Idiopathic hypertrophic cranial pachymeningitis and dural sinus occlusion: two patients with long-term follow up.
Idiopathic hypertrophic cranial pachymeningitis (IHPM) is a clinicopathological entity characterized by thickening and fibrosis of the dura mater with resultant clinical symptoms. It is generally steroid responsive and has a tendency to remit and relapse. We present here two patients with IHPM with associated dural sinus occlusion and describe their clinicoradiological features and long-term course and outcome.
Bhatia
R
R
Department of Neurology, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, 110029, India. rohitbhatia71@yahoo.com
Tripathi
M
M
Srivastava
A
A
Garg
A
A
Singh
M B
MB
Nanda
A
A
Padma
M V
MV
Prasad
K
K
D000328:Adult; D002318:Cardiovascular Diseases / Q000150:complications* / Q000473:pathology; D002533:Cerebral Angiography / Q000379:methods; D003392:Cranial Sinuses / Q000473:pathology*; D004388:Dura Mater / Q000473:pathology*; D006801:Humans; D006984:Hypertrophy; D008137:Longitudinal Studies; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D008581:Meningitis / Q000150:complications* / Q000473:pathology; D055815:Young Adult