title: [Case of lymphangioleiomyomatosis associated with protein-losing gastroenteropathy].
abstract: A 29-year-old woman was referred to our hospital for the intensive examination of leg edema and hypoproteinemia. CT scan of showed multiple thin-walled cysts in both lungs, suggesting lymphangioleiomyomatosis. CT scan of the abdomen, lymphoscintigraphy showed enlarged abdominal lymph nodes. Protein loss from the gastrointestinal tract was documented by measurement of the clearance of alpha-1 antitrypsin from the plasma using a 72 h stool collection and (99m)Tc human serum albumin scintigraphy. We thought that secondary lymphangiectasia with lymphangioleiomyomatosis caused protein-losing gastroenteropathy. Dietary therapy resulted in symptomatic improvement.
authors.affiliation: Division of Gastroenterology and Hepatology, Department of Internal Medicine, The Jikei University School of Medicine.
authors.forename: Akiyoshi
authors.initials: A
authors.lastname: Kinoshita
authors.forename: Isao
authors.initials: I
authors.lastname: Odagi
authors.forename: Yoshihiko
authors.initials: Y
authors.lastname: Aoki
authors.forename: Koji
authors.initials: K
authors.lastname: Hirohama
authors.forename: Haruya
authors.initials: H
authors.lastname: Ishiguro
authors.forename: Toshiki
authors.initials: T
authors.lastname: Nikami
authors.forename: Shigeo
authors.initials: S
authors.lastname: Tamaki
authors.forename: Yasuyuki
authors.initials: Y
authors.lastname: Searashi
authors.forename: Satoshi
authors.initials: S
authors.lastname: Sudou
authors.forename: Atsushi
authors.initials: A
authors.lastname: Hokari
authors.forename: Tomohisa
authors.initials: T
authors.lastname: Ishikawa
authors.forename: Michiko
authors.initials: M
authors.lastname: Negishi
authors.forename: Hirokazu
authors.initials: H
authors.lastname: Nishino
authors.forename: Hisao
authors.initials: H
authors.lastname: Tajiri
authors.forename: Masahiro
authors.initials: M
authors.lastname: Ikegami
mesh_terms: D000328:Adult; D015415:Biomarkers / Q000097:blood; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000150:complications* / Q000175:diagnosis; D008200:Lymphangiectasis / Q000209:etiology; D018192:Lymphangioleiomyomatosis / Q000150:complications* / Q000175:diagnosis; D011504:Protein-Losing Enteropathies / Q000175:diagnosis / Q000209:etiology*; D000515:alpha 1-Antitrypsin / Q000097:blood
chemical_list: D015415:Biomarkers; D000515:alpha 1-Antitrypsin