title: Efficacy of cyclosporine A treatment in relapsing febrile lobular panniculitis associated with small vessel vasculitis.
abstract: Weber-Christian Disease (WCD), also known as relapsing febrile lobular non-suppurative panniculitis, is a rare condition characterized by recurrent subcutaneous inflammatory nodules in the adipose tissue in addition to fever, malaise and other systemic manifestations such as polyarthralgia and polymyalgia. The association with small vessel vasculitis has been rarely reported. We report here an unusual case of WCD associated with small vessels vasculitis also describing the efficacy of Cyclosporin A treatment.
authors.affiliation: Unit of Rheumatology, Interdepartmental Research Center of Systemic Autoimmune and Autoinflammatory Diseases, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100, Siena, Italy. cantariniluca@hotmail.com
authors.forename: Luca
authors.initials: L
authors.lastname: Cantarini
authors.forename: Francesca
authors.initials: F
authors.lastname: Fanti
authors.forename: Mauro
authors.initials: M
authors.lastname: Galeazzi
authors.forename: Silvana
authors.initials: S
authors.lastname: Martino
authors.forename: Clelia
authors.initials: C
authors.lastname: Miracco
authors.forename: Maurizio
authors.initials: M
authors.lastname: Biagioli
authors.forename: Norberto
authors.initials: N
authors.lastname: Dal Canto
authors.forename: Rolando
authors.initials: R
authors.lastname: Cimaz
mesh_terms: D001706:Biopsy; D001808:Blood Vessels / Q000187:drug effects / Q000276:immunology / Q000473:pathology; D002648:Child; D002908:Chronic Disease; D016572:Cyclosporine / Q000494:pharmacology* / Q000627:therapeutic use; D006801:Humans; D007166:Immunosuppressive Agents / Q000494:pharmacology / Q000627:therapeutic use; D008297:Male; D010201:Panniculitis, Nodular Nonsuppurative / Q000150:complications* / Q000188:drug therapy* / Q000503:physiopathology; D012008:Recurrence; D012867:Skin / Q000187:drug effects / Q000276:immunology / Q000473:pathology; D016896:Treatment Outcome; D014657:Vasculitis / Q000188:drug therapy* / Q000209:etiology* / Q000503:physiopathology
chemical_list: D007166:Immunosuppressive Agents; D016572:Cyclosporine