[Congenital cystic adenomatoid lung malformation - diagnosis and treatment - based on literature and own experiences].
Congenital cystic adenomatoid malformation (CCAM) is an uncommon congenital abnormality of the lung which has a wide spectrum of potential outcomes, ranging from hydrops and severe respiratory distress with pulmonary hypoplasia, to resolution of the lesion either antenatally or postnatally. Most of the babies are asymtomaptic. It is caused by arrest of normal foetal pulmonary maturation. The prognosis is generally good. In cases where the lesion persists, surgery is recommended. CCAM is an important diagnosis and can be suspected on routine antenatal ultrasound. It has implication for both the ongoing pregnancy, at delivery and later in life. The authors present a male newborn with CCAM diagnosed during the neonatal period. The diagnosis was based on CT scan and histopathological examination. Characteristic plural cystic defects in the lungs were found. The patient was referred for surgical treatment.
Fiala
Małgorzata
M
Klinika Neonatologii Katedry Ginekologii i PołoZnictwa Slaskiego Uniwersytetu Medycznego w Katowicach, ul. Medyków 14, 40-752 Katowice, Poland. mfiala@wp.pl
Baumert
Małgorzata
M
Walencka
Zofia
Z
Włoch
Agata
A
D000328:Adult; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000000981:diagnostic imaging* / Q000601:surgery*; D005260:Female; D005315:Fetal Diseases / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D011247:Pregnancy; D011256:Pregnancy Outcome; D011295:Prenatal Care / Q000379:methods; D016216:Ultrasonography, Prenatal / Q000379:methods