title: Case report of a child with otoacoustic emissions and profound hearing loss in whom otoacoustic emissions were preserved after cochlear implantation.
abstract: The management of patients characterised by the presence of otoacoustic emissions and/or cochlear microphonics suggesting normal outer hair cell function in conjunction with absent or grossly abnormal auditory brainstem responses is often associated with particularly poor response to amplification. Cochlear implantation has been shown to be an option in affected patients. Here, we report a case of successful cochlear implantation and preserved otoacoustic emissions in a child suffering from this hearing disorder.
authors.affiliation: Department of Otorhinolaryngology, Head and Neck Surgery, University of Cologne, Kerpener Strasse 62, Cologne 50937, Germany. dirk.beutner@uni-koeln.de
authors.forename: Dirk
authors.initials: D
authors.lastname: Beutner
authors.forename: Ruth
authors.initials: R
authors.lastname: Lang-Roth
authors.forename: Astrid
authors.initials: A
authors.lastname: Foerst
authors.forename: Alexander E
authors.initials: AE
authors.lastname: Volk
authors.forename: Martin
authors.initials: M
authors.lastname: Walger
mesh_terms: D001307:Auditory Perception; D019929:Cochlear Implantation; D003054:Cochlear Implants; D018072:Hair Cells, Auditory, Outer / Q000502:physiology*; D034381:Hearing Loss / Q000503:physiopathology* / Q000601:surgery / Q000628:therapy*; D006801:Humans; D007223:Infant; D008297:Male; D017084:Otoacoustic Emissions, Spontaneous