Extraskeletal neuroectodermal tumour of the vagina: a single case report and review.
A case report and review of an extraskeletal neuroectodermal tumour of the vagina.


BACKGROUND
Ewing's sarcoma (ES) and primitive neuroectodermal tumours (PNETs) account for approximately 6-10% of primary malignant bone tumours and, following osteosarcoma, are the second most common group of bone sarcomas in children. Ewing's sarcoma rarely affects the genitourinary tract. We report a rare case of extraskeletal Ewing's sarcoma diagnosed in a 47-year-old Indian woman presenting with a simple cystic lesion in the posterior wall of the vagina. The histopathology revealed a rare presentation of a primitive malignant extraskeletal neuroectodermal tumour.


CONCLUSIONS
As our PubMed review found only six previously reported cases of vaginal extraskeletal Ewing's sarcoma. Presentation as vaginal masses helped in early disease detection.
Al-Tamimi
Halima
H
Women's Hospital, Hamad Medical Corporation, Doha, Qatar.
Al-Hadi
Alia A
AA
Al-Khater
Al-Hareth
AH
Al-Bozom
Issam
I
Al-Sayed
Najla
N
D005260:Female; D006801:Humans; D008875:Middle Aged; D018242:Neuroectodermal Tumors, Primitive / Q000473:pathology* / Q000628:therapy; D014625:Vaginal Neoplasms / Q000473:pathology* / Q000628:therapy