Intraventricular dysembryoplastic neuroepithelial tumor-like neoplasm with disseminated spinal tumor.
Dysembryoplastic neuroepithelial tumor (DNT)- like lesions arise in extracortical locations and behave in a benign fashion similar to that of cortical DNTs. They usually come to attention by symptoms and signs of increased intracranial pressure rather than focal neurological impairment. Here we report a case of 9-year-old boy with a complaint of headache and back pain. A third ventricular mass lesion with disseminated spinal tumor was detected on his magnetic resonance imaging. The presence of floating neurons in a mucinous matrix, oligodendrocyte-like cells (OLCs) aligning axonal columns and vessels, immunohistochemical profile of the neoplasm in addition to the clinical and radiological manifestations of the patient led to the diagnosis of "DNT-like neoplasm of the third ventricle".
Bilginer
Burçak
B
Hacettepe University School of Medicine, Department of Neurosurgery, Ankara, Turkey. burcak@tr.net
Söylemezoğlu
Figen
F
Cila
Ayşenur
A
Akalan
Nejat
N
D002551:Cerebral Ventricle Neoplasms / Q000473:pathology* / Q000601:surgery; D002648:Child; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D018302:Neoplasms, Neuroepithelial / Q000556:secondary* / Q000601:surgery; D009836:Oligodendroglia / Q000473:pathology; D013125:Spinal Neoplasms / Q000556:secondary* / Q000601:surgery; D013724:Teratoma / Q000556:secondary* / Q000601:surgery; D020542:Third Ventricle / Q000473:pathology / Q000601:surgery