Angiomyofibroblastoma: a rare vulvar tumor.
BACKGROUND
Angiomyofibroblastoma is a rare, benign mesenchymal tumor that occurs mainly in the vulval region of middle age (35-45 years) women.


METHODS
We describe a 41-year-old woman, presenting with a 10-cm right vulvar mass and persistent perineal pain lasting 1 month. A surgical excision of the lesion was performed and a large mass with an intact capsule was sent for pathological examination. The results indicated angiomyofibroblastoma.


CONCLUSIONS
The differential diagnosis between angiomyofibroblastoma (AMF) and aggressive angiomyxoma (AAM) is very important because prognoses are not the same. AMF is a well-circumscribed lesion, with a weak risk of local non-destructive recurrence. AAM is a locally aggressive and infiltrative neoplasm, with a high risk of local aggressive recurrence. Wide excision with a rim of normal tissue is recommended in all cases of vulvar tumors.
Ducarme
Guillaume
G
Department of Obstetrics and Gynecology, Hôpital Beaujon, Assistance Publique-Hôpitaux de Paris, Université Paris 7, 100 Boulevard du Général Leclerc, Clichy, France. g.ducarme@gmail.com
Valentin
Morgane
M
Davitian
Carine
C
Felce-Dachez
Michele
M
Luton
Dominique
D
D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D009232:Myxoma / Q000175:diagnosis*; D009379:Neoplasms, Muscle Tissue / Q000175:diagnosis*; D014846:Vulvar Neoplasms / Q000175:diagnosis*