Cardiac papillary fibroelastoma presenting as chorea in childhood.
A 5-year-old boy presented with acute onset of chorea and dysarthria. During his workup, a heart murmur was noted. Echocardiography revealed multiple mobile masses in the left ventricular outflow tract related to the mitral valve. Brain magnetic resonance imaging and magnetic resonance angiography did not detect any abnormalities. He underwent a subtotal resection of the mass to preserve valvular function. The anatomic pathology was papillary fibroelastoma.
Hoashi
Takaya
T
Division of Pediatric Cardiovascular Surgery, Department of Surgery, University of Michigan Medical School, 5144 Cardiovascular Center/SPC 5864, Ann Arbor, MI 48109-5864, USA.
Florentine
Michael S
MS
Gordon
David
D
Ohye
Richard G
RG
D002675:Child, Preschool; D002819:Chorea / Q000209:etiology*; D003937:Diagnosis, Differential; D004452:Echocardiography; D005350:Fibroma / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery*; D006338:Heart Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male