Angiomyofibroblastoma: a rare vulvar tumor.
BACKGROUND
Angiomyofibroblastoma is a rare, benign mesenchymal tumor that occurs mainly in the vulval region of middle age (35-45 years) women.


METHODS
We describe a 41-year-old woman, presenting with a 10-cm right vulvar mass and persistent perineal pain lasting 1 month. A surgical excision of the lesion was performed and a large mass with an intact capsule was sent for pathological examination. The results indicated angiomyofibroblastoma.


CONCLUSIONS
The differential diagnosis between angiomyofibroblastoma (AMF) and aggressive angiomyxoma (AAM) is very important because prognoses are not the same. AMF is a well-circumscribed lesion, with a weak risk of local non-destructive recurrence. AAM is a locally aggressive and infiltrative neoplasm, with a high risk of local aggressive recurrence. Wide excision with a rim of normal tissue is recommended in all cases of vulvar tumors.
Department of Obstetrics and Gynecology, Hôpital Beaujon, Assistance Publique-Hôpitaux de Paris, Université Paris 7, 100 Boulevard du Général Leclerc, Clichy, France. g.ducarme@gmail.com
Guillaume
G
Ducarme
Morgane
M
Valentin
Carine
C
Davitian
Michele
M
Felce-Dachez
Dominique
D
Luton
D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D009232:Myxoma / Q000175:diagnosis*; D009379:Neoplasms, Muscle Tissue / Q000175:diagnosis*; D014846:Vulvar Neoplasms / Q000175:diagnosis*