Surgical experience in a baby with congenital broncho-biliary fistula.
Congenital tracheobiliary and bronchobiliary fistulae are rare malformations in which patent communications exist between the respiratory system and biliary tract, respectively. We present a newborn who was admitted with respiratory distress and bilious tracheal discharge. Investigation revealed a bronchobiliary fistula originating from the left main bronchus, as well as biliary atresia. Excision of the bronchobiliary fistula was successful and the connection between biliary tract and gastrointestinal system was established by performance of a Roux-en-Y cholecysto-jejunostomy. Diagnostic tools, differential diagnosis, and surgical correction strategies are discussed.
Günlemez
Ayla
A
Department of Pediatrics, Neonatal Intensive Care Unit, Kocaeli University School of Medicine, Kocaeli, Turkey.
Tugay
Melih
M
Elemen
Levent
L
Türker
Gülcan
G
Gürcan
Nagihan Inan
NI
Demir
Hakan
H
Gürbüz
Yeşim
Y
Hosten
Tulay
T
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery; D001658:Biliary Fistula / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery*; D001983:Bronchial Fistula / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery*; D003131:Combined Modality Therapy; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D007813:Laparotomy / Q000379:methods; D049268:Positron-Emission Tomography; D013902:Radiography, Thoracic; D035583:Rare Diseases; D012127:Respiratory Distress Syndrome, Newborn / Q000175:diagnosis / Q000209:etiology; D018570:Risk Assessment; D012720:Severity of Illness Index; D013908:Thoracotomy / Q000379:methods; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D014839:Vomiting / Q000175:diagnosis / Q000209:etiology