Intracranial solitary juvenile xanthogranuloma in an infant.
BACKGROUND
Juvenile xanthogranuloma (JXG) is a disorder of histiocyte proliferation. Most cases present with a solitary cutaneous lesion. JXG with systemic involvement is rare with significant morbidity. Intracranial solitary JXG may be misdiagnosed before operation.


METHODS
A 5-month-old boy showed an elevated anterior fontanel but no other abnormalities on admission. Brain MRI showed a large mass in the right parietal region.


RESULTS
The tumor was removed with the encroached meninges. A JXG in the right parietal region was diagnosed pathologically.


CONCLUSIONS
Total excision of the tumor may be curative with a prerequisite of ensuring normal vital signs and nervous function.
Sun
Lian-Ping
LP
Department of Pediatric Neurosurgery, Xin Hua Hospital Affiliated to Shanghai Jiaotong University, Shanghai, 200092, China. slp1128@126.com
Jin
Hui-Ming
HM
Yang
Bo
B
Wu
Xiang-Ru
XR
D001927:Brain Diseases / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D003287:Contrast Media; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D010296:Parietal Lobe / Q000473:pathology / Q000601:surgery; D014972:Xanthogranuloma, Juvenile / Q000150:complications* / Q000175:diagnosis / Q000601:surgery
D003287:Contrast Media