title: Ebstein's anomaly: a case with an unexpected evolution.
abstract: Ebstein's anomaly of the tricuspid valve is a rare and complex congenital heart defect. Its etiology is unknown and in the majority of cases it is multifactorial. Mortality in the neonatal period is high. The authors present a case of severe Ebstein's anomaly diagnosed antenatally. In the perinatal period a Blalock-Taussig shunt was performed and at the age of five months the infant underwent successful percutaneous pulmonary valvuloplasty. The clinical outcome has been favorable and we decided to postpone a Glenn procedure. At 18 months the child is asymptomatic.
authors.affiliation: Serviço de Pediatria do Hospital Fernando Fonseca, Amadora, Portugal.
authors.forename: Marta C
authors.initials: MC
authors.lastname: Moura
authors.forename: Susana
authors.initials: S
authors.lastname: Rocha
authors.forename: Manuel
authors.initials: M
authors.lastname: Ferreira
authors.forename: Maria Ana Sampaio
authors.initials: MA
authors.lastname: Nunes
authors.forename: Manuel Pedro
authors.initials: MP
authors.lastname: Magalhães
mesh_terms: D004437:Ebstein Anomaly / Q000601:surgery*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D012074:Remission Induction