title: Radiologically assisted navigation in cochlear implantation for X-linked deafness malformation.
abstract: The X-linked deafness syndrome is characterised by a complex labyrinth malformation with a shortened cochlea with missing bony separation between the cochlea and internal auditory canal and a deviant route of the facial nerve. Cochlear implant surgery in this malformation may be complicated by an unintended electrode insertion into the internal auditory canal. The authors report a new surgical approach: intraoperative three dimensional-volume tomography (3D-VT)-based navigation and direct intraoperative control by 3D-VT. The navigation dataset was based on intraoperative 3D-VT after performing the mastoidectomy and posterior tympanotomy. The cochleostomy was then performed under navigation control. After insertion, the electrode position was directly visualised by 3D-VT. On the basis of the reconstruction results, the electrode position was corrected and an intracochlear insertion resulted. Cochlear implantation in X-linked deafness malformation can be facilitated using intraoperative 3D-VT-assisted navigation and intraoperative 3D-VT control of the electrode position. This approach enhances the precision of navigation and reduces the risk of improper electrode placement and additional surgery in complex malformations.
authors.affiliation: Department of Otorhinolaryngology, University of Freiburg, Freiburg, Germany. asch@hno.ukl.uni-freiburg.de
authors.forename: Antje
authors.initials: A
authors.lastname: Aschendorff
authors.forename: Wolfgang
authors.initials: W
authors.lastname: Maier
authors.forename: Katrin
authors.initials: K
authors.lastname: Jaekel
authors.forename: Thomas
authors.initials: T
authors.lastname: Wesarg
authors.forename: Susan
authors.initials: S
authors.lastname: Arndt
authors.forename: Roland
authors.initials: R
authors.lastname: Laszig
authors.forename: Pit
authors.initials: P
authors.lastname: Voss
authors.forename: Marc
authors.initials: M
authors.lastname: Metzger
authors.forename: Dirk
authors.initials: D
authors.lastname: Schulze
mesh_terms: D000328:Adult; D003051:Cochlea / Q000002:abnormalities / Q000601:surgery; D019929:Cochlear Implantation / Q000379:methods*; D003638:Deafness / Q000601:surgery*; D007758:Ear, Inner / Q000601:surgery*; D040181:Genetic Diseases, X-Linked; D006801:Humans; D008297:Male