Progressive familial intrahepatic cholestasis complicating pregnancy.
Progressive familial intrahepatic cholestasis complicating pregnancy has not been described in the English language literature. We describe a successful pregnancy in an affected patient initially treated with biliary diversion, then successfully treated by plasmapheresis following failed medical management of progressive cholestasis.
Mathias
Amanda
A
Division of Maternal-Fetal Medicine, Department of Obstetrics and Gynecology, Maine Medical Center, Portland, Maine, USA.
Wax
Joseph R
JR
Pinette
Michael G
MG
Cartin
Angelina
A
Blackstone
Jacquelyn
J
D000293:Adolescent; D001647:Bile Acids and Salts / Q000097:blood; D002780:Cholestasis, Intrahepatic / Q000097:blood / Q000150:complications / Q000235:genetics / Q000628:therapy*; D005260:Female; D006801:Humans; D010956:Plasmapheresis; D011247:Pregnancy; D011248:Pregnancy Complications / Q000235:genetics / Q000628:therapy*; D011537:Pruritus / Q000209:etiology / Q000628:therapy
D001647:Bile Acids and Salts