[Histiocytosis of Langerhans cells. Simultaneous manifestation in both mastoid cavities].
Histiocytosis X (Langerhans cells) is a rare disease with different forms of manifestation in the head and neck, which mostly occurs in children. We report the case of a 52-year-old male patient from Saudi Arabia who presented in the out-patient department of the University Hospital Charité Berlin with therapy-resistant otitis externa. ENT examination additionally showed nasal polyps. A paranasal computed tomography scan revealed as an incidental finding a mass forming tumor in both mastoids with osseous destruction of the posterior cranial fossa. Histological evaluation of the suspected tissue revealed histiocytosis X in both mastoids. After exclusion of a systemic disease local low-dose radiotherapy with 9 Gy (3x3 Gy) of the mastoid cavities was administered.
Thelen
A
A
Klinik für Hals-, Nasen-, Ohrenkrankheiten, Charité-Universitätsmedizin Berlin, Charité Campus Mitte, Charitéplatz 1, 10117, Berlin. ariane.thelen@charite.de
Weikert
S
S
Schrom
T
T
Sedlmaier
B
B
D006646:Histiocytosis, Langerhans-Cell / Q000175:diagnosis* / Q000532:radiotherapy*; D006801:Humans; D008297:Male; D008416:Mastoid; D008417:Mastoiditis / Q000175:diagnosis* / Q000532:radiotherapy*; D008875:Middle Aged; D016896:Treatment Outcome