Severe bilateral pyramidal tract involvement in a patient with Parry-Romberg syndrome.
Parry-Romberg syndrome (PRS) is a rare clinical entity of unknown etiology, generally characterized by a slow and progressive atrophy that affects 1 side of the face. A variety of neurologic abnormalities have been shown to coexist with PRS. However, few studies regarding pyramidal tract involvement in this disorder have been reported. We report a unique case, in which the patient presented with bilateral pyramidal tract insult and an unusual sequence of disease onset and progression. This case suggests a rarer variant of PRS, and the neurologic findings indicate that the underlying essential neural degeneration may contribute to the processing of pyramidal tract insult or this syndrome.
Miao
Jianting
J
Department of Neurology, Tangdu Hospital, Fourth Military Medical University, Xi'an City, Shaanxi Province, China.
Liu
Rui
R
Lin
Hong
H
Su
Changjun
C
Li
Hongzeng
H
Lei
Gesheng
G
Liu
Yu
Y
Zhang
Wei
W
Li
Zhuyi
Z
D000328:Adult; D005150:Facial Hemiatrophy / Q000150:complications* / Q000503:physiopathology; D005260:Female; D006801:Humans; D009410:Nerve Degeneration / Q000209:etiology*; D011712:Pyramidal Tracts / Q000503:physiopathology*