title: Hypoplasia and fibromuscular dysplasia of infrarenal abdominal aorta with downstream aneurysm: case report and review of the literature.
abstract: Fibromuscular dysplasia represents one of the more common types of arterial fibrodysplasia, a heterogeneous group of nonatherosclerotic vascular occlusive and aneurysmal diseases. This disorder mainly affects renal and cerebral arteries, and less frequently, arm, leg, and visceral arteries. Exceptionally, it has been described in the abdominal aorta. Aortic hypoplasia is a tubular narrowing of a long segment of the aorta and is a rare congenital defect, different from coarctation, which is a focal stricture. We present the first case, to our knowledge, of an elderly man with infrarenal aortic fibromuscular dysplasia associated with aortic hypoplasia, without involvement of renal arteries, and contiguous aortoiliac aneurysm.
authors.affiliation: Division of Vascular Surgery, IRCCS Policlinico San Matteo Foundation and University of Pavia, Pavia, Italy.
authors.forename: Attilio
authors.initials: A
authors.lastname: Odero
authors.forename: Antonio
authors.initials: A
authors.lastname: Bozzani
authors.forename: Vittorio
authors.initials: V
authors.lastname: Arici
authors.forename: Manuela
authors.initials: M
authors.lastname: Agozzino
mesh_terms: D000368:Aged; D001012:Aorta, Abdominal; D017544:Aortic Aneurysm, Abdominal / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D001027:Aortography; D019917:Blood Vessel Prosthesis Implantation / Q000379:methods; D003937:Diagnosis, Differential; D005352:Fibromuscular Dysplasia / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D007813:Laparotomy; D008297:Male; D014057:Tomography, X-Ray Computed