A non-midline spheno-orbital encephalocele in a newborn.
Basal encephaloceles in western countries occur in 1 of every 35 000-40 000 live births; with an incidence of less than 10% they are the least common of all encephaloceles. Certain subtypes such as transsphenoidal variants may be as rare as 1 in 700 000 live births. These rare encephaloceles are classified into five anatomic types: spheno-ethmodial, transsphenoidal, spheno-orbital, transethmoidal, and spheno-maxillary. Here we present an exceedingly rare variant of a non-midline basal encephalocele of the spheno-orbital type, which was treated by resection of the encephalocele, which contained dysplastic central nervous system tissue, on day four post partum. The patient had no neurological deficits and a six year follow-up showed a normal intellect and a good cosmetic result.
Knopp
U
U
Department of Neurosurgery, University Hospital Lübeck, Lübeck, Germany.
Knopp
A
A
Stellmacher
F
F
Reusche
E
E
Löning
M
M
Kantelhardt
S R
SR
Domarus
H von
Hv
Arnold
H
H
Giese
A
A
D002610:Cheek / Q000473:pathology; D004677:Encephalocele / Q000473:pathology* / Q000601:surgery*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D019635:Neurosurgical Procedures; D009915:Orbit / Q000002:abnormalities* / Q000473:pathology* / Q000601:surgery; D013100:Sphenoid Bone / Q000002:abnormalities* / Q000473:pathology* / Q000601:surgery; D013518:Surgery, Plastic