Progression of conduction system disease in a paced patient with Kearns-Sayre syndrome.
The Kearns-Sayre syndrome is a rare condition characterized by external ophthalmoplegia, retinal pigmentary degeneration and progressive impairment of cardiac conduction. We report a patient with the permanent pacemaker. The spontaneous cardiac impulse formation disappeared during long-term follow-up in this patient with Kearns-Sayre Syndrome.
Yeşil
Murat
M
Department of Cardiology, Atatürk Teaching Hospital, Izmir, Turkey.
Bayata
Serdar
S
Postaci
Nursen
N
Arikan
Erdinç
E
D000328:Adult; D001145:Arrhythmias, Cardiac / Q000209:etiology* / Q000503:physiopathology / Q000628:therapy; D002304:Cardiac Pacing, Artificial; D020878:Device Removal; D018450:Disease Progression; D004562:Electrocardiography; D004868:Equipment Failure; D005260:Female; D006329:Heart Conduction System / Q000503:physiopathology*; D006801:Humans; D007625:Kearns-Sayre Syndrome / Q000150:complications* / Q000503:physiopathology / Q000628:therapy; D010138:Pacemaker, Artificial; D013997:Time Factors; D016896:Treatment Outcome