title: Neurological manifestations revealing primitive Gougerot-Sjogren syndrome: 9 cases.
abstract: BACKGROUND
  Neurological manifestations in Gougerot-Sjogren syndrome (GSS) are valued differently. This is essentially the achievement of the peripheral nervous system.
  
  
  METHODS
  We report 9 cases of neurological manifestation revealing primitive Gougerot-Sjogren syndrome collected over a period of 8 years (1997-2004). GSS diagnosis was retained according to Americano-European group criteria consensus revised on 2002.
  
  
  RESULTS
  All our patients were female with an average age of 43 years. Peripheral nervous system manifestation occurred in 78% (Truncal Neuropathy in 44%, anterior horn involvement in 2 cases). Central nervous system involvement was observed in 55.6% (chronic myelopathy and aseptic meningoencephalitis).
  
  
  CONCLUSIONS
  The analysis of neurological manifestations in GSS encounters three difficulties: the lack in homogeneity of diagnostic criteria (which makes it difficult to compare the frequency of neurological complications in different series), the limited number of large series, and the cases with neurological manifestations revealing this syndrome.
authors.affiliation: Service de Neurologie, Explorations Fonctionnelles, CHU Ibn Rochd, Quartier des Hôpitaux, Casablanca, Maroc. mo.mi2@caramail.com
authors.forename: Mohammed Abdoh
authors.initials: MA
authors.lastname: Rafai
authors.forename: Fatima Zohra
authors.initials: FZ
authors.lastname: Boulaajaj
authors.forename: Fettouma
authors.initials: F
authors.lastname: Moutawakil
authors.forename: Nawal
authors.initials: N
authors.lastname: Addali
authors.forename: Bouchra
authors.initials: B
authors.lastname: El Moutawakkil
authors.forename: Hicham
authors.initials: H
authors.lastname: Fadel
authors.forename: Khalid
authors.initials: K
authors.lastname: Hakim
authors.forename: Meryem
authors.initials: M
authors.lastname: Bourezgui
authors.forename: Manal
authors.initials: M
authors.lastname: Sibai
authors.forename: Hicham
authors.initials: H
authors.lastname: El Otmani
authors.forename: Ilham
authors.initials: I
authors.lastname: Slassi
mesh_terms: D000328:Adult; D000368:Aged; D002493:Central Nervous System Diseases / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology; D005260:Female; D006801:Humans; D008875:Middle Aged; D010523:Peripheral Nervous System Diseases / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology; D012189:Retrospective Studies; D012859:Sjogren's Syndrome / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology; D014985:Xerophthalmia / Q000209:etiology / Q000503:physiopathology; D014987:Xerostomia / Q000209:etiology / Q000503:physiopathology