Atypical Apert syndrome: sequential and segmental distraction osteogenesis of the skull, midface, and mandible.
We describe a boy with Apert syndrome, including cranial deformities and syndactyly (acrocephalosyndactyly), though intracranial hypertension, exophthalmos, and midfacial hypoplasia were mild. We treated him by mandibular distraction, in addition to fronto-orbital distraction, and Le Fort III midfacial distraction, with good results.
Mitsukawa
Nobuyuki
N
Department of Plastic and Reconstructive Surgery, St. Mary's Hospital, Fukuoka, Japan. nmitsu@air.linkclub.or.jp
Satoh
Kaneshige
K
Hayashi
Takashi
T
Morishita
Tadashi
T
Hosaka
Yoshiaki
Y
D000168:Acrocephalosyndactylia / Q000601:surgery*; D005145:Face / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D008334:Mandible / Q000601:surgery; D019857:Osteogenesis, Distraction / Q000379:methods*; D012886:Skull / Q000601:surgery