Perivascular epithelioid cell tumor (PEComa) of abdominal cavity from falciform ligament: a case report.
We present a case of perivascular epithelioid cell tumors (PEComas) in the abdominal cavity at the falciform ligament. A 30-yr-old Korean man visited to hospital for the evaluation of a growing, palpable abdominal mass. He had felt the mass growing over 6 months. There was no family or personal history of tuberous sclerosis. The resected specimen showed a mass of 8.0x7.0x5.5 cm in size. Histological examination showed sheets of spindle-to-epithelioid cells with clear-to-eosinophilic cytoplasm. Immunohistochemically, tumor cells were positive for HMB-4 (gp100) and smooth muscle actin. They were also positive for the S-100, which is a marker of neurogenic and melanocytic tumors. Patient was treated with radical resection of tumor without any adjuvant therapy. He is well and on follow-up visits without tumor recurrence.
Choi
Cheol Woong
CW
Department of Internal Medicine, Pusan National University College of Medicine, Busan, Korea.
Kim
Tae Oh
TO
Kim
Kyung Yeob
KY
Lee
Sun Mi
SM
Kim
Gwang Ha
GH
Kang
Dae Hwan
DH
Song
Geun Am
GA
Kim
Suk
S
Kim
Dae Hwan
DH
D000008:Abdominal Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D000199:Actins / Q000378:metabolism; D000328:Adult; D000951:Antigens, Neoplasm / Q000378:metabolism; D006801:Humans; D008022:Ligaments / Q000473:pathology; D008297:Male; D058950:Melanoma-Specific Antigens; D009363:Neoplasm Proteins / Q000378:metabolism; D054973:Perivascular Epithelioid Cell Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D009418:S100 Proteins / Q000378:metabolism; D014057:Tomography, X-Ray Computed
D000199:Actins; D000951:Antigens, Neoplasm; D058950:Melanoma-Specific Antigens; D009363:Neoplasm Proteins; D009418:S100 Proteins