title: A life-threatening complication of Ehlers-Danlos syndrome.
abstract: Ehlers-Danlos syndrome predisposes to the development of vascular malformations, which may present as life-threatening haemorrhage. This article presents a patient with Ehlers-Danlos syndrome in whom spontaneous rupture of an unusual arteriovenous fistula occurred. This rare diagnosis can be reached through close attention to the history and examination.
authors.affiliation: Paediatrics, UCL Institute of Child Health, London WC1N 1EH.
authors.forename: Sam
authors.initials: S
authors.lastname: Behjati
authors.forename: Yolande
authors.initials: Y
authors.lastname: Knight
authors.forename: Rudi
authors.initials: R
authors.lastname: Borgstein
authors.forename: Archana
authors.initials: A
authors.lastname: Goebells
authors.forename: Fiona
authors.initials: F
authors.lastname: Myint
mesh_terms: D000328:Adult; D001164:Arteriovenous Fistula / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D006406:Hematoma / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007083:Iliac Artery / Q000002:abnormalities*; D007084:Iliac Vein / Q000002:abnormalities*; D008297:Male; D015607:Stents; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome