Papillon-Lefevre syndrome: a case report.
Papillon-Lefevre syndrome is a rare autosomal recessive genetic disorder. The clinical manifestations include palmer planter hyperkeratosis with precocious progressive periodontal disease that results in premature exfoliation of primary and permanent dentitions. Patients are often edentulous at an early age. This is a case report of prosthodontic rehabilitation of a 15-year-old girl with Papillon-Lefevre syndrome.
Subramaniam
P
P
Department of Pedodontics and Preventive Dentistry, The Oxford Dental College, Hospital and Research Centre, Bommanahalli, Hosur Road, Bangalore - 560 068, Karnataka, India. drpriyapedo@yahoo.com
Mathew
S
S
Gupta
K K
KK
D000293:Adolescent; D016301:Alveolar Bone Loss / Q000503:physiopathology; D003824:Denture, Complete; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D009066:Mouth, Edentulous / Q000534:rehabilitation*; D010214:Papillon-Lefevre Disease / Q000503:physiopathology*; D010518:Periodontitis / Q000503:physiopathology; D016388:Tooth Loss / Q000534:rehabilitation