title: Hepatopulmonary syndrome and liver sarcoidosis: a tale of two diseases.
abstract: Hepatopulmonary syndrome (HSP) is characterized by the triad of advanced liver disease, arterial hypoxemia, and intrapulmonary vascular dilatation. Most cases of HSP are associated with cirrhotic portal hypertension; however, it has also been reported in acute liver failure patients. An estimated prevalence of HPS in patients with chronic liver disease is around 5-32%. Sarcoidosis is a granulomatous disorder with noncaseating granulomas involving the lungs in 90% of cases. Sarcoidosis can involve the liver but in only about 1% of cases does it lead to cirrhosis and portal hypertension. In this review, we report a rare case of liver cirrhosis due to sarcoidosis with associated hepatopulmonary syndrome and discuss this in detail.
authors: SUNY at Buffalo, Hospitalist, Faxton-St. Luke's Hospital, Utica, NY 13502, USA. dranpatel@gmail.com
authors: Anil N
authors: AN
authors: Patel
authors: Khyati
authors: K
authors: Patel
authors: M Jeffrey
authors: MJ
authors: Mador
mesh_terms: D005260:Female; D020065:Hepatopulmonary Syndrome / Q000150:complications*; D006801:Humans; D000860:Hypoxia / Q000209:etiology*; D008103:Liver Cirrhosis / Q000209:etiology; D008107:Liver Diseases / Q000150:complications* / Q000473:pathology*; D008875:Middle Aged; D012507:Sarcoidosis / Q000150:complications* / Q000473:pathology*