title: Delayed diagnosis of a neuroBehçet patient with only brainstem and cerebellar atrophy: literature review.
abstract: We report a 34-year-old male neuroBehçet's Disease (NBD) patient with atypical magnetic resonance imaging (MRI) findings, whose behavioral problems were followed by progressive neurological symptoms. The patient was hospitalized due to forgetfulness, irritability, behavioral dyscontrol and a choking sensation. T2-weighted MRI showed prominent atrophy of cerebellar hemispheres, the cerebellar peduncle, the midbrain and the pons. He was diagnosed with NBD after an evaluation of his medical history together with neuropsychiatric and laboratory findings. There are few reports of NBD with only brainstem and cerebellar atrophy. We discuss our patient in the context of the four previously reported cases. In NBD without evident mucocutaneo-ocular symptoms, neurologists should always consider the medical and family history. Early diagnosis of NBD helps to initiate appropriate treatment, thereby modulating the course of the disease and preventing complications.
authors.affiliation: Department of Neurology, Uludag University Medical Faculty, Bursa, Turkey. ozlemhan@uludag.edu.tr
authors.forename: Ozlem
authors.initials: O
authors.lastname: Taskapilioglu
authors.forename: Meral
authors.initials: M
authors.lastname: Seferoglu
authors.forename: Cengiz
authors.initials: C
authors.lastname: Akkaya
authors.forename: Bahattin
authors.initials: B
authors.lastname: Hakyemez
authors.forename: Canan
authors.initials: C
authors.lastname: Yusufoglu
authors.forename: A Nazli
authors.initials: AN
authors.lastname: Basak
authors.forename: Asli
authors.initials: A
authors.lastname: Gundogdu
authors.forename: Ibrahim
authors.initials: I
authors.lastname: Bora
mesh_terms: D000328:Adult; D001284:Atrophy; D001528:Behcet Syndrome / Q000473:pathology*; D001933:Brain Stem / Q000473:pathology*; D002526:Cerebellar Diseases / Q000473:pathology*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male