Phacomatosis pigmentopigmentalis: aberrant Mongolian spots and segmental café au lait macules.
We report a case of an otherwise healthy male newborn, with segmental café au lait spots on his left buttocks and left thigh down to the medial knee, in a nevoid pattern, and an aberrant Mongolian spot on the ipsilateral cheek of the buttocks in a checkerboard pattern. We propose the name phacomatosis pigmentopigmentalis in analogy to phacomatosis pigmentovascularis, and phacomatosis pigmentokeratotica.
Wolf
Ronni
R
The Dermatology Unit, Kaplan Medical Center, Rechovot, Israel. wolf_r@netvision.net.il
Wolf
Danny
D
Davidovici
Batya
B
D019080:Cafe-au-Lait Spots / Q000150:complications / Q000473:pathology*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D049328:Mongolian Spot / Q000150:complications / Q000473:pathology*