title: Acute constrictive pericarditis after lung transplantation for lymphangioleiomyomatosis.
abstract: Lymphangioleiomyomatosis (LAM) is a rare, cystic, progressive lung disease with many extrapulmonary manifestations, which may complicate allograft function after transplantation. We present a LAM patient with new dyspnea and declining spirometry without rejection, infection or recurrence one year after bilateral lung transplantation. Investigation revealed acute constrictive pericarditis, which has not been reported previously in a lung transplant patient with LAM. This represents a novel complication likely due to progression of extrapulmonary LAM and should be considered in LAM transplant patients with dyspnea.
authors.affiliation: Department of Medicine, University of Washington, Seattle, Washington 98104, USA. mebillin@u.washington.edu
authors.forename: Martha E
authors.initials: ME
authors.lastname: Billings
authors.forename: Michael
authors.initials: M
authors.lastname: Mulligan
authors.forename: Ganesh
authors.initials: G
authors.lastname: Raghu
mesh_terms: D000208:Acute Disease; D000328:Adult; D001706:Biopsy; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000601:surgery*; D016040:Lung Transplantation / Q000009:adverse effects*; D018192:Lymphangioleiomyomatosis / Q000601:surgery*; D010492:Pericardiectomy; D010493:Pericarditis / Q000000981:diagnostic imaging / Q000209:etiology* / Q000473:pathology / Q000601:surgery*; D010996:Pleural Effusion / Q000000981:diagnostic imaging; D011183:Postoperative Complications / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D013902:Radiography, Thoracic; D013147:Spirometry