Vulval and perianal inflammatory linear verrucous epidermal naevus.
Inflammatory linear verrucous epidermal naevus (ILVEN) is a rare form of epidermal naevus. It occurs as a linear dermatitic or psoriasiform plaque, with onset usually in the first 5 years of life. Lesions are characteristically intensely itchy. We present a case of ILVEN occurring on the vulva and perianal region of a 6-year-old girl. The lesion was initially thought to be an area of lichenified dermatitis; however, treatment with even super-potent topical corticosteroids did not significantly improve the inflammation. A biopsy was performed and histopathological examination showed characteristic features. ILVEN is frequently refractory to topical treatment and surgical excision of lesions may be an option for relief of symptoms. ILVEN occasionally presents in the inguinogenital region and in this area may, like many vulval naevi, be misdiagnosed as vulvitis, psoriasis, genital warts or sexual abuse.
Le
Katie
K
Department of Dermatology, The Children's Hospital at Westmead, Westmead, New South Wales, Australia. katie.le@unsw.edu.au
Wong
Li-Chuen
LC
Fischer
Gayle
G
D000287:Administration, Topical; D002648:Child; D005260:Female; D006801:Humans; D008775:Methylprednisolone / Q000008:administration & dosage / Q000627:therapeutic use; D009506:Nevus / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology; D011537:Pruritus / Q000209:etiology; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology; D014844:Vulva / Q000473:pathology
D008775:Methylprednisolone