title: Adult presentation of combined unilateral atresia of the right proximal pulmonary artery and left patent ductus arteriosus: case report and embryological considerations.
abstract: We report on a rare case of combined unilateral atresia of the proximal right pulmonary artery (PA) and left patent ductus arteriosus (PDA). A 46 year-old female patient with known PDA and associated advanced pulmonary arterial hypertension presented with progressive hemoptysis and increasing exertional dyspnea. Computed tomography of the chest proved the presence of the known PDA but surprisingly failed to demonstrate an extrapulmonary proximal right PA. We show the imaging features and discuss the embryological background of this rare congenital cardiovascular malformation.
authors.forename: Marcus-André
authors.initials: MA
authors.lastname: Deutsch
authors.forename: Sven F
authors.initials: SF
authors.lastname: Thieme
authors.forename: Martin
authors.initials: M
authors.lastname: Hinterseer
authors.forename: Thorsten R C
authors.initials: TR
authors.lastname: Johnson
authors.forename: Achim
authors.initials: A
authors.lastname: Pfosser
authors.forename: Bruno
authors.initials: B
authors.lastname: Reichart
authors.forename: Konstantin
authors.initials: K
authors.lastname: Nikolaou
authors.forename: Jürgen
authors.initials: J
authors.lastname: Behr
mesh_terms: D000367:Age Factors; D003937:Diagnosis, Differential; D004374:Ductus Arteriosus, Patent / Q000150:complications / Q000175:diagnosis* / Q000196:embryology; D005260:Female; D006801:Humans; D008875:Middle Aged; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000196:embryology*; D014057:Tomography, X-Ray Computed; D054079:Vascular Malformations / Q000150:complications / Q000175:diagnosis* / Q000196:embryology