Bilateral trapped lung with concomitant Wermer's syndrome and cutis laxa.
We report a rare occurrence of trapped lung associated with Wermer's syndrome and cutis laxa. A 25-year-old man with bilateral trapped lung presented with respiratory distress. Additional investigation revealed adenoma of the parathyroid and hypophysis, a neuroendocrine abdominal tumor, and cutis laxa. Successful treatment of the respiratory symptoms was achieved through a median sternotomy with bilateral decortication, and excision of the bilateral fibrous pleural bands and bullae on the right upper lobe. Octreotide therapy was initiated and a percutaneous ultrasound-guided alcohol injection to the parathyroid adenoma was done. The patient has gynecomastia, acromegaly, and kyphoscoliosis. The patient remains well at 19 months after treatment.
Kilic
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D
Department of Thoracic Surgery, Baskent University Faculty of Medicine, Adana Teaching and Medical Research Center, Adana, Turkey. dalokay7@yahoo.com
Findikcioglu
A
A
Sahin
E
E
Bilen
A
A
Bakiner
O
O
Hatipoglu
A
A
D000328:Adult; D003483:Cutis Laxa / Q000150:complications*; D006801:Humans; D008168:Lung / Q000473:pathology*; D008297:Male; D018761:Multiple Endocrine Neoplasia Type 1 / Q000150:complications* / Q000473:pathology