Cutaneous polyarteritis nodosa in adult onset Still's disease.
Adult onset Still's disease (AOSD) is a well recognized clinical disorder characterized by a typical rash. However, there have been several atypical cutaneous findings reported in patients with AOSD. Cutaneous polyarteritis nodosa (PAN) is a necrotizing vasculitis of the small and medium sized arteries, distinguishing itself from systemic PAN by its restriction to the skin and to the neurological and osteo-muscular systems. We report the case of a patient with AOSD who is unique in having developed cutaneous polyarteritis nodosa (PAN) during the active phase of her disease. To the best of our knowledge, no previous cases of AOSD associated with a cutaneous variant of PAN have been reported.
Mylona
Eleni
E
5th Department of Internal Medicine, Evangelismos Hospital, 45-47 Hipsilantou Str., Kolonaki, GR-106 76 Athens, Greece. emylon@med.uoa.gr
Vadala
Chariklia
C
Papadakos
Vasilios
V
Loverdos
Dionysios
D
Samarkos
Michael
M
Skoutelis
Athanasios
A
D000328:Adult; D018501:Antirheumatic Agents / Q000627:therapeutic use; D003937:Diagnosis, Differential; D004359:Drug Therapy, Combination; D005260:Female; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D010488:Polyarteritis Nodosa / Q000150:complications* / Q000175:diagnosis* / Q000188:drug therapy; D016706:Still's Disease, Adult-Onset / Q000150:complications* / Q000175:diagnosis* / Q000188:drug therapy; D016896:Treatment Outcome
D018501:Antirheumatic Agents; D005938:Glucocorticoids