Total knee replacements in a patient with the Morquio syndrome.
The Morquio syndrome is a rare disorder which presents with a number of musculoskeletal problems. The literature describing total knee replacement in these patients is sparse. We describe the management of a patient with bilateral instability and pain in the knees using bilateral constrained knee replacements, and followed up for five years with pre- and postoperative knee scores. We highlight the difficulties encountered and discuss the end results.
Atinga
M
M
Northern General Hospital, Sheffield, England. odiero7@hotmail.com
Hamer
A J
AJ
D019645:Arthroplasty, Replacement, Knee / Q000009:adverse effects / Q000379:methods*; D017076:Computer-Aided Design; D005269:Femur / Q000002:abnormalities / Q000601:surgery*; D006801:Humans; D007719:Knee Joint / Q000601:surgery*; D008297:Male; D009085:Mucopolysaccharidosis IV / Q000150:complications*; D011183:Postoperative Complications / Q000209:etiology; D011474:Prosthesis Design / Q000379:methods*; D016059:Range of Motion, Articular / Q000502:physiology; D016896:Treatment Outcome; D055815:Young Adult