title: Surgical case of partial anomalous pulmonary venous connection to superior vena cava with cor triatriatum: Williams' modification and excision of diaphragm.
abstract: We experienced a successful pediatric surgical case of partial anomalous pulmonary venous connection to the superior vena cava with cor triatriatum. Echocardiography and multidetector-row computed tomography showed partial anomalous pulmonary venous connection (right upper pulmonary vein connected to the high superior vena cava) and atypical cor triatriatum (analogue to type III-A2 of Lucas-Schmidt classification: left upper pulmonary vein had dual connection to the innominate vein via vertical vein and the accessory chamber). At 8 years of age, the male patient underwent extracardiac right atrial pedicle repair of partial anomalous pulmonary venous connection to the superior vena cava (Williams' modification) and excision of the diaphragm between the accessory chamber and the left atrium simultaneously. The postoperative course was uneventful in normal sinus rhythm and there was no stenosis of newer drainage root from right upper pulmonary vein.
authors.affiliation: Department of Thoracic and Cardiovascular Surgery, Wakayama Medical University, 811-1 Kimiidera, Wakayama, Wakayama 641-8509, Japan. thiramat@wakayama-med.ac.jp
authors.forename: Takeshi
authors.initials: T
authors.lastname: Hiramatsu
authors.forename: Shigeru
authors.initials: S
authors.lastname: Komori
authors.forename: Yoshitaka
authors.initials: Y
authors.lastname: Okamura
authors.forename: Hiroyuki
authors.initials: H
authors.lastname: Suzuki
authors.forename: Takashi
authors.initials: T
authors.lastname: Takeuchi
authors.forename: Syoichi
authors.initials: S
authors.lastname: Shibuta
mesh_terms: D000015:Abnormalities, Multiple; D006348:Cardiac Surgical Procedures / Q000379:methods*; D002648:Child; D003310:Cor Triatriatum / Q000175:diagnosis / Q000601:surgery*; D003937:Diagnosis, Differential; D004452:Echocardiography; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery; D014057:Tomography, X-Ray Computed; D054079:Vascular Malformations / Q000175:diagnosis / Q000601:surgery*; D014656:Vascular Surgical Procedures / Q000379:methods*; D014683:Vena Cava, Superior / Q000002:abnormalities* / Q000601:surgery