title: Uncommon cause of juvenile cataract: adenoma of the nonpigmented ciliary epithelium.
abstract: Adenoma of the nonpigmented ciliary epithelium developed in a 36-year-old woman, causing decreased visual acuity and a total cataract in the involved eye. Ultrasound biomicroscopy disclosed associated persistent hyperplasic primary vitreous (PHPV). Sectoral cyclectomy with removal of the mass and intracapsular cataract extraction were performed, and the tumor was submitted for histological examination. Although ciliary adenomas arising in adults are considered to be acquired, the associated PHPV suggests a congenital origin in view of the tumor's possible interference in the normal replacement of the primary vitreous by the secondary vitreous.
authors.affiliation: Department of Ophthalmology, University La Sapienza, II Faculty, Rome, Italy.
authors.forename: Rossella
authors.initials: R
authors.lastname: Appolloni
authors.forename: Marina
authors.initials: M
authors.lastname: Modesti
authors.forename: Irene
authors.initials: I
authors.lastname: Pecorella
authors.forename: Danila
authors.initials: D
authors.lastname: Palladino
authors.forename: Luciano
authors.initials: L
authors.lastname: Ciocci
mesh_terms: D000236:Adenoma / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D000328:Adult; D002386:Cataract / Q000209:etiology*; D002387:Cataract Extraction; D002924:Ciliary Body / Q000473:pathology*; D005260:Female; D006801:Humans; D033401:Microscopy, Acoustic; D054514:Persistent Hyperplastic Primary Vitreous / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery; D010857:Pigment Epithelium of Eye / Q000473:pathology*; D041623:Tomography, Optical Coherence; D014604:Uveal Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D014792:Visual Acuity