title: [Pseudo-tumoral and ischemic encephalic Erdheim-Chester disease].
abstract: BACKGROUND
  Erdheim-Chester disease (ECD) is a rare non-langerhans cell histiocytosis of unknown etiology. It is a multi-systematic xanthogranulomatous infiltration with almost constant bone involvement; the neurological manifestations are not specific and occur in 15-20% of cases.
  
  
  METHODS
  We report the case of a 59-year-old woman hospitalized for a frontal syndrome and right hemiparesis.
  
  
  RESULTS
  Imaging revealed a left caudate nucleus process with recent infarct. Cardiovascular involvement and bilateral osteosclerosis of long bones strongly suggested ECD, confirmed after biopsies of the pericardium and bone.
  
  
  CONCLUSIONS
  Pseudo-tumor encephalic ECD is very rare; the caudate nuclei is an unusual localization; ischemic stroke has been exceptionally described. Prognosis depends largely on the involvement of the central nervous and cardiovascular systems.
authors.affiliation: Service de médecine interne B, hôpital militaire d'instruction Mohammed-V, 10000 Hay Ryad, Rabat, Maroc. amez.tao@caramail.com
authors.forename: T
authors.initials: T
authors.lastname: Amezyane
authors.forename: A
authors.initials: A
authors.lastname: Abouzahir
authors.forename: D
authors.initials: D
authors.lastname: Bassou
authors.forename: Y
authors.initials: Y
authors.lastname: Zoubeir
authors.forename: S
authors.initials: S
authors.lastname: Hammi
authors.forename: F
authors.initials: F
authors.lastname: Mahassin
authors.forename: V
authors.initials: V
authors.lastname: Ohayon
authors.forename: M-I
authors.initials: MI
authors.lastname: Archane
mesh_terms: D001842:Bone and Bones / Q000000981:diagnostic imaging / Q000473:pathology; D001921:Brain / Q000473:pathology; D002544:Cerebral Infarction / Q000473:pathology; D031249:Erdheim-Chester Disease / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D010496:Pericardium / Q000473:pathology; D011559:Pseudotumor Cerebri / Q000150:complications*; D011877:Radionuclide Imaging