title: Hybrid transcatheter-surgical strategy in arterial tortuosity syndrome.
abstract: Arterial tortuosity syndrome is a rare connective tissue disorder characterized by elongation and tortuosity of large elastic arteries resulting in multiple vascular stenoses. This article reports on a novel hybrid transcatheter-surgical strategy to treat bilateral peripheral pulmonary artery stenoses due to this syndrome. Operation consisted of stent implantation by midline sternotomy and reductive reconstruction of the proximal pulmonary arteries. This approach resulted in right ventricular overload relief and sudden improvement of the patient's clinical condition.
authors.affiliation: Department of Cardiology, A O Monaldi 2nd University of Naples, Naples, Italy. santoropino@tin.it
authors.forename: Giuseppe
authors.initials: G
authors.lastname: Santoro
authors.forename: Giuseppe
authors.initials: G
authors.lastname: Caianiello
authors.forename: Giovanni
authors.initials: G
authors.lastname: Rossi
authors.forename: Gabriella
authors.initials: G
authors.lastname: Farina
authors.forename: Maria Giovanna
authors.initials: MG
authors.lastname: Russo
authors.forename: Raffaele
authors.initials: R
authors.lastname: Calabrò
mesh_terms: D001013:Aorta, Thoracic / Q000002:abnormalities; D001017:Aortic Coarctation / Q000175:diagnosis; D006332:Cardiomegaly / Q000175:diagnosis; D002675:Child, Preschool; D006801:Humans; D006972:Hypertelorism; D007593:Joint Instability; D008297:Male; D009123:Muscle Hypotonia; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery*; D011859:Radiography; D015607:Stents; D013577:Syndrome; D054079:Vascular Malformations / Q000000981:diagnostic imaging / Q000601:surgery*