Aortic valve replacement in a patient with Osler-Rendu-Weber disease.
Osler-Rendu-Weber (hereditary hemorrhagic telangiectasia) disease is an uncommon disease characterized by the presence of abnormal telangiectasias and arteriovenous malformations that cause recurrent episodes of bleeding. We present a patient with Osler-Rendu-Weber disease, with a history of multiple major bleeding events and severe aortic valve stenosis, who underwent aortic valve replacement. Unexpectedly, the postoperative course was uneventful, and there was no untoward bleeding in the early or in the late postoperative follow-up.
Benzadón
Mariano N
MN
Cardiothoracic Intensive Care Unit, Instituto Cardiovascular de Buenos Aires, Buenos Aires, Argentina. marianobenzadon@yahoo.com.ar
Costabel
Juan Pablo
JP
de Lima
Alberto Alves
AA
Botto
Fernando
F
Aris Cancela
María Ester
ME
Vaccarino
Guillermo
G
Trivi
Marcelo
M
Navia
Daniel
D
D001024:Aortic Valve Stenosis / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D015150:Echocardiography, Doppler; D005500:Follow-Up Studies; D006350:Heart Valve Prosthesis; D019918:Heart Valve Prosthesis Implantation / Q000379:methods*; D006801:Humans; D008297:Male; D008875:Middle Aged; D035583:Rare Diseases; D018570:Risk Assessment; D012720:Severity of Illness Index; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications / Q000175:diagnosis*; D016896:Treatment Outcome