Severe exophthalmos in trigeminal plexiform neurofibroma involving the orbit and the infratemporal fossa.
Trigeminal plexiform neurofibromas involving the orbit and the infratemporal fossa are rare tumours. An uncommon case of a plexiform neurofibroma of the trigeminal nerve occurring in a 53-year-old female patient with severe cosmetic deformity is reported. The clinical findings, neuroradiographic features, surgical management, postoperative results and follow-up of trigeminal plexiform neurofibromas are reviewed.
Otorhinolaryngology Service, Basurto Hospital, School of Medicine, University of the Basque Country, UPV/EHU, Gurtubay, s/n, 48013 Bilbao, Spain. francisco.santaolalla@ehu.es
F
F
Santaolalla
J M
JM
Sanchez
C
C
Ereño
G
G
Lecumberri
C
C
Valdes
D005094:Exophthalmos / Q000209:etiology* / Q000601:surgery; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods; D008875:Middle Aged; D018318:Neurofibroma, Plexiform / Q000150:complications* / Q000601:surgery; D010524:Peripheral Nervous System Neoplasms / Q000150:complications* / Q000473:pathology / Q000601:surgery; D014276:Trigeminal Nerve / Q000473:pathology*