title: Aortic valve replacement in a patient with Osler-Rendu-Weber disease.
abstract: Osler-Rendu-Weber (hereditary hemorrhagic telangiectasia) disease is an uncommon disease characterized by the presence of abnormal telangiectasias and arteriovenous malformations that cause recurrent episodes of bleeding. We present a patient with Osler-Rendu-Weber disease, with a history of multiple major bleeding events and severe aortic valve stenosis, who underwent aortic valve replacement. Unexpectedly, the postoperative course was uneventful, and there was no untoward bleeding in the early or in the late postoperative follow-up.
authors: Cardiothoracic Intensive Care Unit, Instituto Cardiovascular de Buenos Aires, Buenos Aires, Argentina. marianobenzadon@yahoo.com.ar
authors: Mariano N
authors: MN
authors: Benzadón
authors: Juan Pablo
authors: JP
authors: Costabel
authors: Alberto Alves
authors: AA
authors: de Lima
authors: Fernando
authors: F
authors: Botto
authors: María Ester
authors: ME
authors: Aris Cancela
authors: Guillermo
authors: G
authors: Vaccarino
authors: Marcelo
authors: M
authors: Trivi
authors: Daniel
authors: D
authors: Navia
mesh_terms: D001024:Aortic Valve Stenosis / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D015150:Echocardiography, Doppler; D005500:Follow-Up Studies; D006350:Heart Valve Prosthesis; D019918:Heart Valve Prosthesis Implantation / Q000379:methods*; D006801:Humans; D008297:Male; D008875:Middle Aged; D035583:Rare Diseases; D018570:Risk Assessment; D012720:Severity of Illness Index; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications / Q000175:diagnosis*; D016896:Treatment Outcome