A case of catecholaminergic polymorphic ventricular tachycardia.
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a familial cardiac arrhythmia that is related to RYR2 or CASQ2 gene mutation. It occurs in patients with structurally normal heart and causes exercise-emotion-triggered syncope and sudden cardiac death. We experienced a case of CPVT in an 11 year-old female patient who was admitted for sudden cardiovascular collapse. The initial electrocardiogram (ECG) on emergency department revealed ventricular fibrillation. After multiple defibrillations, sinus rhythm was restored. However, recurrent ventricular fibrillation occurred during insertion of nasogastric tube without sedation in coronary care unit. On ECG monitoring, bidirectional ventricular tachycardia occurred with sinus tachycardia and then degenerated into ventricular fibrillation. To our knowledge, there has been no previous case report of CPVT triggered by sinus tachycardia in Korea. Therefore, we report the case as well as a review of the literature.
Lee
Seung-Yul
SY
Division of Cardiology, Yonsei Cardiovascular Center and Cardiovascular Research Institute, Yonsei University College of Medicine, 250 Seongsan-ro, Seodaemun-gu,Seoul, Korea.
Kim
Jin-Bae
JB
Im
Eui
E
Yang
Woo-In
WI
Joung
Boyoung
B
Lee
Moon-Hyoung
MH
Kim
Sung-Soon
SS
D002395:Catecholamines / Q000378:metabolism*; D002648:Child; D004562:Electrocardiography; D005260:Female; D006801:Humans; D017180:Tachycardia, Ventricular / Q000175:diagnosis* / Q000235:genetics / Q000473:pathology
D002395:Catecholamines