title: A case of catecholaminergic polymorphic ventricular tachycardia.
abstract: Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a familial cardiac arrhythmia that is related to RYR2 or CASQ2 gene mutation. It occurs in patients with structurally normal heart and causes exercise-emotion-triggered syncope and sudden cardiac death. We experienced a case of CPVT in an 11 year-old female patient who was admitted for sudden cardiovascular collapse. The initial electrocardiogram (ECG) on emergency department revealed ventricular fibrillation. After multiple defibrillations, sinus rhythm was restored. However, recurrent ventricular fibrillation occurred during insertion of nasogastric tube without sedation in coronary care unit. On ECG monitoring, bidirectional ventricular tachycardia occurred with sinus tachycardia and then degenerated into ventricular fibrillation. To our knowledge, there has been no previous case report of CPVT triggered by sinus tachycardia in Korea. Therefore, we report the case as well as a review of the literature.
authors: Division of Cardiology, Yonsei Cardiovascular Center and Cardiovascular Research Institute, Yonsei University College of Medicine, 250 Seongsan-ro, Seodaemun-gu,Seoul, Korea.
authors: Seung-Yul
authors: SY
authors: Lee
authors: Jin-Bae
authors: JB
authors: Kim
authors: Eui
authors: E
authors: Im
authors: Woo-In
authors: WI
authors: Yang
authors: Boyoung
authors: B
authors: Joung
authors: Moon-Hyoung
authors: MH
authors: Lee
authors: Sung-Soon
authors: SS
authors: Kim
mesh_terms: D002395:Catecholamines / Q000378:metabolism*; D002648:Child; D004562:Electrocardiography; D005260:Female; D006801:Humans; D017180:Tachycardia, Ventricular / Q000175:diagnosis* / Q000235:genetics / Q000473:pathology
chemical_list: D002395:Catecholamines