title: [Anaesthetic management of patients with Steinert myotonia: two case reports].
abstract: Steinert disease, the most common myopathy in adults, is a challenge for anaesthesiologists and critical care physicians during the perioperative time. The risk of myotonic crisis, malign hyperthermia and the increased sensitivity to anaesthetic drugs shouldn't be forgotten. On contrary, Steinert disease is rarely revealed in the postoperative period. It should be evoked in case of postoperative pulmonary complications such as difficult weaning with neurological symptoms like hypotonia or muscular weakness.
authors.affiliation: Service d'anesthésie-réanimation, hôpital cardiovasculaire et pneumologique Louis-Pradel, hospices civils de Lyon, 59 boulevard Pinel, Lyon cedex 03, France. aureliemahr@free.fr
authors.forename: A
authors.initials: A
authors.lastname: Mahr
authors.forename: Y
authors.initials: Y
authors.lastname: Attof
authors.forename: C
authors.initials: C
authors.lastname: Flamens
authors.forename: O
authors.initials: O
authors.lastname: Bastien
authors.forename: J-J
authors.initials: JJ
authors.lastname: Lehot
mesh_terms: D000328:Adult; D000768:Anesthesia, General / Q000379:methods*; D000771:Anesthesia, Intravenous; D055191:Delayed Emergence from Anesthesia / Q000209:etiology; D005112:Extracorporeal Circulation; D005260:Female; D006343:Heart Septal Defects / Q000150:complications / Q000601:surgery; D006801:Humans; D007431:Intraoperative Complications / Q000209:etiology / Q000517:prevention & control*; D008297:Male; D008945:Mitral Valve Prolapse / Q000150:complications / Q000601:surgery; D009123:Muscle Hypotonia / Q000209:etiology; D009207:Myoclonus / Q000209:etiology; D009223:Myotonic Dystrophy / Q000150:complications* / Q000175:diagnosis; D011183:Postoperative Complications / Q000209:etiology / Q000517:prevention & control*; D015742:Propofol / Q000008:administration & dosage; D012120:Respiration Disorders / Q000209:etiology; D012131:Respiratory Insufficiency / Q000209:etiology; D017409:Sufentanil / Q000008:administration & dosage; D020775:Thoracic Surgery, Video-Assisted
chemical_list: D017409:Sufentanil; D015742:Propofol