Rosai-Dorfman disease: a case with lymphadenopathy and liver involvement.
Rosai-Dorfman disease (RDD), originally described as sinus histiocytosis with massive lymphadenopathy, is a rare histiocytic proliferative disorder with a distinctive microscopic appearance. Formerly thought to be a disease process limited to lymph nodes, RDD has now been reported in many organ systems like bone, skin and soft tissue, central nervous system, eye and orbit, and upper respiratory tract. Here we report a case of RDD with hepatic involvement, which is even more rare.
Maheshwari
Anu
A
Department of Pediatrics, Lady Hardinge Medical College, New Delhi, India.
Seth
Anju
A
Choudhury
Monisha
M
Aggarwal
Varun
V
Patra
Bijoy
B
Aggarwal
Shilpi
S
Mukherjee
Sharmila B
SB
Aneja
Satinder
S
D002675:Child, Preschool; D005260:Female; D015618:Histiocytosis, Sinus / Q000150:complications* / Q000473:pathology; D006801:Humans; D008107:Liver Diseases / Q000209:etiology*; D008198:Lymph Nodes / Q000473:pathology; D008206:Lymphatic Diseases / Q000209:etiology* / Q000473:pathology; D014057:Tomography, X-Ray Computed