Ebstein's anomaly: a case with an unexpected evolution.
Ebstein's anomaly of the tricuspid valve is a rare and complex congenital heart defect. Its etiology is unknown and in the majority of cases it is multifactorial. Mortality in the neonatal period is high. The authors present a case of severe Ebstein's anomaly diagnosed antenatally. In the perinatal period a Blalock-Taussig shunt was performed and at the age of five months the infant underwent successful percutaneous pulmonary valvuloplasty. The clinical outcome has been favorable and we decided to postpone a Glenn procedure. At 18 months the child is asymptomatic.
Moura
Marta C
MC
Serviço de Pediatria do Hospital Fernando Fonseca, Amadora, Portugal.
Rocha
Susana
S
Ferreira
Manuel
M
Nunes
Maria Ana Sampaio
MA
Magalhães
Manuel Pedro
MP
D004437:Ebstein Anomaly / Q000601:surgery*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D012074:Remission Induction