Full-thickness skin grafting in pseudosyndactily with recessive dystrophic epidermolysis bullosa.
Two 17- and 11-year-old brothers appeared with mitten pseudosyndactily of both hands. They have been suffering from recessive dystrophic epidermolysis bullosa with recurrent cutaneous blister formation either spontaneously or due to minor trauma. Surgeries were performed to release and widen the first web space. Full thickness skin graft which was used to cover the resulting raw surface appears stable as normal skin to them. The two brothers have improvement in range of motion of their thumbs and index fingers.
Prasetyono
Theddeus O H
TO
Department of Surgery, University of Indonesia, Jakarta, Indonesia. teddyohprasetyono@yahoo.com
Yantoko
D000293:Adolescent; D002648:Child; D003286:Contracture / Q000601:surgery; D016108:Epidermolysis Bullosa Dystrophica / Q000235:genetics*; D005385:Fingers / Q000002:abnormalities* / Q000601:surgery*; D006801:Humans; D008297:Male; D016059:Range of Motion, Articular; D035781:Siblings; D013524:Surgical Flaps; D013576:Syndactyly / Q000601:surgery*