Desmoid tumor of the tongue.
Desmoid tumors are rare neoplasms accounting for 0.03% of all neoplasms and have an estimated incidence of 2 to 4 per million per year. World Health Organization currently refers to all of the deep types of fibromatosis as desmoid-type of fibromatoses. The term "desmoid" refers to the hard, tendon-like appearance of the tumor. The etiological factors suggested include genetic, endocrine and physical factors. About fifty percent of desmoid tumors arise in the abdominal region. The extra-abdominal desmoid tumors present a difficult problem in recognition and management especially because of the striking discrepancy between its deceptively harmless microscopic appearance and its potential to attain a large size, to recur, and to infiltrate neighboring tissues in the manner of a fibrosarcoma. Desmoid tumors are very rare in the oral cavity with less than 5% of cases constituting oral soft tissue fibromatosis. A 22-year old mentally retarded female patient with desmoid tumor occurring in the tongue is presented here.
Suresh
Chandra Sekharan
CS
Department of Biomedical Dental Sciences, College of Dentistry, King Faisal University, Saudi Arabia.
Ali
Aiman A
AA
D005260:Female; D018222:Desmoid Tumors / Q000473:pathology*; D006801:Humans; D014062:Tongue Neoplasms / Q000473:pathology*; D055815:Young Adult