title: [Desquamative interstitial pneumonia and respiratory bronchiolitis-associated interstitial lung disease: data from the Spanish patient registry].
abstract: Among the idiopathic interstitial lung diseases, respiratory bronchiolitis-associated interstitial lung disease (RB-ILD) and desquamative interstitial pneumonia (DIP) make up a subgroup of rare diseases that are clearly smoking related. Few large case series have been published. We describe 19 cases registered in Spain: 12 patients with DIP and 7 with RB-ILD. Clinical and radiologic features are described along with clinical course, treatments applied, and outcomes. With the exception of 2 patients with DIP, all were smokers or ex-smokers. Cough and dyspnea were the most common symptoms at onset in both diseases. The most frequent radiologic findings were ground-glass opacity in DIP and pulmonary nodules in BR-ILD. Most patients were treated with corticosteroids. Outcomes were good in general; only 1 patient, with DIP, died.
authors.affiliation: Servicio de Neumología, Complejo Hospitalario, Pontevedra, España. adolfobaloira@sogapar.org
authors.forename: Adolfo
authors.initials: A
authors.lastname: Baloira
authors.forename: Antoni
authors.initials: A
authors.lastname: Xaubet
authors.forename: Eulogio
authors.initials: E
authors.lastname: Rodríguez Becerra
authors.forename: Ana Dolores
authors.initials: AD
authors.lastname: Romero
authors.forename: Alvaro
authors.initials: A
authors.lastname: Casanova
authors.forename: Julio
authors.initials: J
authors.lastname: Ancochea
mesh_terms: D001988:Bronchiolitis / Q000175:diagnosis / Q000188:drug therapy; D005260:Female; D006801:Humans; D017563:Lung Diseases, Interstitial / Q000175:diagnosis / Q000188:drug therapy; D008297:Male; D008875:Middle Aged; D012042:Registries; D013030:Spain