Microscopic polyangiitis: a rare ANCA-associated small-vessel vasculitis.
Microscopic Polyangiitis (MPA) is an autoimmune disease characterized by pauci-immune, necrotizing, small-vessel vasculitis without clinical or pathological evidence of necrotizing granulomatous inflammation. Because many different organ systems may be involved, a wide range of symptoms are possible in MPA. Cutaneous involvement is not frequent. We describe a young girl who presented with multiple vasculitic skin lesions along with arthralgia and after the onset of illness it took 4 years for appropriate diagnosis and management of the disease.
Farooq
Muhammad
M
Department of Dermatology, Combined Military Hospital, Muzaffarabad.
Arfan-ul-Bari
D019268:Antibodies, Antineutrophil Cytoplasmic / Q000276:immunology*; D001327:Autoimmune Diseases / Q000473:pathology*; D005260:Female; D006801:Humans; D012867:Skin / Q000098:blood supply*; D014657:Vasculitis / Q000473:pathology*; D055815:Young Adult
D019268:Antibodies, Antineutrophil Cytoplasmic