title: [Case of lymphangiomyomatosis of the kidney and retroperitoneum].
abstract: We report a 44-year-old female with lymphangiomyomatosis (LAM) of the kidney and retroperitoneum. Abdominal ultrasonography revealed a right kidney tumor, and she was referred to our department. Computed tomography (CT) revealed a para-aortic phyma in addition to the tumor. We performed retroperitoneal tumorectomy and partial resection of the right kidney via laparotomy. Pathological findings suggested LAM. LAM usually induces pulmonary lesions and its prognosis is relatively unfavorable. Female hormones are considered to be involved in the aggravation of LAM. The lesion may not have reached the lung in this postmenopausal woman because of the absence of these hormones.
authors.affiliation: Department of Urology and Renal Transplantation, Yokohama City University Medical Center.
authors.forename: Manabu
authors.initials: M
authors.lastname: Kakizoe
authors.forename: Akitoshi
authors.initials: A
authors.lastname: Takizawa
authors.forename: Yusuke
authors.initials: Y
authors.lastname: Hattori
authors.forename: Junichi
authors.initials: J
authors.lastname: Teranishi
authors.forename: Keiichi
authors.initials: K
authors.lastname: Kondou
authors.forename: Takeshi
authors.initials: T
authors.lastname: Kishida
authors.forename: Kazuo
authors.initials: K
authors.lastname: Saitou
authors.forename: Kazumi
authors.initials: K
authors.lastname: Noguchi
authors.forename: Yoshinobu
authors.initials: Y
authors.lastname: Kubota
authors.forename: Ayumi
authors.initials: A
authors.lastname: Murakami
authors.forename: Takeshi
authors.initials: T
authors.lastname: Sasaki
mesh_terms: D004967:Estrogens; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000000981:diagnostic imaging / Q000209:etiology / Q000473:pathology / Q000601:surgery*; D007813:Laparotomy; D018192:Lymphangioleiomyomatosis / Q000000981:diagnostic imaging / Q000209:etiology / Q000473:pathology / Q000601:surgery*; D008593:Menopause; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary; D009392:Nephrectomy; D012186:Retroperitoneal Neoplasms / Q000000981:diagnostic imaging / Q000209:etiology / Q000473:pathology / Q000601:surgery*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
chemical_list: D004967:Estrogens