Fatal cardiac arrest due to an unusual fibroma of the pulmonary valve.
Fibroma, the second most common tumor in childhood, usually is a large solitary mass involving the ventricular septum or the left and rarely the right free ventricular wall. An unusual case of a 5.2-year-old boy with a large mass originating from the pulmonary valve is reported. The patient presented for evaluation of a murmur. Echocardiography and cardiac magnetic resonance imaging showed a large tumor extending from the distal right ventricular outflow tract through the pulmonary valve and into the main pulmonary artery causing moderate obstruction. The patient had a fatal cardiac arrest while awaiting surgery. The postmortem examination proved the tumor to be a fibroma.
Pediatric Cardiology Department, Onassis Cardiac Surgery Center, Athens, Greece. kiaffasm@otenet.gr
Maria G
MG
Kiaffas
Peter G
PG
Danias
Loukas
L
Kaklamanis
Spyridon
S
Rammos
D002648:Child; D017809:Fatal Outcome; D005350:Fibroma / Q000150:complications / Q000473:pathology*; D006323:Heart Arrest / Q000209:etiology*; D006338:Heart Neoplasms / Q000150:complications / Q000473:pathology*; D006349:Heart Valve Diseases / Q000150:complications / Q000473:pathology*; D006801:Humans; D008297:Male; D011664:Pulmonary Valve