[Peridural anaesthesia with ropivacaine for a patient with Friedrich's ataxia. Caesarean section after dorsal stabilisation of the spinal column (Th5-L1)].
Friedreich's ataxia (FA) is a hereditary disease, which leads to degenerative changes in the spinal cord and cerebellum (incidence 1:50,000). These changes are caused by a defect in the gene that encodes a mitochondrial gene called frataxin and causes muscle weakness, scoliosis, cardiomyopathy and impaired glucose tolerance. Therefore, these patients require special care during anaesthesia. We report the case of a 25-year-old primigravida with a history of FA and dorsal stabilisation of the vertebral column, who was admitted to our hospital for elective caesarean section. Due to increased sensitivity to muscle relaxants, peridural anaesthesia with 8 ml 0.75% ropivacaine and 10 microg sufentanil was used in this case. The perioperative neurological consultation revealed no undue exacerbation of symptoms.
Hanusch
P
P
Klinik für Anästhesiologie und Intensivmedizin, Klinikum der Universität München, Marchioninistr. 15, 81377, München.
Heyn
J
J
Well
H
H
Weninger
E
E
Hasbargen
U
U
Rehm
M
M
D000328:Adult; D000577:Amides; D000767:Anesthesia, Epidural; D000773:Anesthesia, Obstetrical; D018686:Anesthetics, Intravenous; D000779:Anesthetics, Local; D001860:Bone Plates; D002585:Cesarean Section; D005260:Female; D005621:Friedreich Ataxia / Q000150:complications / Q000503:physiopathology*; D006801:Humans; D011182:Postoperative Care; D011247:Pregnancy; D000077212:Ropivacaine; D013131:Spine / Q000601:surgery; D017409:Sufentanil
D000577:Amides; D018686:Anesthetics, Intravenous; D000779:Anesthetics, Local; D000077212:Ropivacaine; D017409:Sufentanil