Chronic catastrophic-like antiphospholipid syndrome: a “smoldering” variant?
Catastrophic antiphospholipid syndrome (CAPS) is characterized by life-threatening diffuse thrombotic manifestations involving particularly small vessels of kidney, lungs, brain and skin. We report a 20-year-old female with systemic lupus erythematosus and secondary antiphospholipid syndrome who presented typical organ and histological involvement as seen in CAPS but with protracted course suggesting a “smoldering” form of the disease.
Athanazio
Daniel
D
Universidade Federal da Bahia, Salvador, Brazil.
Rocha
Maria Cristina
MC
de Souza e Souza
Túlio Geraldo
TG
Oliveira e Silva
Natália
N
Jezler
Sérgio
S
Santiago
Mittermayer Barreto
MB
D016736:Antiphospholipid Syndrome / Q000145:classification / Q000175:diagnosis / Q000188:drug therapy / Q000276:immunology*; D002388:Catastrophic Illness; D002908:Chronic Disease; D004359:Drug Therapy, Combination; D005260:Female; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use; D008180:Lupus Erythematosus, Systemic / Q000150:complications / Q000188:drug therapy / Q000276:immunology*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D055815:Young Adult
D007166:Immunosuppressive Agents