Cushing's syndrome caused by an ACTH-producing ovarian steroid cell tumor, NOS, in a prepubertal girl.
Ectopic ACTH syndrome is a very rare cause of pediatric Cushing's syndrome. And if present, bronchial or thymic carcinoids predominate as causes. We hereby demonstrate a first case report of ACTH-producing ovarian steroid cell tumor, NOS, causing ectopic ACTH syndrome in a prepubertal girl.
Sawathiparnich
Pairunyar
P
Division of Pediatric Endocrinology, Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand. sipry@mahidol.ac.th
Sitthinamsuwan
Panitta
P
Sanpakit
Kleebsabai
K
Laohapensang
Mongkol
M
Chuangsuwanich
Tuenjai
T
D000182:ACTH Syndrome, Ectopic / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D000471:Alkalosis / Q000150:complications; D018394:CA-125 Antigen / Q000097:blood; D002648:Child; D002940:Circadian Rhythm; D003480:Cushing Syndrome / Q000175:diagnosis / Q000209:etiology*; D003907:Dexamethasone; D005260:Female; D006801:Humans; D006854:Hydrocortisone / Q000097:blood; D006973:Hypertension / Q000150:complications; D007008:Hypokalemia / Q000150:complications; D007150:Immunohistochemistry; D010051:Ovarian Neoplasms / Q000378:metabolism* / Q000473:pathology / Q000601:surgery; D014057:Tomography, X-Ray Computed
D018394:CA-125 Antigen; D003907:Dexamethasone; D006854:Hydrocortisone