title: Perivascular epithelioid cell tumor (PEComa) of abdominal cavity from falciform ligament: a case report.
abstract: We present a case of perivascular epithelioid cell tumors (PEComas) in the abdominal cavity at the falciform ligament. A 30-yr-old Korean man visited to hospital for the evaluation of a growing, palpable abdominal mass. He had felt the mass growing over 6 months. There was no family or personal history of tuberous sclerosis. The resected specimen showed a mass of 8.0x7.0x5.5 cm in size. Histological examination showed sheets of spindle-to-epithelioid cells with clear-to-eosinophilic cytoplasm. Immunohistochemically, tumor cells were positive for HMB-4 (gp100) and smooth muscle actin. They were also positive for the S-100, which is a marker of neurogenic and melanocytic tumors. Patient was treated with radical resection of tumor without any adjuvant therapy. He is well and on follow-up visits without tumor recurrence.
authors.affiliation: Department of Internal Medicine, Pusan National University College of Medicine, Busan, Korea.
authors.forename: Cheol Woong
authors.initials: CW
authors.lastname: Choi
authors.forename: Tae Oh
authors.initials: TO
authors.lastname: Kim
authors.forename: Kyung Yeob
authors.initials: KY
authors.lastname: Kim
authors.forename: Sun Mi
authors.initials: SM
authors.lastname: Lee
authors.forename: Gwang Ha
authors.initials: GH
authors.lastname: Kim
authors.forename: Dae Hwan
authors.initials: DH
authors.lastname: Kang
authors.forename: Geun Am
authors.initials: GA
authors.lastname: Song
authors.forename: Suk
authors.initials: S
authors.lastname: Kim
authors.forename: Dae Hwan
authors.initials: DH
authors.lastname: Kim
mesh_terms: D000008:Abdominal Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D000199:Actins / Q000378:metabolism; D000328:Adult; D000951:Antigens, Neoplasm / Q000378:metabolism; D006801:Humans; D008022:Ligaments / Q000473:pathology; D008297:Male; D058950:Melanoma-Specific Antigens; D009363:Neoplasm Proteins / Q000378:metabolism; D054973:Perivascular Epithelioid Cell Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D009418:S100 Proteins / Q000378:metabolism; D014057:Tomography, X-Ray Computed
chemical_list: D000199:Actins; D000951:Antigens, Neoplasm; D058950:Melanoma-Specific Antigens; D009363:Neoplasm Proteins; D009418:S100 Proteins