Congenital infiltrating lipomatosis.
The congenital infiltrating lipomatosis (LCI) represents a distinct, clinical and pathological aspect of fat soft-tissue neoplasia; very few cases of which have been described in literature. In 1983, Slavin and Cols described the main characteristics of LCI as:(1) non-encapsulated tumours containing mature adipocites, (2) fat infiltration in muscles and adjacent soft parts, (3) absence of malignant characteristics, (4) absence of lipoblasts, (5) presence of fibrous elements, increased number of vessels and nerves and (6) adjacent bone hypertrophy. In this article, we describe a congenital infiltrating lipomatosis of the face in a child and discuss the diagnoses and the treatment of this disease.
Pires Fraga
Murillo Francisco
MF
Plastic Surgery Discipline of the Surgery Department, Santa Casa de São Paulo, Faculty of Medical Sciences, São Paulo, Brazil. Murifraga@ig.com.br
Mello
Daniel
D
Jorge
Douglas
D
Perin
Luis Fernando
LF
Helene
Américo
A
D002675:Child, Preschool; D003937:Diagnosis, Differential; D005145:Face / Q000473:pathology* / Q000601:surgery; D017809:Fatal Outcome; D006801:Humans; D008068:Lipomatosis / Q000151:congenital* / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D008297:Male; D009059:Mouth Diseases / Q000151:congenital / Q000175:diagnosis / Q000601:surgery