Pityriasis rubra pilaris type 1 spontaneously resolving after 20 years.
Pityriasis rubra pilaris (PRP) is an uncommon, idiopathic, papulosquamous eruption. We report a longitudinal study of a patient with PRP type 1 who was treated with retinoid therapy for 9 years and whose symptoms resolved spontaneously after 20 years. There are no data in the literature on the disease course of PRP type 1 persisting beyond the usual 3 years. This case highlights both the extreme chronicity of PRP and the possibility of remission after many years of active disease.
Abbott
R A
RA
Department of Dermatology, Guy's and St Thomas' NHS Trust, London, UK. rachel.abbott@nhs.net
Griffiths
W A D
WA
D000328:Adult; D005050:Etretinate / Q000627:therapeutic use; D005500:Follow-Up Studies; D006801:Humans; D007641:Keratolytic Agents / Q000627:therapeutic use; D008297:Male; D010916:Pityriasis Rubra Pilaris / Q000188:drug therapy / Q000473:pathology*; D011379:Prognosis; D012075:Remission, Spontaneous
D007641:Keratolytic Agents; D005050:Etretinate