Craniofacial fibrous dysplasia of orbit.
Fibrous dysplasia is a benign, rare, and idiopathic skeletal disorder characterized by replacement and expansion of medullary bone by disorganized fibro-osseous tissue. Treatment for these lesions is usually sought for cosmetic or functional reasons. The surgical approaches vary from watchful expectancy for the lesion to stop growing after puberty to conservative resection to radical resection. In this case reports, 3 patients with craniofacial fibrous dysplasia involving orbital region underwent surgery. In these primary cases, resection and immediate reconstruction were performed to regain facial contour, dental occlusion, and masticatory function. Significant improvement was seen in facial appearance, and all patients also felt that there had been improvement aesthetically. Therefore, conservative treatment for fibrous dysplasia, unless there is involvement of vital structure as orbital region, can be suggested. Early surgery to address progressive sensory disturbance is recommended so as to avoid the hazards of late-stage decompression.
Tabrizi
Reza
R
Craniomaxillofacial Surgery Research Center, University of Shiraz, Medical Science, Shiraz, Iran.
Ozkan
Birkan Taha
BT
D002648:Child; D004954:Esthetics; D005260:Female; D005357:Fibrous Dysplasia of Bone / Q000601:surgery*; D005500:Follow-Up Studies; D005624:Frontal Bone / Q000601:surgery; D006467:Hemophilia A / Q000601:surgery; D006801:Humans; D006972:Hypertelorism / Q000601:surgery; D008297:Male; D008439:Maxillary Diseases / Q000601:surgery; D015508:Nasal Obstruction / Q000601:surgery; D009408:Nerve Compression Syndromes / Q000601:surgery; D009901:Optic Nerve Diseases / Q000601:surgery; D009916:Orbital Diseases / Q000601:surgery*; D010159:Palate / Q000601:surgery; D017060:Patient Satisfaction; D019651:Plastic Surgery Procedures / Q000379:methods; D013577:Syndrome; D014057:Tomography, X-Ray Computed; D055815:Young Adult