Primary extrauterine endometrial stromal cell sarcoma: a case and review.
BACKGROUND
Extrauterine endometrial stromal sarcoma (ESS) is a rare neoplasm. Little is known about its pathophysiology or best treatment approach.


METHODS
We are describing a case of extrauterine ESS in a 70-year-old woman on hormone replacement therapy and with a history of endometriosis. We also present a brief review of the literature on ESS and its relationship to endometriosis and hormonal therapy.


CONCLUSIONS
Complete resection should remain the treatment of choice for ESS. Unresectable or metastatic low-grade ESS may respond well to progestin therapy, but outcomes of high-grade ESS tend to be poor.
Zemlyak
Alla
A
Stony Brook University Medical Center, Stony Brook, NY, USA.
Hwang
Sonya
S
Chalas
Eva
E
Pameijer
Colette R J
CR