title: A non-midline spheno-orbital encephalocele in a newborn.
abstract: Basal encephaloceles in western countries occur in 1 of every 35 000-40 000 live births; with an incidence of less than 10% they are the least common of all encephaloceles. Certain subtypes such as transsphenoidal variants may be as rare as 1 in 700 000 live births. These rare encephaloceles are classified into five anatomic types: spheno-ethmodial, transsphenoidal, spheno-orbital, transethmoidal, and spheno-maxillary. Here we present an exceedingly rare variant of a non-midline basal encephalocele of the spheno-orbital type, which was treated by resection of the encephalocele, which contained dysplastic central nervous system tissue, on day four post partum. The patient had no neurological deficits and a six year follow-up showed a normal intellect and a good cosmetic result.
authors.affiliation: Department of Neurosurgery, University Hospital Lübeck, Lübeck, Germany.
authors.forename: U
authors.initials: U
authors.lastname: Knopp
authors.forename: A
authors.initials: A
authors.lastname: Knopp
authors.forename: F
authors.initials: F
authors.lastname: Stellmacher
authors.forename: E
authors.initials: E
authors.lastname: Reusche
authors.forename: M
authors.initials: M
authors.lastname: Löning
authors.forename: S R
authors.initials: SR
authors.lastname: Kantelhardt
authors.forename: H von
authors.initials: Hv
authors.lastname: Domarus
authors.forename: H
authors.initials: H
authors.lastname: Arnold
authors.forename: A
authors.initials: A
authors.lastname: Giese
mesh_terms: D002610:Cheek / Q000473:pathology; D004677:Encephalocele / Q000473:pathology* / Q000601:surgery*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D019635:Neurosurgical Procedures; D009915:Orbit / Q000002:abnormalities* / Q000473:pathology* / Q000601:surgery; D013100:Sphenoid Bone / Q000002:abnormalities* / Q000473:pathology* / Q000601:surgery; D013518:Surgery, Plastic