title: Transcatheter closure of a fenestration in intracardiac Fontan circulation.
abstract: We present a case of tricuspid atresia and the treatment that was used in a child now aged 12. The malformation was corrected at the age of five through intracardiac Fontan circulation. Later, the child developed a right-to-left shunt due to dehiscence in the intra-atrial conduit, causing significant desaturation. This was treated by transcatheter closure with a 10 mm Amplatzer device at 8 years of age. Currently the child is asymptomatic with no residual shunts, and the position of the device is normal. The percutaneous closure of Fontan fenestrations using the Amplatzer device is a therapeutic approach that provides good results. It results in normal oxygen saturation and has low morbidity. The technique is simple, available to most cardiac catheterization laboratories, safe, and offers a reasonable cost-benefit ratio. In addition, the design of the device is suitable for this type of defect.
authors.affiliation: Unidade de Cardiologia Pediátrica dos Hospitals da Universidade de Coimbra, Coimbra, Portugal. helenaandradecarvalho@gmail.com
authors.forename: Helena
authors.initials: H
authors.lastname: Andrade
authors.forename: Dina
authors.initials: D
authors.lastname: Rodrigues
authors.forename: A Marinho
authors.initials: AM
authors.lastname: da Silva
authors.forename: F Maymone
authors.initials: FM
authors.lastname: Martins
authors.forename: António
authors.initials: A
authors.lastname: Sá e Melo
mesh_terms: D006328:Cardiac Catheterization; D006348:Cardiac Surgical Procedures / Q000379:methods; D002648:Child; D003326:Coronary Circulation; D005260:Female; D006801:Humans; D018785:Tricuspid Atresia / Q000601:surgery*