Compression therapy and liposuction of lower legs for bilateral hereditary primary lymphedema praecox.
In this report, we describe a case of bilateral non-syndromic hereditary lymphedema praecox of lower legs. The patient was diagnosed at age 16. Ten years later, he was unable to ambulate due to increased bilateral lower leg volume, continuous pain, and recurrent episodes of cellulitis. He was treated at our tertiary-care center with compression therapy and circumferential liposuction of lower legs, ankles, and dorsum of feet in order to remove hypertrophic fat deposits, facilitate conservative therapy, and decrease further risk of cellulitis. No complications were seen and compression therapy was continued. Fourteen month follow-up reveals no increase in leg volume over time, absence of pain, and no further episodes of cellulitis with complete ability to ambulate and return to normal activities. Even when it does not eliminate the underlying cause of primary lymphedema, combined therapy consisting of compression and liposuction is safe and is able to achieve control, at least on a short term, of clinically disabling conditions associated with advanced stages.
Espinosa-de-Los-Monteros
Antonio
A
Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico City, Mexico. aedlms@hotmail.com
Hinojosa
Carlos A
CA
Abarca
Leonardo
L
Iglesias
Martín
M
D000328:Adult; D002481:Cellulitis / Q000235:genetics / Q000628:therapy; D003131:Combined Modality Therapy; D004604:Elephantiasis / Q000150:complications / Q000235:genetics / Q000503:physiopathology / Q000601:surgery / Q000628:therapy*; D006801:Humans; D007866:Leg / Q000473:pathology / Q000503:physiopathology*; D015187:Lipectomy; D008209:Lymphedema / Q000150:complications / Q000235:genetics / Q000503:physiopathology / Q000601:surgery / Q000628:therapy*; D008297:Male; D010146:Pain / Q000235:genetics; D059408:Pain Management; D010147:Pain Measurement; D020127:Recovery of Function; D053828:Stockings, Compression; D016896:Treatment Outcome; D016138:Walking