: I
authors.lastname: Stierle
authors.forename: T
authors.initials: T
authors.lastname: Grieser
authors.forename: G
authors.initials: G
authors.lastname: Mohr
authors.forename: H J
authors.initials: HJ
authors.lastname: Gerner
authors.forename: C H
authors.initials: CH
authors.lastname: Fürstenberg
authors.forename: B
authors.initials: B
authors.lastname: Wiedenhöfer
mesh_terms: D000293:Adolescent; D018450:Disease Progression; D006801:Humans; D007738:Kyphosis / Q000150:complications* / Q000175:diagnosis / Q000532:radiotherapy / Q000601:surgery; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D010264:Paraplegia / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D011859:Radiography; D012544:Scheuermann Disease / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D013904:Thoracic Vertebrae / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery