Transient monoparesis after blade plate removal in a Hutchinson-Gilford progeria syndrome patient: a case report.
Treatment of patients with Hutchinson-Gilford progeria syndrome (HGPS) is based on the abnormalities of accelerated aging that affect the healing processes, combined with a fragile cardiovascular status. A classic HGPS case, of Korean ancestry, previously treated for severe coxa valga with bilateral varus osteotomies using blade plate fixation is presented. Complications over the blade plate area required removal of the hardware, after which the patient showed right-sided hypertonicity--determined to be a cerebrovascular accident. Subsequently, the patient returned almost completely to her presurgical neurologic status. Perioperative planning for HGPS patients should include risks that are typically considered in the planning for geriatric patient care.
Yandow
Suzanne M
SM
Central Texas Pediatric Orthopaedics and Scoliosis Research, USA. smyandow@yahoo.com
Rimoin
David L
DL
Grace
Aimee M
AM
Fillman
Ramona R
RR
Raney
Ellen M
EM
D001860:Bone Plates; D005260:Female; D006617:Hip Dislocation / Q000601:surgery; D006621:Hip Joint / Q000601:surgery; D006801:Humans; D007223:Infant; D016268:Internal Fixators; D009122:Muscle Hypertonia / Q000209:etiology / Q000473:pathology; D010027:Osteotomy / Q000295:instrumentation; D010291:Paresis / Q000209:etiology* / Q000473:pathology; D011183:Postoperative Complications; D011371:Progeria / Q000473:pathology / Q000601:surgery*; D020127:Recovery of Function