title: Primary extrauterine endometrial stromal cell sarcoma: a case and review.
abstract: BACKGROUND
  Extrauterine endometrial stromal sarcoma (ESS) is a rare neoplasm. Little is known about its pathophysiology or best treatment approach.
  
  
  METHODS
  We are describing a case of extrauterine ESS in a 70-year-old woman on hormone replacement therapy and with a history of endometriosis. We also present a brief review of the literature on ESS and its relationship to endometriosis and hormonal therapy.
  
  
  CONCLUSIONS
  Complete resection should remain the treatment of choice for ESS. Unresectable or metastatic low-grade ESS may respond well to progestin therapy, but outcomes of high-grade ESS tend to be poor.
authors.affiliation: Stony Brook University Medical Center, Stony Brook, NY, USA.
authors.forename: Alla
authors.initials: A
authors.lastname: Zemlyak
authors.forename: Sonya
authors.initials: S
authors.lastname: Hwang
authors.forename: Eva
authors.initials: E
authors.lastname: Chalas
authors.forename: Colette R J
authors.initials: CR
authors.lastname: Pameijer