title: Aggressive leptomeningeal hemangioblastomatosis of the central nervous system in a patient with von Hippel-Lindau disease.
abstract: Hemangioblastomas of the central nervous system are the most common tumors seen in patients with von Hippel-Lindau (VHL) disease. A very rare case of diffuse leptomeningeal hemangioblastomatosis obliterating large areas of the subarachnoid space, both intracranial and within the spinal canal, which developed during a relatively short period, in a patient with VHL disease is presented.
authors.affiliation: Department of Radiology and Medical Imaging, University Hospital of Alexandroupolis, Democritus University of Thrace, Alexandroupolis, Greece. ncourcou@med.duth.gr
authors.forename: N A
authors.initials: NA
authors.lastname: Courcoutsakis
authors.forename: P K
authors.initials: PK
authors.lastname: Prassopoulos
authors.forename: N J
authors.initials: NJ
authors.lastname: Patronas
mesh_terms: D002490:Central Nervous System / Q000473:pathology*; D017809:Fatal Outcome; D018325:Hemangioblastoma / Q000209:etiology* / Q000473:pathology; D006801:Humans; D008297:Male; D008577:Meningeal Neoplasms / Q000209:etiology* / Q000473:pathology; D008875:Middle Aged; D013115:Spinal Canal / Q000473:pathology; D013346:Subarachnoid Space / Q000473:pathology; D006623:von Hippel-Lindau Disease / Q000150:complications* / Q000473:pathology