title: Left ventricular noncompaction: a rare cause of hydrops fetalis.
abstract: We present a case of isolated left ventricular noncompaction (LVNC), a severe congenital cardiomyopathy, which presented in the neonatal period as fetal hydrops. To our knowledge, this is the first child with LVNC presenting with hydrops fetalis to survive infancy. Once considered a uniformly fatal and extremely rare form of cardiomyopathy, LVNC has recently been shown to be more common than previously reported, with a varying range of clinical severity. Although long-term morbidity and mortality are not clearly known, recent work suggests better survivability than once reported.
authors.affiliation: National Capital Consortium Pediatric Residency Program, National Naval Medical Center, Bethesda, MD, USA.
authors.forename: Autumn
authors.initials: A
authors.lastname: Richards
authors.forename: Chad Y
authors.initials: CY
authors.lastname: Mao
authors.forename: Nicole R
authors.initials: NR
authors.lastname: Dobson
mesh_terms: D000015:Abnormalities, Multiple; D009202:Cardiomyopathies / Q000151:congenital* / Q000188:drug therapy; D002585:Cesarean Section; D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006801:Humans; D015160:Hydrops Fetalis / Q000000981:diagnostic imaging* / Q000209:etiology*; D007231:Infant, Newborn; D011247:Pregnancy; D016216:Ultrasonography, Prenatal; D018487:Ventricular Dysfunction, Left / Q000151:congenital* / Q000188:drug therapy