[Total intravenous anesthesia in Osteogenesis imperfecta patient: case report.].
OBJECTIVE
Osteogenesis Imperfecta is an uncommon genetic connective tissue disease with prevalence of 1/10000, primarily involving endochondral ossification, resulting in brittle bones, multiple fractures and skeletal deformities. This article aimed at reporting a case of Osteogenesis Imperfecta patient submitted to total intravenous anesthesia for fractured femur surgical repair.


METHODS
Male patient, 15 years old, 41 kg, 140 cm, with history of Osteogenesis Imperfecta and cardiopathy, scheduled for fractured femur surgical repair. In the operating room patient was monitored with ECG, HR, NIBP and SpO2 and was submitted to total intravenous anesthesia with propofol, alfentanil and cisatracurium. Monitoring of P ET CO2 and esophageal temperature was introduced after TI. There have been no complications both in the intraoperative period and in the post-anesthetic care unit. Patient was discharged 5 days later.


CONCLUSIONS
This report has shown satisfactory intra and postoperative evolution of Osteogenesis Imperfecta patient submitted to total intravenous general anesthesia. Disease complexity has shown the need for anesthesiologists adequate evaluation and monitoring.
Neves
José Francisco Nunes Pereira das
JF
CET, SBA, Universidade Federal de Juiz de Fora.
Sant'anna
Roberto Silva
RS
Almeida
João Rosa de
JR
Saldanha
Rodrigo Machado
RM
Magalhães
Marcos Gonçalves
MG