Recurrent syncope episodes in a 33-year-old male patient: case report and review of literature.
Case report and review of literature of a 33-year-old-male patient who was suffering from recurrent events of loss of consciousness (syncope) found to have multiple events of sustained and non sustained left bundle-branch morphology ventricular tachycardia during Holter evaluation. Both, the echocardiographic and magnetic resonance studies demonstrated morphological changes as seen in Arrhythmogenic right ventricular cardiomyopathy. Arrhythmogenic Right Ventricular Dysplasia (ARVD) is a rare cardiomyopathy characterized by life-threatening ventricular arrhythmias in the absence of apparent structural left heart disease, predominantly occurring within the male gender. Though it is mostly a hereditary condition, there are some sporadic cases. It is characterized by progressive degeneration and fibrous-fatty replacement of the right ventricular myocardium. The European Society of Cardiology and the International Society and Federation Task force is useful for the diagnosis of the condition because of the difficulties in as well as inaccuracies in tissue diagnosis. Patients with a diagnosis of ARVD who suffers from recurrent syncope events and ventricular arrhythmias an Implantable Cardiovertor-Defibrillator (ICD) is indicated to decrease their risk of sudden cardiac death events.
Del Rio-Santiago
Valentín
V
Cardiovascular Medicine Section, Department of Medicine, VA Caribbean Healthcare System, Puerto Rico, USA.
Vicenty-Rivera
Sonia I
SI
Judge
Daniel
D
Ortiz-Muñoz
Luis
L
D000328:Adult; D000368:Aged; D000369:Aged, 80 and over; D019571:Arrhythmogenic Right Ventricular Dysplasia / Q000175:diagnosis* / Q000235:genetics / Q000628:therapy; D002648:Child; D017147:Defibrillators, Implantable; D003937:Diagnosis, Differential; D004562:Electrocardiography; D015716:Electrocardiography, Ambulatory; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D010375:Pedigree; D012008:Recurrence; D013575:Syncope / Q000209:etiology*; D017180:Tachycardia, Ventricular / Q000175:diagnosis