title: Familial hypophosphatemic vitamin D-resistant rickets--prevention of spontaneous dental abscesses on primary teeth: a case report.
abstract: Familial hypophosphatemic vitamin D-resistant rickets is a hereditary disease generally transmitted as an X-linked dominant trait and characterized by distinctive general clinical signs. Dental features include spontaneous dental abscesses that occur in the absence of a history of trauma or dental decay. The challenge for the dentist is to prevent and treat these lesions. This report describes the case of a young hypophosphatemic boy with abscesses. In this case, the application of fluid resin composites with a self-etching primer bonding system to all primary teeth prevented abscess formation for more than 1 year and thus avoided endodontic treatment or extraction. This constitutes a new approach to the prevention of spontaneous abscesses on primary teeth in children with familial hypophosphatemic rickets.
authors.affiliation: Department of Pediatric Dentistry, Dental School, Bretonneau Hospital, AP-AH, Paris Descartes University, Paris, France.
authors.forename: Diane
authors.initials: D
authors.lastname: Douyere
authors.forename: Clara
authors.initials: C
authors.lastname: Joseph
authors.forename: Céline
authors.initials: C
authors.lastname: Gaucher
authors.forename: Catherine
authors.initials: C
authors.lastname: Chaussain
authors.forename: Frederic
authors.initials: F
authors.lastname: Courson
mesh_terms: D002675:Child, Preschool; D003188:Composite Resins / Q000627:therapeutic use*; D001840:Dental Bonding; D053098:Familial Hypophosphatemic Rickets / Q000150:complications* / Q000235:genetics; D040181:Genetic Diseases, X-Linked; D006801:Humans; D008297:Male; D009154:Mutation; D053402:PHEX Phosphate Regulating Neutral Endopeptidase / Q000235:genetics; D010375:Pedigree; D010482:Periapical Abscess / Q000209:etiology / Q000517:prevention & control*; D010895:Pit and Fissure Sealants / Q000627:therapeutic use*; D014094:Tooth, Deciduous / Q000473:pathology*
chemical_list: D003188:Composite Resins; D010895:Pit and Fissure Sealants; D053402:PHEX Phosphate Regulating Neutral Endopeptidase