Familial cherubism: the experience of the Moscow Central Institute for Stomatology and Maxillo-Facial Surgery.
The Central Institute for Stomatology and Maxillo-facial Surgery in Moscow is one the main centers for the treatment of pediatric head and neck tumors in the territory of the former Soviet Union. A series of 33 patients presenting with cherubism (24 children and 9 of their parents) is presented. The authors discuss the atypical clinical presentations, the relevant associated anomalies and the different treatment strategies. They report the first case of cherubism associated with gingival hypertrophy without neurological signs.
Roginsky
V V
VV
Central Institute for Stomatology and Maxillo-Facial Surgery, Moscow, Russia.
Ivanov
A L
AL
Ovtchinnikov
I A
IA
Khonsari
R H
RH
D002636:Cherubism / Q000150:complications / Q000235:genetics / Q000473:pathology* / Q000628:therapy; D002648:Child; D002675:Child, Preschool; D005260:Female; D005351:Fibromatosis, Gingival / Q000150:complications* / Q000473:pathology; D005886:Gingival Hypertrophy / Q000150:complications* / Q000473:pathology; D006801:Humans; D008297:Male; D008334:Mandible / Q000002:abnormalities* / Q000473:pathology; D008437:Maxilla / Q000002:abnormalities / Q000473:pathology; D010290:Parents; D010375:Pedigree; D012189:Retrospective Studies; D012426:Russia; D012720:Severity of Illness Index; D013704:Temporomandibular Joint / Q000002:abnormalities / Q000473:pathology; D014071:Tooth Abnormalities / Q000150:complications* / Q000473:pathology