title: Clinical management for epidermolysis bullosa dystrophica.
abstract: Epidermolysis bullosa (EB) consists of a group of genetic hereditary disorders in which patients frequently present fragile skin and mucosa that form blisters following minor trauma. More than 20 subtypes of EB have been recognized in the literature. Specific genetic mutations are well characterized for most the different EB subtypes and variants. The most common oral manifestations of EB are painful blisters affecting all the oral surfaces. Dental treatment for patients with EB consists of palliative therapy for its oral manifestations along with typical restorative and periodontal procedures. The aim of this article is to describe two dental clinical treatments of recessive dystrophic EB cases and their specific clinical manifestations. The psychological intervention required during the dental treatment of these patients is also presented.
authors.affiliation: Bauru School of Dentistry, University of São Paulo.
authors.forename: Thais M
authors.initials: TM
authors.lastname: Oliveira
authors.forename: Vivien T
authors.initials: VT
authors.lastname: Sakai
authors.forename: Liliani A
authors.initials: LA
authors.lastname: Candido
authors.forename: Salete M B
authors.initials: SM
authors.lastname: Silva
authors.forename: Maria Aparecida A M
authors.initials: MA
authors.lastname: Machado
mesh_terms: D000293:Adolescent; D000891:Anti-Infective Agents, Local / Q000627:therapeutic use; D001768:Blister / Q000523:psychology / Q000628:therapy; D002675:Child, Preschool; D002710:Chlorhexidine / Q000627:therapeutic use; D003773:Dental Plaque / Q000628:therapy; D003793:Dental Restoration, Permanent; D016108:Epidermolysis Bullosa Dystrophica / Q000523:psychology / Q000628:therapy*; D005260:Female; D005500:Follow-Up Studies; D005891:Gingivitis / Q000628:therapy; D006801:Humans; D007576:Jaw, Edentulous, Partially / Q000534:rehabilitation; D008297:Male; D009059:Mouth Diseases / Q000523:psychology / Q000628:therapy*; D019226:Oral Ulcer / Q000628:therapy; D010166:Palliative Care; D010347:Patient Care Planning; D010510:Periodontal Diseases / Q000523:psychology / Q000628:therapy; D011862:Radiography, Panoramic; D014081:Tooth Extraction; D014099:Toothbrushing
chemical_list: D000891:Anti-Infective Agents, Local; D002710:Chlorhexidine