title: Autonomic failure in primary amyloidosis.
abstract: Amyloidosis is an uncommon plasma cell dyscrasia affecting Multisystem, characterized by deposition of amyloid proteins in extracellular spaces and the tissues. Reported incidence of amyloidosis is 8 cases per million per year. Deposition of amyloid fibrils occurs in peripheral nerves in 20% of the cases in Primary Amyloidosis. Though. polyneuropathy is one of the presenting manifestations in cases of Primary Amyloidosis, pure autonomic failure without involving peripheral nerves is not a documented entity. Here, we present a case of Primary Amyloidosis presenting as Pure Autonomic Failure (Dysautonomia).
authors.affiliation: Medicine and Cardiology, Bharat Ratna Dr. Babasaheb Ambedkar Memorial Hospital, Central Railway, Byculla, Mumbai.
authors.forename: Aditi
authors.initials: A
authors.lastname: Pandit
authors.forename: Savita
authors.initials: S
authors.lastname: Gangurde
authors.forename: S B
authors.initials: SB
authors.lastname: Gupta