Long-term survival of Uhl's anomaly with total cavopulmonary conversion.
We report a long-term survivor with Uhl's anomaly who underwent one and a half ventricle repair combined with a partial right ventriculectomy in infancy, followed by successful total cavopulmonary conversion with right ventricular exclusion 5 years later. The combination of total cavopulmonary connection and right ventricular exclusion could be the optimal surgical option for a critically ill infant with Uhl's anomaly.
Takizawa
Koki
K
Department of Surgery, University of Yamanashi, Chuo-city, Yamanashi, 409-3898, Japan. koki0610jp@yahoo.co.jp
Suzuki
Shoji
S
Honda
Yoshihiro
Y
Kaga
Shigeaki
S
Inoue
Hidenori
H
Matsumoto
Masahiko
M
D002648:Child; D018610:Heart Bypass, Right; D006330:Heart Defects, Congenital / Q000601:surgery*; D006352:Heart Ventricles / Q000002:abnormalities / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D012086:Reoperation; D017741:Survivors; D013997:Time Factors; D016896:Treatment Outcome