Surgical management of univentricular heart with total anomalous pulmonary venous drainage and intrapulmonary vertical vein.
We report a patient with univentricular heart, heterotaxy syndrome with total anomalous pulmonary venous connection, and an intrapulmonary vertical vein draining into the left superior vena cava who underwent a successful bidirectional Glenn shunt without cardiopulmonary bypass. A polytetrafluoroethylene tube interposition graft was used between the superior vena cava and the pulmonary artery. This condition is unusual and physiologic palliation, rather than anatomic correction as described in this report, may be appropriate for managing this condition.
Malankar
Dhananjay
D
Cardiothoracic Sciences Center, All India Institute of Medical Sciences, New Delhi, India.
Talwar
Sachin
S
Makhija
Neeti
N
Sharma
Sanjeev
S
Choudhary
Shiv Kumar
SK
D006348:Cardiac Surgical Procedures / Q000379:methods; D006352:Heart Ventricles / Q000002:abnormalities / Q000601:surgery*; D006801:Humans; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities / Q000601:surgery*; D014683:Vena Cava, Superior / Q000002:abnormalities / Q000601:surgery*; D055815:Young Adult