Anesthetic management of seven deliveries in three sisters with the May-Hegglin anomaly.
May-Hegglin anomaly is a rare genetic hematological disorder characterized by thrombocytopenia, but platelet function is usually normal. Three sisters with May-Hegglin anomaly and thrombocytopenia (platelet counts 14,000-100,000/mm(3)) were given neuraxial anesthesia for a total of 7 deliveries, 5 vaginal and 2 cesarean. None of the women had complications and no blood products were transfused.
Fishman
Eric B
EB
Department of Anesthesiology, WellStar Kennestone Hospital, Marietta, Georgia, USA.
Connors
Jean M
JM
Camann
William R
WR
D000767:Anesthesia, Epidural / Q000009:adverse effects; D000773:Anesthesia, Obstetrical / Q000009:adverse effects; D000775:Anesthesia, Spinal / Q000009:adverse effects; D002585:Cesarean Section; D036861:Delivery, Obstetric; D005260:Female; D006801:Humans; D050498:Live Birth; D010976:Platelet Count; D011247:Pregnancy; D011250:Pregnancy Complications, Hematologic / Q000097:blood*; D035781:Siblings; D013921:Thrombocytopenia / Q000097:blood* / Q000151:congenital