title: Collagen VI myopathies: from the animal model to the clinical trial.
authors.affiliation: Laboratory of Cell Biology, Institute "Rizzoli", Bologna, Italy. maraldi@area.bo.cnr.it
authors.forename: Nadir M
authors.initials: NM
authors.lastname: Maraldi
authors.forename: Patrizia
authors.initials: P
authors.lastname: Sabatelli
authors.forename: Marta
authors.initials: M
authors.lastname: Columbaro
authors.forename: Alessandra
authors.initials: A
authors.lastname: Zamparelli
authors.forename: Francesco A
authors.initials: FA
authors.lastname: Manzoli
authors.forename: Paolo
authors.initials: P
authors.lastname: Bernardi
authors.forename: Paolo
authors.initials: P
authors.lastname: Bonaldo
authors.forename: Luciano
authors.initials: L
authors.lastname: Merlini
mesh_terms: D000818:Animals; D017209:Apoptosis / Q000187:drug effects; D002986:Clinical Trials as Topic; D024142:Collagen Type VI / Q000235:genetics / Q000378:metabolism* / Q000648:ultrastructure; D016572:Cyclosporine / Q000494:pharmacology / Q000627:therapeutic use; D004195:Disease Models, Animal; D004791:Enzyme Inhibitors / Q000494:pharmacology / Q000627:therapeutic use; D005109:Extracellular Matrix / Q000378:metabolism / Q000648:ultrastructure; D006801:Humans; D008928:Mitochondria / Q000378:metabolism; D018482:Muscle, Skeletal / Q000378:metabolism / Q000473:pathology / Q000648:ultrastructure; D009135:Muscular Diseases / Q000188:drug therapy / Q000235:genetics* / Q000473:pathology / Q000503:physiopathology*; D009154:Mutation
chemical_list: D024142:Collagen Type VI; D004791:Enzyme Inhibitors; D016572:Cyclosporine