[Desquamative interstitial pneumonia and respiratory bronchiolitis-associated interstitial lung disease: data from the Spanish patient registry].
Among the idiopathic interstitial lung diseases, respiratory bronchiolitis-associated interstitial lung disease (RB-ILD) and desquamative interstitial pneumonia (DIP) make up a subgroup of rare diseases that are clearly smoking related. Few large case series have been published. We describe 19 cases registered in Spain: 12 patients with DIP and 7 with RB-ILD. Clinical and radiologic features are described along with clinical course, treatments applied, and outcomes. With the exception of 2 patients with DIP, all were smokers or ex-smokers. Cough and dyspnea were the most common symptoms at onset in both diseases. The most frequent radiologic findings were ground-glass opacity in DIP and pulmonary nodules in BR-ILD. Most patients were treated with corticosteroids. Outcomes were good in general; only 1 patient, with DIP, died.
Baloira
Adolfo
A
Servicio de Neumología, Complejo Hospitalario, Pontevedra, España. adolfobaloira@sogapar.org
Xaubet
Antoni
A
Rodríguez Becerra
Eulogio
E
Romero
Ana Dolores
AD
Casanova
Alvaro
A
Ancochea
Julio
J
D001988:Bronchiolitis / Q000175:diagnosis / Q000188:drug therapy; D005260:Female; D006801:Humans; D017563:Lung Diseases, Interstitial / Q000175:diagnosis / Q000188:drug therapy; D008297:Male; D008875:Middle Aged; D012042:Registries; D013030:Spain