Juvenile Paget's disease with paranasal sinus aplasia.
Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.
Department of Otorhinolaryngology-Head and Neck Surgery, Maryknoll Medical Center, Busan, Korea.
Ki Beom
KB
Bae
Jae Hwan
JH
Kwon
Young Ho
YH
Kim
Tae Young
TY
Jung
Joong Hwan
JH
Cho