title: Wegener's granulomatosis: a new entity in the growing differential diagnosis of Degos' disease.
abstract: Wegener's granulomatosis (WG) is a multisystemic vasculitis, with skin involvement in 14% of cases and with palpable purpura, subcutaneous nodules and necrotic papules as the common features.(1) We present a patient diagnosed with WG who had multiple whitish papules similar to those of malignant atrophic papulosis (Degos' disease), which appeared during a flare of his disease. Lesions of malignant atrophic papulosis are said to be pathognomonic; nevertheless, various diseases with similar clinical lesions have been described. To our knowledge, this is the first reported case of such lesions in a patient with WG, and we suggest WG should be included in the differential diagnosis of Degos' disease.
authors.affiliation: Dermatology Services, Hospital Universitario de la Princesa, Madrid, Spain. guhl@aedv.es
authors.forename: G
authors.initials: G
authors.lastname: Guhl
authors.forename: B
authors.initials: B
authors.lastname: Diaz-Ley
authors.forename: Y
authors.initials: Y
authors.lastname: Delgado
authors.forename: E
authors.initials: E
authors.lastname: Daudén
authors.forename: J
authors.initials: J
authors.lastname: Fraga
authors.forename: A
authors.initials: A
authors.lastname: García-Diez
mesh_terms: D000368:Aged; D001706:Biopsy; D003937:Diagnosis, Differential; D014890:Granulomatosis with Polyangiitis / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008297:Male; D054853:Malignant Atrophic Papulosis / Q000175:diagnosis* / Q000473:pathology