Custom-made covered transjugular intrahepatic portosystemic shunt (TIPS) in an infant with trisomy 22 and biliary atresia.
We report an 8-month-old girl with portal hypertension secondary to biliary atresia. The decision to treat with TIPS was made at the age of 8 months due to recurrent variceal bleeding. The procedure was carried out with a 6-mm bare stent due to her small size. Radiological follow-up with Doppler US showed gradual stenosis and finally occlusion of the stent 80 days after implantation. Revision was performed with placement of an additional 6-mm expanded polytetrafluoroethylene (e-PTFE) stent-graft that had remained patent for 9 months, proving that in small children with a portal vein diameter less than 8 mm, the combination of a bare stent and stent-graft can provide excellent results.
Chlapoutaki
Chrysanthi Emmanouil
CE
Department of Paediatric Radiology, Bicêtre Hospital University Paris XI, Assistance Publique Hôpitaux de Paris, 78 rue du General Leclerc, Le Kremlin-Bicetre, Cedex 94275, Paris, France. schlapoutaki@yahoo.com
Franchi-Abella
Stephanie
S
Habes
Dalila
D
Pariente
Daniele
D
D001656:Biliary Atresia / Q000175:diagnosis* / Q000601:surgery*; D002892:Chromosomes, Human, Pair 22; D005260:Female; D006801:Humans; D007223:Infant; D019168:Portasystemic Shunt, Transjugular Intrahepatic / Q000295:instrumentation* / Q000379:methods*; D019919:Prosthesis Implantation / Q000379:methods; D016896:Treatment Outcome; D014314:Trisomy / Q000175:diagnosis*