title: Bilateral trapped lung with concomitant Wermer's syndrome and cutis laxa.
abstract: We report a rare occurrence of trapped lung associated with Wermer's syndrome and cutis laxa. A 25-year-old man with bilateral trapped lung presented with respiratory distress. Additional investigation revealed adenoma of the parathyroid and hypophysis, a neuroendocrine abdominal tumor, and cutis laxa. Successful treatment of the respiratory symptoms was achieved through a median sternotomy with bilateral decortication, and excision of the bilateral fibrous pleural bands and bullae on the right upper lobe. Octreotide therapy was initiated and a percutaneous ultrasound-guided alcohol injection to the parathyroid adenoma was done. The patient has gynecomastia, acromegaly, and kyphoscoliosis. The patient remains well at 19 months after treatment.
authors.affiliation: Department of Thoracic Surgery, Baskent University Faculty of Medicine, Adana Teaching and Medical Research Center, Adana, Turkey. dalokay7@yahoo.com
authors.forename: D
authors.initials: D
authors.lastname: Kilic
authors.forename: A
authors.initials: A
authors.lastname: Findikcioglu
authors.forename: E
authors.initials: E
authors.lastname: Sahin
authors.forename: A
authors.initials: A
authors.lastname: Bilen
authors.forename: O
authors.initials: O
authors.lastname: Bakiner
authors.forename: A
authors.initials: A
authors.lastname: Hatipoglu
mesh_terms: D000328:Adult; D003483:Cutis Laxa / Q000150:complications*; D006801:Humans; D008168:Lung / Q000473:pathology*; D008297:Male; D018761:Multiple Endocrine Neoplasia Type 1 / Q000150:complications* / Q000473:pathology