Giant pulmonary sequestration: the rare case requiring the EXIT procedure with resection and ECMO.
Although most prenatally diagnosed pulmonary sequestrations (PS) are asymptomatic, large lesions are associated with pleural effusions and pulmonary hypoplasia. We present the first reported case of a prenatally diagnosed giant extralobar pulmonary sequestration that required the ex utero intrapartum treatment (EXIT) procedure with resection and extracorporeal membrane oxygenation (ECMO). We discuss the compelling rationale for performing EXIT-resection-ECMO in the setting of a large thoracic mass and anticipated severe respiratory failure at birth.
Mychaliska
George B
GB
The Fetal Diagnosis and Treatment Center, University of Michigan, Ann Arbor, MI, USA. mychalis@umich.edu
Bryner
Benjamin S
BS
Nugent
Clark
C
Barks
John
J
Hirschl
Ronald B
RB
McCrudden
Kimberly
K
Chames
Mark
M
Gomez-Fifer
Carlen
C
Servin
Monica N
MN
Chiravuri
S Devi
SD
D000328:Adult; D001998:Bronchopulmonary Sequestration / Q000000981:diagnostic imaging / Q000601:surgery* / Q000628:therapy; D015199:Extracorporeal Membrane Oxygenation; D005260:Female; D005333:Fetus / Q000098:blood supply / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011247:Pregnancy; D014463:Ultrasonography