Concordant posterior urethral valves in male monochorionic twins with secondary prune belly syndrome.
BACKGROUND
Posterior urethral valves (PUVs), the most common congenital cause of lower urinary tract obstruction, have been described to occur in identical and nonidentical twins. Until now, reports have been published on 15 cases of PUVs.


OBJECTIVE
We report a new case of concordant PUVs in one set of male monochorionic twins with secondary Prune Belly Syndrome.


METHODS
The twins were born by elective cesarean section at 38 weeks of gestation to a 36-year-old mother, gravida 6, para 6. On ultrasound perfomed at 18 weeks's gestation, both fetuses showed signs of PUVs. At birth, physical examination of both revealed a secondary Prune Belly Syndrome (PBS). Postnatal renal ultrasound confirmed the diagnosis of PUV. The two infants underwent transurethral resection of the valves after a cystoscopic evaluation of the urethra. Since this procedure, their voiding has been unremarkable with stable renal function and sterile urine until their discharge.


CONCLUSIONS
We have documented a rare association between VUP and PBS in two monochiorionic twins. More studies are needed to throw light on the significance of the present associated anomalies.
Nouaili
Emira Ben Hamida
EB
Department of Neonatology, Charles Nicolle Hospital of Tunis.
Chaouachi
Sihem
S
Nouira
Faouzi
F
Benmassoud
Ines
I
Laabidi
Kamel
K
Chaouachi
Beji
B
Marrakchi
Zahra
Z
D003456:Cryptorchidism / Q000150:complications; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011535:Prune Belly Syndrome / Q000150:complications*; D014427:Twins; D014521:Urethra / Q000002:abnormalities* / Q000601:surgery