Efficacy of cyclosporine A treatment in relapsing febrile lobular panniculitis associated with small vessel vasculitis.
Weber-Christian Disease (WCD), also known as relapsing febrile lobular non-suppurative panniculitis, is a rare condition characterized by recurrent subcutaneous inflammatory nodules in the adipose tissue in addition to fever, malaise and other systemic manifestations such as polyarthralgia and polymyalgia. The association with small vessel vasculitis has been rarely reported. We report here an unusual case of WCD associated with small vessels vasculitis also describing the efficacy of Cyclosporin A treatment.
Cantarini
Luca
L
Unit of Rheumatology, Interdepartmental Research Center of Systemic Autoimmune and Autoinflammatory Diseases, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100, Siena, Italy. cantariniluca@hotmail.com
Fanti
Francesca
F
Galeazzi
Mauro
M
Martino
Silvana
S
Miracco
Clelia
C
Biagioli
Maurizio
M
Dal Canto
Norberto
N
Cimaz
Rolando
R
D001706:Biopsy; D001808:Blood Vessels / Q000187:drug effects / Q000276:immunology / Q000473:pathology; D002648:Child; D002908:Chronic Disease; D016572:Cyclosporine / Q000494:pharmacology* / Q000627:therapeutic use; D006801:Humans; D007166:Immunosuppressive Agents / Q000494:pharmacology / Q000627:therapeutic use; D008297:Male; D010201:Panniculitis, Nodular Nonsuppurative / Q000150:complications* / Q000188:drug therapy* / Q000503:physiopathology; D012008:Recurrence; D012867:Skin / Q000187:drug effects / Q000276:immunology / Q000473:pathology; D016896:Treatment Outcome; D014657:Vasculitis / Q000188:drug therapy* / Q000209:etiology* / Q000503:physiopathology
D007166:Immunosuppressive Agents; D016572:Cyclosporine