Clear cell "sugar" tumors of urethra: a previously undescribed occurrence and review of published data.
Clear cell "sugar" tumor is a rare benign tumor considered as a member of the family of perivascular epithelioid cell tumors. To the best of our knowledge, this is the first case of clear cell "sugar" tumor presented as a mass protruding from the urethra in a 15-year-old girl. Pathologic examination revealed a tumor composed of epithelioid cells with "water" clear cytoplasm that stained positively for melanocytic and smooth muscle-specific markers. Treatment of this tumor included a surgical excision and complete removal of the urethral mass, with examination of surgical margins. Three months after surgery, the patient remains clinically free of disease.
De Dominicis
Gianfranco
G
Unit of Pathologic Anatomy, AORN Cardarelli, A. Cardarelli, Naples, Italy.
Boscaino
Amedeo
A
Marsilia
Giuseppina Marino
GM
D'Antonio
Antonio
A
Nappi
Oscar
O
D000293:Adolescent; D005260:Female; D006801:Humans; D054973:Perivascular Epithelioid Cell Neoplasms / Q000473:pathology / Q000601:surgery; D014523:Urethral Neoplasms / Q000473:pathology / Q000601:surgery