title: Cystic adenomatoid malformation of the lung causing hydrops fetalis: case report and review of the literature.
abstract: OBJECTIVE
  Fetal congenital cystic adenomatoid malformation (CCAM) is a rare lung abnormality with a highly variable prognosis depended on the presence of fetal hydrops and the size of the cysts. In case of fetal hydrops the prognosis is fatal without intervention.
  
  
  METHODS
  Case report and literature review.
  
  
  METHODS
  We report on the ultrasound and pathological findings of a hydropic fetus due to a CCAM Type II at 22 weeks of gestation.
  
  
  CONCLUSIONS
  Congenital cystic adenomatoid malformation is a rare fetal lung disease with an excellent prognosis in the absence of fetal hydrops. CCAM associated with fetal hydrops carries a grave prognosis but survival rates of 70% can be achieved by thoraco-amniotic drainage in those with macrocystic lesions.
authors.affiliation: Institute of Pathology, University Hospital Tuebingen, Tübingen, Germany. sarah.schott@med.uni-tuebingen.de
authors.forename: Sarah
authors.initials: S
authors.lastname: Schott
authors.forename: Susanne
authors.initials: S
authors.lastname: Mackensen-Haen
authors.forename: Markus
authors.initials: M
authors.lastname: Wallwiener
authors.forename: Gabriele
authors.initials: G
authors.lastname: Meyberg-Solomayer
authors.forename: Karl Oliver
authors.initials: KO
authors.lastname: Kagan
mesh_terms: D000328:Adult; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000150:complications*; D005260:Female; D006801:Humans; D015160:Hydrops Fetalis / Q000209:etiology*; D011247:Pregnancy