Cardiac angiosarcoma with cardiac tamponade diagnosed as a ruptured aneurysm of the sinus valsalva.
Primary cardiac angiosarcoma is a rare, diagnostically elusive disease with a poor prognosis. In this report, we describe the case of a 56-year-old woman with a right atrial angiosarcoma. The patient presented with impending cardiac tamponade caused by right atrial perforation, but was misdiagnosed as a ruptured aneurysm of the sinus valsalva based on findings of a continuous murmur and an aorta to right atrium shunt by echocardiography. In the emergent operation that ensued, we found a right atrial perforation and a right coronary artery fistula to the right atrium. Coronary artery fistula is a rare complication of primary cardiac angiosarcoma, and a continuous murmur is also extremely rare as a clinical finding of angiosarcoma. We report the case and review the literature.
Yoshitake
Isamu
I
Department of Cardiovascular Surgery, Nihon University School of Medicine, Tokyo, Japan. iyoshing@yahoo.co.jp
Hata
Mitsumasa
M
Sezai
Akira
A
Niino
Tetsuya
T
Unosawa
Satoshi
S
Shimura
Kazuma
K
Kasamaki
Yuji
Y
Minami
Kazutomo
K
D017542:Aneurysm, Ruptured / Q000175:diagnosis* / Q000601:surgery; D001014:Aortic Aneurysm / Q000175:diagnosis* / Q000601:surgery; D002305:Cardiac Tamponade / Q000175:diagnosis* / Q000601:surgery; D004452:Echocardiography; D005260:Female; D006337:Heart Murmurs / Q000175:diagnosis; D006338:Heart Neoplasms / Q000175:diagnosis* / Q000601:surgery; D006394:Hemangiosarcoma / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D008875:Middle Aged; D012850:Sinus of Valsalva / Q000473:pathology* / Q000601:surgery