Abnormally thickened papillary muscle resulting in dynamic left ventricular outflow tract obstruction: an unusual presentation of hypertrophic cardiomyopathy.
We report the case of a symptomatic 18-year-old patient, gene-positive for hypertrophic cardiomyopathy (HCM), who presented with symptomatic dynamic left ventricular outflow tract (LVOT) obstruction caused by an abnormally thickened papillary muscle in the absence of septal hypertrophy. This was confirmed using multimodality imaging, including echocardiography and magnetic resonance imaging. He successfully underwent surgery for papillary muscle realignment without septal myectomy.
Austin
Bethany A
BA
Department of Cardiovascular Medicine, Heart and Vascular Institute, Cleveland Clinic, Cleveland, OH 44195, USA.
Kwon
Deborah H
DH
Smedira
Nicholas G
NG
Thamilarasan
Maran
M
Lever
Harry M
HM
Desai
Milind Y
MY
D009202:Cardiomyopathies / Q000150:complications* / Q000000981:diagnostic imaging*; D002312:Cardiomyopathy, Hypertrophic / Q000150:complications* / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D010210:Papillary Muscles / Q000000981:diagnostic imaging*; D035583:Rare Diseases; D014463:Ultrasonography; D014694:Ventricular Outflow Obstruction / Q000150:complications* / Q000000981:diagnostic imaging*