Cystic meningioangiomatosis in neurofibromatosis type 2: an MRI-pathological study.
We report cerebral cystic meningioangiomatosis in a patient with neurofibromatosis type 2. An 18-year-old woman presented with progressive hemiparesis secondary to a meningioma at the foramen magnum. Her MR examination also demonstrated three small cortical and subcortical cystic lesions. She underwent surgery for the meningioma, but died from brainstem infarction. Post-mortem histopathological examination of the cystic lesions showed enlarged subcortical perivascular spaces with overlying meningioangiomatosis. The unusual features and possible pathogenesis are discussed.
Fedi
M
M
Department of Neurology, Austin Health, Heidelberg, Victoria 3084, Australia.
Kalnins
R M
RM
Shuey
N
N
Fitt
G J
GJ
Newton
M
M
Mitchell
L A
LA
D000293:Adolescent; D020863:Central Nervous System Cysts / Q000150:complications / Q000473:pathology*; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008577:Meningeal Neoplasms / Q000150:complications / Q000473:pathology*; D008579:Meningioma / Q000150:complications / Q000473:pathology*; D016518:Neurofibromatosis 2 / Q000150:complications*; D010291:Paresis / Q000209:etiology / Q000473:pathology; D014057:Tomography, X-Ray Computed