Papillary tumor of the pineal region: report of a rapidly progressive tumor with possible multicentric origin.
Papillary tumor of the pineal region (PTPR) is an uncommon tumor recently added to the WHO classification of CNS tumors. We report a case of PTPR in a young boy that was noteworthy for early CSF dissemination and relentless progression. In spite of intensive chemotherapy and comprehensive radiotherapy, the boy died. The neuroimaging appearance is unique with possible multicentric origin of the tumor and intense uptake of (111)In-DTPA-pentetreotide.
Sato
Takashi S
TS
Carver College of Medicine, University of Iowa, Iowa City, IA, USA.
Kirby
Patricia A
PA
Buatti
John M
JM
Moritani
Toshio
T
D001932:Brain Neoplasms / Q000175:diagnosis*; D002291:Carcinoma, Papillary / Q000175:diagnosis*; D017809:Fatal Outcome; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D004369:Pentetic Acid / Q000031:analogs & derivatives*; D010870:Pineal Gland / Q000000981:diagnostic imaging* / Q000473:pathology*; D010871:Pinealoma / Q000175:diagnosis*; D011877:Radionuclide Imaging; D019275:Radiopharmaceuticals
C452379:DTPA pentetreotide; D019275:Radiopharmaceuticals; D004369:Pentetic Acid