Surgical repair of supravalvular aortic stenosis with use of Brom's technique: short-term results in 9 children.
There are few published reports of the results of supravalvular aortic stenosis correction with the use of Brom's 3-patch technique. Herein, we report our use of this procedure and the short-term results therefrom.From 2002 through 2007, 9 children underwent surgical correction of localized supravalvular aortic stenosis at our hospital. The patients ranged in age from 5 to 14 years, and 8 had Williams syndrome. All operations were performed by the same surgical team.No clinically significant associated cardiac anomalies were encountered. Each aortic repair involved the use of pericardium, Dacron, or both. One patient had an uncorrected right coronary artery obstruction and died postoperatively of refractory supraventricular tachycardia. In all 8 patients who survived, postoperative transaortic blood pressure gradients were improved (range, 0-16 mmHg), and no repeat operations were needed after 6 to 55 months' follow-up.We consider Brom's technique to be safe in the repair of supravalvular aortic stenosis. In our limited series, it produced effective anatomic restoration, with good short-term and potentially good long-term results.
Cruz-Castañeda
Brenda Fabiola
BF
Cardiosurgery Department, Hospital Civil de Guadalajara Fray Antonio Alcalde OPD, UMAE Hospital de Especialidades, CMNO IMSS, Guadalajara, Jalisco, CP 44340, México.
Carrillo-Llamas
Fernando
F
Ramos-Higuera
Saúl
S
López-Taylor
Jaime Gilberto
JG
Buen
Eliseo Portilla-de
EP
D000293:Adolescent; D021921:Aortic Stenosis, Supravalvular / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D001794:Blood Pressure; D001807:Blood Vessel Prosthesis; D019917:Blood Vessel Prosthesis Implantation / Q000009:adverse effects / Q000295:instrumentation; D006348:Cardiac Surgical Procedures / Q000009:adverse effects / Q000295:instrumentation; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008297:Male; D010496:Pericardium / Q000637:transplantation; D011093:Polyethylene Terephthalates; D011474:Prosthesis Design; D011859:Radiography; D013997:Time Factors; D016896:Treatment Outcome
D011093:Polyethylene Terephthalates