Wegener's granulomatosis: a new entity in the growing differential diagnosis of Degos' disease.
Wegener's granulomatosis (WG) is a multisystemic vasculitis, with skin involvement in 14% of cases and with palpable purpura, subcutaneous nodules and necrotic papules as the common features.(1) We present a patient diagnosed with WG who had multiple whitish papules similar to those of malignant atrophic papulosis (Degos' disease), which appeared during a flare of his disease. Lesions of malignant atrophic papulosis are said to be pathognomonic; nevertheless, various diseases with similar clinical lesions have been described. To our knowledge, this is the first reported case of such lesions in a patient with WG, and we suggest WG should be included in the differential diagnosis of Degos' disease.
Guhl
G
G
Dermatology Services, Hospital Universitario de la Princesa, Madrid, Spain. guhl@aedv.es
Diaz-Ley
B
B
Delgado
Y
Y
Daudén
E
E
Fraga
J
J
García-Diez
A
A
D000368:Aged; D001706:Biopsy; D003937:Diagnosis, Differential; D014890:Granulomatosis with Polyangiitis / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008297:Male; D054853:Malignant Atrophic Papulosis / Q000175:diagnosis* / Q000473:pathology