[Noonan syndrome with atrial septal defect and hypertrophic cardiomyopathy].
Noonan syndrome is one of the most common nonchromosomal syndromes seen in children with congenital heart disease. The major cause of death is congestive heart failure. We report a case of Noonan syndrome with hypertrophic cardiomyopathy and arterial septal defect (ASD). Since 10 years old he had been suffering from congestive heart failure. ASD patch closure with a fenestrated flap valve patch was performed at 12 years of age. After operation, left-to-right shunt flow through the patch gradually decreased and he was discharged at 19 postoperative day in good condition.
Nakayama
M
M
Department of Cardiovascular Surgery, Nagoya First Red Cross Hospital, Nagoya, Japan.
Itou
T
T
Abe
T
T
Yamana
T
T
Kawamura
A
A
Yoshizumi
T
T
Sunada
M
M
D002312:Cardiomyopathy, Hypertrophic / Q000150:complications*; D002648:Child; D006344:Heart Septal Defects, Atrial / Q000150:complications*; D006801:Humans; D008297:Male; D009634:Noonan Syndrome / Q000150:complications*