Periumbilical perforating pseudoxanthoma elasticum.
A 58-year-old, gravida 6, obese woman presented with a pruritic yellowish plaque around the umbilicus, which first appeared about 3 years ago. She also had flat yellow papules on the axilla and neck. After a burn from a heating device, a few perforating papules and a violaceous hue occurred on the plaque. Histological examination revealed pathological elastic fibers with a keratotic plug and perforation in the deep dermis, which was consistent with perforating pseudoxanthoma elasticum. This case indicates that perforating pseudoxanthoma elasticum, a variant of hereditary pseudoxanthoma elasticum may perforate due to mechanical factors.
Kocatürk
Emek
E
Goztepe Training and Research Hospital, Department of Dermatology, Istanbul, Turkey. emekozgur@yahoo.com
Kavala
Mukaddes
M
Zindanci
Ilkin
I
Koç
Melek
M
D005260:Female; D006801:Humans; D008875:Middle Aged; D011561:Pseudoxanthoma Elasticum / Q000175:diagnosis* / Q000188:drug therapy; D013256:Steroids / Q000008:administration & dosage; D014472:Umbilicus / Q000473:pathology*
D013256:Steroids