Congenital absence of portal vein associated with nodular regenerative hyperplasia of the liver and pulmonary hypertension.
We present a 15-year-old girl with congenital absence of the portal vein, pulmonary arterial hypertension and multiple liver lesions proven to be nodular regenerative hyperplasia with biopsy. Ultrasonography, computed tomography, and magnetic resonance imaging findings of the liver lesions and Type I portosystemic shunt are presented.
Peker
Ahmet
A
Department of Radiology, Ankara University, School of Medicine, Ankara, Turkey. ahmet_peker@hotmail.com
Ucar
Tayfun
T
Kuloglu
Zarife
Z
Ceyhan
Koray
K
Tutar
Ercan
E
Fitoz
Suat
S
D000293:Adolescent; D000792:Angiography / Q000379:methods*; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications* / Q000175:diagnosis*; D008099:Liver / Q000473:pathology*; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging*